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http://dx.doi.org/10.12655/KADH.2015.11.2.67

DENTAL TREATMENT IN A PRADER-WILLI SYNDROME PATIENT : A CASE REPORT  

Lee, Soo Jeong (Division of Pediatric Dentistry, Department of Dentistry, Ajou University School of Medicine)
Baek, Kwangwoo (Division of Pediatric Dentistry, Department of Dentistry, Ajou University School of Medicine)
Publication Information
The Journal of Korea Assosiation for Disability and Oral Health / v.11, no.2, 2015 , pp. 67-71 More about this Journal
Abstract
Prader-will syndrome (PWS) is a genetic disorder displayed with short stature and behavioral problems. The major manifestation is hyperphagia and obesity but there is no known effective drug that can solve this problem. This article presents a case report of a 3-year 9-month old girl affected with PWS syndrome treated under general anesthesia due to lack of cooperation and multiple caries. The dentist should work as a member of the multidisciplinary medical team. Careful long term follow up is required to prevent dental caries and periodontal diseases as well as maintain good oral hygiene. A strict diet control should also be encouraged.
Keywords
Prader-willi syndrome; Dental caries; General anesthesia;
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