Journal of mucopolysaccharidosis and rare diseases
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v.2
no.1
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pp.5-7
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2016
Mucolipidoses II and III alpha/beta (ML II and ML III) are lysosomal disorders in which the essential mannose-6-phosphate recognition marker is not synthesized onto lysosomal hydrolases and other glycoproteins. The disorders are caused by mutations in GNPTAB, which encodes two of three subunits of the heterohexameric enzyme, N-acetylglucosamine-1-phosphotransferase ML II, recognizable at birth, often causes intrauterine growth impairment and sometimes the prenatal "Pacman" dysplasia. The main postnatal manifestations of ML II include gradual coarsening of neonatally evident craniofacial features, early cessation of statural growth and neuromotor development, dysostosis multiplex and major morbidity by hardening of soft connective tissue about the joints and in the cardiac valves. Fatal outcome occurs often before or in early childhood. ML III with clinical onset rarely detectable before three years of age, progresses slowly with gradual coarsening of the facial features, growth deficiency, dysostosis multiplex, restriction of movement in all joints before or from adolescence, painful gait impairment by prominent hip disease. Cognitive handicap remains minor or absent even in the adult, often wheelchair-bound patient with variable though significantly reduced life expectancy. As yet, there is no cure for individuals affected by these diseases. So, clinical manifestations and conservative treatment is important. This review aimed to highlight the extra-skeletal clinical problems in ML II and III.
Kim Hee-Soon;Shin Yeong-Hee;Oh Ka-Sil;Kim Tae-Im;Sim Mi-Kyung
Child Health Nursing Research
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v.11
no.4
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pp.415-426
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2005
Purpose: The purpose of this study was to identify relations among the parenting stress, maternal sensitivity to infant cues, parenting environment of first-time mothers. Method: The participants were 194 first-time mothers of babies aged 1-6 months who visited well-baby clinics in 5 hospitals. The data were collected from April 15 to June 15, 2003. Results: The parenting stress level was moderate with a mean score of 2.4(range 1-5). The parent domain and parent-child relationship domain of the parenting stress scale were significantly correlated with maternal sensitivity to infant feeding cues (r=-.178, p<.05; r=-.197, p<.01). Parenting stress was significantly correlated with childrearing environment(r=-2.19, p<.01). Parenting stress and childrearing environment were significantly different according to the educational level of the mothers and their prenatal care. Conclusions: Nursing interventions to reduce parenting stress in first-time mothers are needed to improve maternal sensitivity to infant cues and childrearing environment which foster infant development.
Purpose: The objective of this study was to investigate the relationship between fatigue, sleep disturbance, and gestational stress in women during late stage of pregnancy. Methods: This study was conducted with 113 healthy pregnant women at gestational age greater than 27 weeks who were registered at community health centers and received prenatal care. A structured questionnaire regarding fatigue, sleep disturbance, and gestational stress was used. The data was analyzed using a t-test, an ANOVA, and Pearson correlation coefficients. Results: The subjects with unplanned pregnancies and irregular exercise patterns showed a higher level of fatigue than those with planned pregnancies and regular exercise patterns. Pregnant women with caffeine intake manifested higher levels of gestational stress and sleep disturbance than those without. The levels of sleep disturbance and gestational stress increased as the fatigue levels increased. The fatigue levels increased with increased levels of sleep disturbance. Conclusion: Planned pregnancy, regular exercise patterns, and caffeine intake were related with fatigue, sleep disturbance, and gestational stress in women during late stages of pregnancy. Fatigue, sleep disturbance, and gestational stress had close associations to each other. In the future, such results should guide development of nursing intervention programs for women in late stages of pregnancy.
A study was conducted on a group of 107 women, attending the three peripheral community clinics in Seoul and Kyunggi area for their prenatal care, to ascertain the relationship between maternal serum zinc concentration measured in pregnancy and several pregnancy outcomes. The serum zinc concentration was adjusted for estimated gestational age at the time of drawing blood. Mean daily zinc intake of the pregnant women estimated by a 24-hour recall method was 7.68$\pm$3.70$\mu\textrm{g}$/dl, 51% of RDA. and mean serum zinc concentration of the women was 94.03$\pm$36.99ug/dl. Adjusted maternal serum zinc level was significantly related to gestational maternal weight gain(p<0.05) and infant birth weight(p<0.05). Pregnant women with tgreater than 9kg weight gain during the gestation period had higher adjusted serum zinc levels than the subjects with less than 8kg weight gain. Adjusted serum zinc levels of mothers who delivered 3.0-3.5kg and greater than 4.0kg birth-weight infants were higher than those of mothers of low-birth-weight infants. Any association between maternal serum zinc level and gestational length, complications and morning sickness was not observed. There results suggest that the maternal serum zinc level may predict perhaps the author could be none specific.
Purpose: The purpose of this study was to investigate the relationships among marital satisfaction, spousal support and practice of Taekyo among pregnant women. Methods: This study was conducted by the use of questionnaire surveys with two hundred and eighty-three pregnant women at several hospitals located in Gyeonggi province and Daejeon city from October 2008 to April 2009. Contents of questionnaire included marital satisfaction, spousal support and practice of Taekyo. Descriptive statistics, t-test, ANOVA, Pearson correlation, and stepwise multiple regression were conducted for data analysis using SPSS/WIN 17.0 program. Results: Degree of marital satisfaction, spousal support, and practice of Taekyo showed the high ranking among pregnant women. There was a significant difference in order of fetus, need for Taekyo, and time in Taekyo. There was a positive relationship between marital satisfaction, spousal support, and practice of Taekyo. The significant factors influencing the practice of Taekyo was connected with marital satisfaction, order of fetus and time in Taekyo. The total explanatory range was 29.3%. Conclusion: There is a need for multidimensional strategy in improving marital satisfaction. This study can be used as a foundation for maternal nursing education program and can be developed for practice of Taekyo.
Purpose: This study examined the influencing factors on antenatal depression among pregnant women. Methods: This was a cross sectional descriptive study with 255 pregnant women who visited a general hospital in a metropolitan city for their regularly scheduled check-up. Measurement tools employed were the Korean version of Beck Depression Inventory (BDI), the food habits, and the Pittsburg Sleep Quality Index (PSQI). Socio-demographic variables and the status of high risk pregnancy were identified. Influencing factors on antenatal depression were identified using a stepwise multiple regression analysis. Results: The mean score of antenatal depression was $7.2{\pm}5.0$; 18.4% with mild depression, 5.9% had moderate depression, with 0.8% identified with severe depression on BDI scale. Influencing factors on antenatal depression accounted for 47.8% of the total variance which consisted of quality of sleep, marital satisfaction, food habits, gestation periods, sexual satisfaction, high risk pregnancy, and age. Conclusion: Findings show that antenatal depression should be monitored on a regular basis during early pregnancy and in high risk pregnancy if possible, and quality of sleep and food habits should be incorporated in the management of antenatal depression.
Purpose: This study aimed to review recent findings from birth cohort studies on maternal and child environmental health. Methods: Birth cohort studies regarding environmental health outcomes for mothers and their children were investigated through a systematic review. A literature search was conducted in PubMed, CINAHL, the Cochrane Library, Embase, and RISS to identify published studies using the keywords using a combination of the following keywords: maternal exposure, environmental exposure, health, cohort, and birth cohort. Articles were searched and a quality appraisal using the Newcastle-Ottawa Scale for cohort studies was done. Results: A review of the 14 selected studies revealed that prenatal and early life exposure to environmental pollutants had negative impacts on physical, cognitive, and behavioral development among mothers and children up to 12 years later. Environmental pollutants included endocrine disruptors, air pollution (e.g., particulate matter), and heavy metals. Conclusion: This systematic review demonstrated that exposure to environmental pollutants negatively influences maternal and children's environmental health outcomes from pregnancy to the early years of life. Therefore, maternal health care professionals should take steps to reduce mothers' and children's exposure to environmental pollutants.
Purpose: This study aimed to identify the perceptions, importance, and performance of midwives' roles among midwives and nurses in Korea. Methods: A descriptive correlational design was employed. Data were collected from 164 nurses and 79 midwives from April 1 to June 25, 2021. Midwives enrolled in the Korean Midwifery Association and nurses and midwives from two hospitals each Daegu and Gyeonggi Province in Korea were invited to participate. The independent t-test, chi-square test, the Welch-Aspin test, and Pearson correlation coefficient were used for analysis. Results: The midwives' role perception score (3.47±1.46) was lower than that of nurses (3.95±0.85), and the midwives' role performance score (2.98±0.83) was also lower than that of nurses (3.34±0.89). Significant differences were observed between midwives and nurses in their perception and performance of roles related to prenatal management, childbirth management, management of psychological changes, postpartum management, and newborn care. Higher role perception and performance among midwives were linked to the management of psychological changes and women's health, indicating potential areas for future development. Conclusion: The study results suggest directions for developing new roles for midwives. It is necessary to find a way to expand the field of midwives in public health by benchmarking the roles of midwives in various countries.
A Pregnancy is the women's normal physiological and developmental process, in which many psychological changes including sexual problems always occur. But there have been few guidelines on sexual life during pregnancy. So this study was performed to evaluate the sexual life of pregnant women, and to analyze the factors affecting satisfaction of sexual life during pregnancy. Questionnaires were given to pregnant women who visited two general hospitals for antenatal care as well as to attendants at a prenatal Lamaze class. The results were as followings : 1) The average age of the 194 pregnant women was 28.5 years ; 98.4% of them had educated more than 12 years. ; the average monthly income was about 15,000,000 won ; primigravida women were 81.4% of the total cases. 2) As the pregnancy progressed, the frequency of the sexual intercourses was decreased in 48.5% because of the anxiety on the fetal damages. The was no significant differences between frequency of sexual intercourses and the degrees of physical discomfort and spouse intimacy. Man superior position was taken in 88.1% ; the incidence of orgasms before and during pregnancy were 71.1% and 41.1%, respectively ; the incidence of painful sexual intercourse in primigravida women was decreased by pregnancy in 4.6%, and in the case of multigravida women it was increased in 2.1%. 3) The average point of sexual knowledge was 11.5 in total points of 20 ; that of sexual attitude was 29.1 in total points of 40 ; that of sexual satisfaction was 28.5 in perfects points of 40. 4) The factors which significantly related to the satisfaction of sexual life were spouse intimacy, sexual attitude, change of sexual body position during pregnancy, and the orgasms before and during pregnancy. Considering above results, nursing care and nursing intervention including sexual education and counselling programs are needed during pregnancy as well as before pregnancy.
Journal of Family Resource Management and Policy Review
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v.10
no.1
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pp.17-32
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2006
This essay has attempted to document the actual behavior patterns and the social networks related to the child delivery in the pre-industrial Korean society. We interviewed 30 women who had given birth to their first child during the 1930s and the 1940s in order to accumulate data related to son-prayer rites, prenatal care and food avoidance, sacred-string culture, and other incantation rituals. The characteristics of the social relationships with the person who had assisted the delivery and the recovery were also analyzed in terms of kinship networks. The results are as follows. First, there was a big gap between knowledge and the actual practices in birth rituals and customs. We assume that this is due to the adverse social-economic conditions at that time which may have restricted the actual performances of these customs. Second, there were almost no differences of the performance of these' birth customs between the urban areas and the rural areas. Third, the people who assisted the delivery were women who were mostly from the husband's family. Help from the wife's family were quite exceptional. Finally, it has been found out that only about half of the women who were interviewed performed the well-known custom of three-week after-birth confinement.
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