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http://dx.doi.org/10.12655/KADH.2014.10.1.26

DENTAL MANAGEMENT OF A PATIENT WITH PRADER-WILLI SYNDROME : A CASE REPORT  

Lee, Myeong-Yeon (Department of Pediatric Dentistry, College of Dentistry, Yonsei University)
Jung, Younwook (Department of Pediatric Dentistry, College of Dentistry, Yonsei University)
Kim, Seong-Oh (Department of Pediatric Dentistry, College of Dentistry, Yonsei University)
Choi, Hyung-Jun (Department of Pediatric Dentistry, College of Dentistry, Yonsei University)
Son, Heung-Kyu (Department of Pediatric Dentistry, College of Dentistry, Yonsei University)
Lee, Hyo-Seol (Department of Pediatric Dentistry, College of Dentistry, Yonsei University)
Publication Information
The Journal of Korea Assosiation for Disability and Oral Health / v.10, no.1, 2014 , pp. 26-30 More about this Journal
Abstract
Prader-Willi syndrome (PWS) is a rare neurodevelopmental disease caused by abnormality of chromosome 15q11-13. The estimated prevalence of PWS is 1/10,000-30,000. Most common features of this disease are feeding problems characterized by poor sucking habit related with neonatal or infantile hypotonia and obesity due to early childhood hyperphagia involved with lack of satiety. In the orodental findings, enamel hypoplasia, rampant caries, delayed eruption, poor oral hygiene, hypodontia, supernumerary teeth, increased tooth wear, decreased salivary flow and change in saliva composition were reported. This case report describes the dental treatment of 3-year-9-months-old male patient with PWS. Periodic check-ups and conservative treatments were followed, however, rapid dental caries progression caused by estimating hyposalivation was observed. Because of lack of patient cooperation, dental procedures were performed under general anesthesia.
Keywords
Prader-Willi syndrome; Hereditary neuropathy; Dental management; Oral health;
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Times Cited By KSCI : 2  (Citation Analysis)
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