• Journal of Interdisciplinary Genomics
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• 제2권2호
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• pp.13-17
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• 2020

Infantile nystagmus syndrome (INS) is a genetically heterogeneous disorder. To date, more than 100 genes have been reported to cause INS and there is significant overlap in phenotypic characteristics. The most common form of X-linked INS is attributed to FRMD7 at Xq26. Recent advances in molecular genetics have facilitated the identification of pathogenic variants of FRMD7 and the investigation for underlying mechanisms of FRMD7-associated INS. This review summarizes genetic and clinical features of FRMD7-associated INS, and introduces updates on the pathogenesis of FRMD7 mutation.

• 대한전자공학회:학술대회논문집
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• 대한전자공학회 2005년도 추계종합학술대회
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• pp.61-64
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• 2005

본 연구에서는 $5mm{\times}7mm$ 크기의 적층 세라믹 SMD(surface mounted device)형 PECL VCXO에 테스트지그를 이용하여 스펙트럼을 분석한다. 패키지에 PECL 칩을 장착 후 와이어결선(wire bonding)을 완료한 VCXO는 그 길이 및 패키지 내부의 패턴 등에 의하여 부유인덕턴스(stray inductance) 및 커패시턴스가 발생하고, 칩의 발진부 임피던스에 영향을 준다. 이에 칩이 패키지에 장착된 상태에서 발진부 입력임피던스 영향을 제거하고 안정한 발진기 측정을 통하여 발진기의 정확한 스펙트럼 분석 및 성능을 평가한다.

• Journal of international Conference on Electrical Machines and Systems
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• 제3권4호
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• pp.415-421
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• 2014

In this paper, reactorless high efficiency boost DC/DC converter for EV is proposed. In proposed converter, improves efficiency because decrease power loss when the switches are turned on/off using zero current switching (ZCS) at all switch of primary full bridge. By replacing reactance ingredients of L-C resonance circuit for ZCS with leakage inductance ingredients of high frequency transformer, it reduces system size and expense because of not add special reactor. For validity verification of proposed converter, in the paper implements simulation using PSIM and perform experiment by making 5KW DC/DC converter. In experimental results, efficiency of proposed converter conformed superiority.

• Journal of international Conference on Electrical Machines and Systems
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• 제3권4호
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• pp.472-480
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• 2014

The In solar power system, the height and azimuth of the sun are important parameters which control generated power magnitude. The tracking method that controls the daily generation magnitude according to latitude and longitude using the two axles is often used in the existing sunlight tracking system today. In this two-axle PV track control system, the self-load is concentrated on one FRAME. It is influenced of the regular load, snow load and the wind load, etc. It is difficult to set up the system in the conventional building. This research is a development about the small-scale economy track device of independent load-dispersing solar generation system. The position tracking algorithm is through new coordinates transformation calculating the height and azimuth of the sun.

• 산업공학
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• 제15권2호
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• pp.147-151
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• 2002

Presented in this paper is a prototype of dedicated CAM system for a human bust, not a relief, machining. The input of this system is a STL file which comes from measuring machine, and the output is machining data for a 3-axis CNC milling machine with an index table. The system consists of three main modules, which are shape import and transformation, modeling of jig and fixture, and calculation of machining area. Proposed system architecture and the main modules are briefly described. To get machining region for semi-finish and finish machining stages, two concepts of machining area, machinable and scannable, were tried. Machinable area was suitable for the purpose.

• Journal of Welding and Joining
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• 제14권5호
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• pp.78-86
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• 1996

Vision sensor was used to track the weld line of the compressor case. The compressor case was fixed in jig equipped with the rotating system, and two torches having one degree of freedom was applied in automatic welding system. The radius of rotation for the compressor case is varying with each rotating angle, while, the angle velocity is constant Therefore, an algorithm to extract the feature of the compressor case for varying rotation angle is needed. To over come the avove difficulties, the curve fitting and composite curve were used. The experiment to verify the proposed algorithm showed desirable results for tracking the welding line of compressor case.

• 대한조선학회논문집
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• 제42권4호
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• pp.350-356
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• 2005

Prediction of green water loads acting on the bow deck is au essential part for the design of bow structures against the green water impact. Proper technique of the green water simulation is highly required for the prediction of green water loads. in this paper, the green water flow on bow deck is simulated by FDM(finite difference method). Using the results of green water simulation, impact load on bow deck is calculated. Also, experiments are carried out to compare with the numerical calculation. Through the comparisons between experimental results and numerical results, it is verified that the present numerical tool is adequate as a practical calculation tool for the green water problem.

• 대한치과교정학회지
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• 제24권1호
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• pp.87-94
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• 1994

The purpose of this study was to evaluate the torque effect of othodontic wires. Ten types of orthodontic wires (five types of materials, two types of cross-sectional dimensions) were selected. Each group of ire type was constituted with five specimens. These specimens were tested on the universal testing machine(Instron) with specially-designed jig. The torque-twist curve of each wire was obtained and the results were analyzed statistically. The results were as follows. 1. 0.017'$\times$ 0.025' wire showed more torque effect than 0.016'$\times$ 0.022' wire at the same twist. 2.Torque effect was the greatest in stainless steel and the least in Nitinol. 3.The maximum amount of torque was the greatest in heat-treated Blue Elgiloy and the least in Nitinol.

• Asia Pacific Journal of Business Review
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• 제2권1호
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• pp.1-20
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• 2017

The model of success in South Korea from a pariah state coming from the ruins of the Korean War into a member of the Organization for Economic Cooperation and Development (OECD) with a trillion dollar economy is encouraging. The Korean economic experience in terms of entrepreneurship and poverty reduction is an intriguing jig saw puzzle to researchers. This paper looks at Korean entrepreneurship history from the 1960s and how it shaped the contemporary sustainable economic development success of the Korean economy. Using a qualitative approach, the study used the Korean case study in comparison with Sub Saharan Africa to explore five powerful lessons on how the region can replicate the Korean entrepreneurship experience. The study shows that entrepreneurship was key to the radical transformation of its economy and government was instrumental in latent nurturing of Korean entrepreneurial spirit.

• 한국생산제조학회지
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• 제21권2호
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• pp.276-282
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• 2012

This study looked for Mode status of each for fatigue crack growth behavior about the repeat load of mode I and the static load of mode II. The experiment was performed in the state of the repetition frequency of the sine wave 10Hz, the stress ratio 0.1, maximum load 300kg.f, a static load 0, 100, 200, 300kg.f, As the experimental results, in mode of static load, while the load value increases, the crack growth rate is slower as the energy of a crack mixing grows. Mode I and the power mode II get an influence each other in the direction of crack propagation path, but as they eventually get closer to the breaking point of the crack growth, it is dominated by the mode I.