• The Journal of Korea Assosiation for Disability and Oral Health
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• v.11 no.2
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• pp.67-71
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• 2015

Prader-will syndrome (PWS) is a genetic disorder displayed with short stature and behavioral problems. The major manifestation is hyperphagia and obesity but there is no known effective drug that can solve this problem. This article presents a case report of a 3-year 9-month old girl affected with PWS syndrome treated under general anesthesia due to lack of cooperation and multiple caries. The dentist should work as a member of the multidisciplinary medical team. Careful long term follow up is required to prevent dental caries and periodontal diseases as well as maintain good oral hygiene. A strict diet control should also be encouraged.

• Childhood Kidney Diseases
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• v.9 no.1
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• pp.112-116
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• 2005

Our patient is the first reported case of Prader-Willi syndrome(PWS) with bilateral Hutch's diverticula. We believe that hypotonia in PWS is associated with multiple bladder diverticula and vesicoureteral reflux. We conclude that PWS can be considered a possible associated syndrome in patients with multiple bladder diverticula.

• Journal of Genetic Medicine
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• v.7 no.1
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• pp.45-52
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• 2010

Purpose: The objectives were to examine following 2 questions related to cognitive profile for the children with Williams syndrome (WS); 1) Is there a significant advantage for verbal IQ over performance IQ in WS?; 2) Is there selective impairment in visuospatial ability in the children with WS? Materials and Methods: Five children with WS with the age of $90.86{\pm}20.73$ months were compared with 12 children with Prader-Willi syndrome (PWS) or Down syndrome (DS) with comparable age and IQ. Results: All 5 children with WS showed intellectual disability whose mean scaled scores were $15.71{\pm}9.27$ in verbal subtests and $14.29{\pm}7.50$ in performance subtests, which did not show significant difference. There was no significant difference in the total sum of scaled scores of verbal subtests among WS, PWS and DS. There was no selective impairment in subtests which represented visuospatial tasks for the children with WS. However, the scaled score of object assembly was significantly lower in WS ($2.29{\pm}0.95$) compared to that of PWS ($4.75{\pm}2.77$; P <0.05). Conclusion: The general notion that the children with WS would be relatively strong in verbal function when compared with their overall cognitive function was not observed in this study. The verbal function of the children with WS was not better when compared to the children with DS or PWS. There was no selective impairment of visuospatial function in the children with WS at this age. However, the visuospatial function was significantly low in the children with WS only when compared to the children with PWS.

• Journal of mucopolysaccharidosis and rare diseases
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• v.3 no.2
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• pp.44-46
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• 2017

• BMB Reports
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• v.41 no.3
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• pp.248-253
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• 2008

Stresses and nutritional starvation are two main external signals for the induction of sex pheromones in the fission yeast Schizosaccharomyces pombe. In an attempt to identify the components involved in transduction of starvation signals, we screened 135 temperature-sensitive (ts) mutants and isolated 6 mutants that induced the pheromone even in the presence of a nitrogen source. These mutants exhibited two distict induction phenotypes: pheromone induction at restrictive but not at permissive temperatures; and pheromone induction at both permissive and restrictive temperatures. The times required for the maximum pheromone induction at the restrictive temperature differed slightly in each mutant. In addition to the pheromone induction phenotype, the ts243 and ts304 mutants exhibited cell-division-cycle defects. The ts304 mutant cells showed an abnormal cytoplasmic DAPI staining pattern. The nucleolus of this mutant seemed to be fragmented, a phenomenon which is typically observed in aged yeast cells. The result of our genetic analysis indicated that the pheromone induction mutants belonged to 6 separate complementation groups. We designated these mutants pws1 to pws6.

• Proceedings of the KIEE Conference
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• 1998.07g
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• pp.2351-2353
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• 1998

This paper suggests the wheel controller for PWS(Power Wheeled Steering) mobile robot. The proposed controller consists of two parts. To control each motor, the sliding mode controller implemented. This method has robustness about modeling error and disturbance, so the velocity tracking is well guaranteed in the presence of varying load. The design of a fuzzy cross-coupling controller for a PWS mobile robot is described here. Fuzzy cross-coupling control directly minimizes the tracking error by coordinating the motion of the two drive wheels. The fuzzy cross-coupling controller has excellent disturbance rejection and therefore is advantageous when the robot is not loaded symmetrically. The capability of the proposed controller was verified through the computer simulation.

• The Journal of Korea Assosiation for Disability and Oral Health
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• v.10 no.1
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• pp.26-30
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• 2014

Prader-Willi syndrome (PWS) is a rare neurodevelopmental disease caused by abnormality of chromosome 15q11-13. The estimated prevalence of PWS is 1/10,000-30,000. Most common features of this disease are feeding problems characterized by poor sucking habit related with neonatal or infantile hypotonia and obesity due to early childhood hyperphagia involved with lack of satiety. In the orodental findings, enamel hypoplasia, rampant caries, delayed eruption, poor oral hygiene, hypodontia, supernumerary teeth, increased tooth wear, decreased salivary flow and change in saliva composition were reported. This case report describes the dental treatment of 3-year-9-months-old male patient with PWS. Periodic check-ups and conservative treatments were followed, however, rapid dental caries progression caused by estimating hyposalivation was observed. Because of lack of patient cooperation, dental procedures were performed under general anesthesia.

• Phonetics and Speech Sciences
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• v.1 no.4
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• pp.195-201
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• 2009

The purpose of this study was to use high-speed digital imaging (HSDI) to compare vocal vibratory behaviors of persons who stutter (PWS) and persons with muscle tension dysphonia (PMTD) for uttering the /i/ vowel in a bid to identify the characteristics of vocal fold vibratory behaviors of PWS. This study surveyed seven developmental PWSs and seven PMTDs. The findings of the study indicated the following: first, regarding the two groups' vocal fold vibratory behaviors, of seven PWSs, three were found to be close vocal tract (VC) and four were found to be combination vocal tract (VCB). Of the seven PMTDs, one was found to be VC, and the other six were found to be VCB. These results indicate that a voiceprint which is different from the open vocal tract (VO) found in normal groups in research conducted by Jung, et al. (2008b) appeared in both groups of this study. Even between the two groups, there is a difference in the voiceprint before vocalization. Second, a VKG analysis was conducted to identify the two groups' vocal cord contact quotient. As a result, the PWS group's vocal cord contact quotient changed gradually from an irregular one at the initial vocalization stage to a regular one. The PMTD group continued the tension at the initial vocalization. Putting together all of these results, there is a difference in vocal fold vibratory behaviors between PWSs and PMTDs when they speak. Thus, there was a difference in muscular tension between the two groups.

• International Journal of Computer Science & Network Security
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• v.22 no.2
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• pp.272-282
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• 2022

Between 2014 and 2019, the US lost more than 2.1 billion USD to phishing attacks, according to the FBI's Internet Crime Complaint Center, and COVID-19 scam complaints totaled more than 1,200. Phishing attacks reflect these awful effects. Phishing websites (PWs) detection appear in the literature. Previous methods included maintaining a centralized blacklist that is manually updated, but newly created pseudonyms cannot be detected. Several recent studies utilized supervised machine learning (SML) algorithms and schemes to manipulate the PWs detection problem. URL extraction-based algorithms and schemes. These studies demonstrate that some classification algorithms are more effective on different data sets. However, for the phishing site detection problem, no widely known classifier has been developed. This study is aimed at identifying the features and schemes of SML that work best in the face of PWs across all publicly available phishing data sets. The Scikit Learn library has eight widely used classification algorithms configured for assessment on the public phishing datasets. Eight was tested. Later, classification algorithms were used to measure accuracy on three different datasets for statistically significant differences, along with the Welch t-test. Assemblies and neural networks outclass classical algorithms in this study. On three publicly accessible phishing datasets, eight traditional SML algorithms were evaluated, and the results were calculated in terms of classification accuracy and classifier ranking as shown in tables 4 and 8. Eventually, on severely unbalanced datasets, classifiers that obtained higher than 99.0 percent classification accuracy. Finally, the results show that this could also be adapted and outperforms conventional techniques with good precision.

• Korean Journal of Pharmacognosy
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• v.39 no.3
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• pp.199-202
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• 2008

A high performance liquid chromatographic (HPLC) method for the simultaneous determination of hesperidin and glycyrrhizin was established for the quality control of traditional herbal medicinal preparation, Pyungwi-san (PWS). Separation and quantification were successfully achieved with a Waters XTerra RP18 column ($5{\mu}m$, 4.6 mm I.D. ${\times}$ 150 mm) by gradient elution of a mixture of acetonitrile and water containing 0.03% phosphoric acid (pH 2.03) at a flow rate of 1.0 ml/min. The diode-array UV/vis detector (DAD) was used for the detection and the wavelength for quantification was set at 230 nm. The presence of hesperidin and glycyrrhizin in this extract was ascertained by retention time, spiking with each authentic standard and UV spectrum. All four compounds showed good linearity $(r^2>0.995)$ in a relatively wide concentration ranges. The R.S.D. for intra-day and inter-day precision was less than 7.0% and the limits of detection (LOD) were less than 60 ng. The mean recovery of each compound was 99.0-105.6% with R.S.D. values less than 4.0%. This method was successfully applied to the determination of contents of hesperidin and glycyrrhizin in three commercial products of PWS. These results suggest that the developed HPLC method is simple, effective and could be readily utilized as a quality control method for commercial PWS products.