• Journal of the Korean Child Neurology Society
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• v.25 no.3
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• pp.204-207
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• 2017

Hyperornithinemia-hyperammonemia-homocitrullinuria syndrome (HHH syndrome) is a neurometabolic disorder with highly variable clinical severity ranging from mild learning disability to severe encephalopathy. Diagnosis of HHH syndrome can easily be delayed or misdiagnosed due to insidious symptoms and incomplete biochemical findings, in that case, genetic testing should be considered to confirm the diagnosis. HHH syndrome is caused by biallelic mutations of SLC25A15, which is involved in the urea cycle and the ornithine transport into mitochondria. Here we report a boy with spastic paraplegia and asymptomatic younger sister who have compound heterozygous mutations of c.535C>T (p.R179^*) and c.116C>A (p.T39K) in the SLC25A15 gene. We identified that p.T39K mutation is a novel pathogenic mutation causing HHH syndrome and that p.R179^*, which is prevalent in Japanese and Middle Eastern heritage, is also found in the Korean population.

• Asia-Pacific Journal of Business Venturing and Entrepreneurship
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• v.7 no.2
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• pp.215-225
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• 2012

The purpose of this study was to examine the influential factors of the marital satisfaction of Korean couples and international couples and the impact of related variables involving marital equity and marital conflicts on marital satisfaction in a bid to give some suggestions on how to keep on leading a happy married life. A survey was conducted from July to September, 2010, and the answer sheets from 79 Korean couples and 79 international couples who numbered 316 were analyzed except for the incomplete answer sheets. The women of the international couples got the best mean scores. When the men and women of the international couples were compared, the women scored significantly higher than the men, which showed that the former group found themselves to put more investment in their marital relationship. Concerning ways of coping with marital conflicts in the groups, conflict intervention by oneself was most prevalent among the men of the international couples and least among the women of the Korean couples. Regarding sex-role attitude and communication, there were no significant differences in sex-role attitude. As to marital satisfaction, the men of the Korean couples got the highest mean scores, and the women of the international couples scored lowest. When the correlation analysis was conducted, the variable that had the closest correlation to marital satisfaction overall was positive problem solving by the spouse(.469), followed by conflict intervention by the spouse(-.453), positive problem solving by oneself(.451), the academic credential of the spouse(.443) and one's own retreat from conflict(-.409). As a result of making the regression analysis to find out which variables affected marital satisfaction, the most predictable variable was communication scores, followed by conflict intervention by the spouse, positive problem solving by oneself, one's own retreat from conflict, the academic credential of the spouse and psychoemotional equity.

• Journal of Korea Water Resources Association
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• v.55 no.10
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• pp.775-784
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• 2022

In this study, to determine the optimal order of the full-logged I-D-F polynomial equation, which is mainly used to calculate the probable rainfall over a temporal rainfall duration, the probable rainfall was calculated and the regression coefficients of the full-logged I-D-F polynomial equation was estimated. The optimal variable of the polynomial equation for each station was selected using a stepwise selection method, and statistical significance tests were performed through ANOVA. Using these results, the statistically appropriately calculated rainfall intensity equation for each station was presented. As a result of analyzing the variable selection outputs of the full-logged I-D-F polynomial equation at 9 stations in Gyeongbuk, the 1^st to 3^rd order equations at 6 stations and the incomplete 3^rd order at 1 station were determined as the optimal equations. Since the 1^st order equation is similar to the Sherman type equation and the 2^nd order one is similar to the general type equation, it was presented as a unified form of rainfall intensity equation for convenience of use by increasing the number of independent variables. Therefore, it is judged that there is no statistical problem in considering only the 3^rd order polynomial regression equation for the full-logged I-D-F.

• Journal of the Korean Geotechnical Society
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• v.23 no.11
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• pp.109-117
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• 2007

Uncertainty is pervasive in rock slope stability analysis due to various reasons and subsequently it may cause serious rock slope failures. Therefore, the importance of uncertainty has been recognized and subsequently the probability theory has been used to quantify the uncertainty since 1980's. However, some uncertainties, due to incomplete information, cannot be handled satisfactorily in the probability theory and the fuzzy set theory is more appropriate for those uncertainties. In this study the random variable is considered as fuzzy number and the fuzzy set theory is employed in rock slope stability analysis. However, the previous fuzzy analysis employed the approximate method, which is first order second moment method and point estimate method. Since previous studies used only the representative values from membership function to evaluate the stability of rock slope, the approximated analysis results have been obtained in previous studies. Therefore, the Monte Carlo simulation technique is utilized to evaluate the probability of failure for rock slope in the current study. This overcomes the shortcomings of previous studies, which are employed vertex method. With Monte Carlo simulation technique, more complete analysis results can be secured in the proposed method. The proposed method has been applied to the practical example. According to the analysis results, the probabilities of failure obtained from the fuzzy Monte Carlo simulation coincide with the probabilities of failure from the probabilistic analysis.

• Economic and Environmental Geology
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• v.30 no.6
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• pp.553-566
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• 1997

Origin, behavior and enrichment of environmental toxic elements from the Deokpyeong area were investigated on the basis of major, trace and rare earth element geochemistry. Coaly metapelites of the Deokpyeong area are subdivided into grey phyllite, dark grey phyllite, coaly slate and black slate, which are interbedded along the Ogcheon Supergroup. The coaly slate had been mined for coal, but mining is closed. The coaly and black slates are lower contents of $SiO_2$ and $Al_2O_3$, and higher contents of LOI, CaO, $Na_2O$ and BaO as compared with the phyllitic rocks. Rare earth elements are highly enriched in the coaly and black slate. Average compositions (ppm) of minor and/or environmental toxic elements in the coaly and black slate are revealed as As=127, Ba=30,163, Cd=18, Cr=740, Cu=84, Mo=378, Pb=43, Sb=12, Se=44, U=144, V=8,147 and Zn=292, which are extremely high concentrations than those in the NASC compositions. Major elements (average enrichment index; 5.34) in the coaly metapelites are mostly depleted, excepting $P_2O_5$ and BaO, normalized by NASC. Rare earth elements (average enrichment index; 1.48) are enriched in the coaly slate. On the basis of NASC, minor and/or environmental toxic elements in the coaly metapelites were strongly enriched of all the elements with the exception of Co, Cs, Ni and Sr. Average enrichment index of trace elements in coaly metapelite is 31.51 (coaly slate; 51.94 and black slate; 15.46). Especially, enrichment index of potentially toxic elements (As, Ba, Cr, Cu, Mo, Ni, Sb, Se, U, V and Zn) of the rock is 46.10 (grey phyllite; 7.15, dark grey phyllite; 4.77, coaly slate; 88.96 and black slate; 22.11). These coal formations were deposited in basin of boundary between terrestrial and marine environments deduced to carbon, sulfur (C/S=2.2 to 275.7), trace and rare earth elements characteristics. Irregular behavior and dispersion between major, minor and rare earth elements of those metapelites indicates a variable source materials, incomplete mixing of differential source and/or reequilibrium of diagenesis and metamorphism.

• Membrane Journal
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• v.17 no.3
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• pp.254-268
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• 2007

Sodium type faujasite(FAU) zeolite layers with diverse materials characteristics(Si/Al ratio, thickness, and structural discontinuity) were hydrothermally grown on a porous $\alpha-Al_2O_3$ tube, and then the $CO_2/N_2$ separation was evaluated at $30^{\circ}C$ for an equimolar mixture of $CO_2$ and $N_2$. Among hydrothermal conditions, $SiO_2$ content in hydrothermal solution seriously affected materials characteristics: with an increment in the $SiO_2$ content, Si/Al ratio, thickness, and structural discontinuity of grown FAU zeolite layer simultaneously increased. The present study reveals that structural discontinuity(intercrystalline voids due to an incomplete densification and cracks induced by GIS Na-P1 phase) is the most important variable affecting the $CO_2/N_2$ separation. Also, it was suggested that the $CO_2$ desorption in permeate side be the rate-determining(slowest) step in the overall $CO_2$ permeation.

• The Korean Journal of Zoology
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• v.33 no.4
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• pp.499-508
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• 1990

Surveys of elecirophoretic variations in isozymes and proteins encoded by 25 persumtive loci were conducted to estimate the degree of genic variation and to assess species recognition for three species of the Family Gasterosteidae (Pisces) in Korea. The average degree of genic variation of Gasterosteus aculeatus was HD = 0.086, HG = 0.084, and P =36% and it was similar to Pungitius sinensis (HD = 0.080, HG = 0.091, P = 29%). But P.kaibarae was less variable than these species (HD = 0.034; HG = 0.034, P = 13%). The average genetic similarities among the populations in each species of Gasterosteus aculeatus pungitius sinensis and P. kaibarae were S = 0.963, S = 0.953 and S = 0.800 respectively.Yongchon and Kyongiu populations of P. kaibarae were genetically remote from the rest of the conspecific populations (S = 0.690). Chae (1988) also observed morphological differences between them. The value of genetic similariiy coefficients of S = 0.606 between P. sinensis and P. kaibarae is low enough to consider as specific level of genetic difference, but moderate rate of hybridization (44%) between them at a synpatric area of Kangnung indicates that isolating mechanism is incomplete. Therefore it is concluded that P. sinensis and P. kaffarae are semispecitic status. Intergeneric genetic similarities between the genus Gasrerosteus and Pungitius were S = 0.052 and this value is the lowest estimate up to date in freshwater fishes.

• Journal of the Korean Society of School Health
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• v.12 no.1
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• pp.45-56
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• 1999

Adolescence is vulnerable to various Health Risk Behaviors (HRB). These behaviors can affect his remaining life as well as adolescence, thus prevention of HRB is a critical issue in health education. This study is aimed to provide basic information for prevention of HRB. Thus, this study was conducted to analyze the impact of peer group's health risk behaviors on health risk perception (HRP) and that of health risk perception on health risk behaviors based on 832 respondents. The 852 subjects were selected in six middle and high schools in Seoul through random sampling. Data were collected from September, 18-October, 21, 1998, and the 832 data were analyzed after excluding the 20 incomplete and inaccurate data. Questionnaire items and measures are based on an instrument to measure Perceived Health Risk Perception, which Hodge B.C. developed in 1992. Cronbach alpha is used to test the reliability. The reliability of HRP and HRB is 0.9473, 0.8768 in this study, Statistical analysis divided into four phases. First, the impact of socio-demographic characteristics on HRP is analyzed by oneway ANOV A. Male students have lower HRP than female students. As grade goes up, HRP is getting lower. Perceived higher concern of parents and HRP are correlated. And the experience of school health education and HRP are correlated. Second, the impact of peer group's HRB on the HRP is analyzed by linear regression. Peer group's HRB and HRP are negatively correlated, Third, the impact of HRP on HRB is analyzed by linear regression. There is a correlation between high HRP and low HRB. Fourth, Powerful impact factors on HRB are analyzed by stepwise multiple regression. Grade, gender, peer group's HRB, and related HRP is entered as independent variables. Because of correlation between entered variables, three interaction variables between grade, gender, peer group's HRB and related HRP also entered, In general, peer group's HRB is the most accountable factor to HRB. And Interaction variable between HRP and peer group's HRB and HRB are negatively correlated. These results indicate that HRP may reduce the impact of peer group's HRB on HRB. Some recommendations are as follows: First, health educational programs suitable for gender and grade are required. Second, a systematic cooperation between school and home is necessary for effective prevention of HRB. Third, the educational effect for decreasing HRB by increasing HRP is statistically assisted. However, peer group has much stronger impact on HRB than subjective HRP, thus special consideration and management are necessary for peer group which does HRB more frequently.

• Journal of the Korean Society of Hazard Mitigation
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• v.10 no.5
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• pp.75-82
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• 2010

To study the combustion characteristics of forest fuel by fire intensity, the experiment of combustion characteristics on Pinus Densiflora living leaves, which is the weakest species to the forest fire, was delivered, using variables of heat flux(25 kW/$m^2$, 50 kW/$m^2$, 75 kW/$m^2$). With the equipment of Cone calorimeter, the characteristics of ignition, heat, smoke release, CO and $CO_2$ release, and mass loss were analyzed. Pinus Densiflora living leaves containing moisture of 60.66% were not ignited at the heat flux of variables 25 kW/$m^2$, 50 kW/$m^2$, 75 kW/$m^2$. In proportion to the heat flux value, heat release amount and heat release rate reached maximum value rapidly: higher variables came to the maximum by the half rapidity and the maximum value were twice higher than the former lower variables respectively. As for the smoke release, the less heat flux the variable had, the more smoke release it had, due to incomplete combustion. The release amount of CO and $CO_2$ had more maximum value as the heat flux increased and more radiant heat meaned more carbon oxide. When the forest fire breaks out, therefore, a great amount of CO and $CO_2$ will be released by Pinus Densiflora.

• Journal of the Korea Academia-Industrial cooperation Society
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• v.19 no.7
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• pp.481-492
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• 2018

The steel-plate concrete composite beam is composed of a steel plate, concrete and shear connector to combine two inhomogeneous materials. In general, the steel plate is assembled by welding an existing composite beam. In this study, the SPC beam was composed of folding steel plates and concrete, without a headed stud. The folding steel plate was assembled by a high strength bolt instead of welding. To improve the workability in a field construction, a hat-shaped cap was attached to the junction with a slab. Monotonic load testing under two points was conducted under displacement control mode to analyze the flexural strength of the SPC beam using a cap as the shear connector. Five specimens with shear connector types, protrusion length, and different thickness of steel plates were constructed and tested. The experimental results were analyzed through the relationship between the shear strength ratio and flexural strength in KBC 2009. The test results showed a shear strength ratio of more than 40 %. In the case of using a cap-like specimen as the shear connector, the flexural strength was 70% of the value calculated as a fully composite beam. In addition, the cap showed a smaller shear strength than the stud, but the cap served as a shear connection. When the thickness of the steel plate was taken as a variable, the steel plate exhibited a bending strength of approximately 70% compared to a fully formed steel plate, and exhibited similar deformation performance. Local buckling occurred due to incomplete composite behavior, but local buckling occurred at a 5% higher strength for a relatively thick steel plate. The buckling width also decreased by 15%.