• Title/Summary/Keyword: congenital disease

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Family Stress, Perceived Social Support, and Coping of Mothers Who have a Child Newly Diagnosed with Congenital Heart Disease (선천성 심장병환아 어머니가 인지하는 가족 스트레스, 사회적 지지, 대처)

  • Tak Young-Ran
    • Child Health Nursing Research
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    • v.7 no.4
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    • pp.451-460
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    • 2001
  • Congenital heart disease is now estimated to be the most prevalent chronic illness in children. The overall purpose of study is to enhance our understanding of mother's perception of family stress, perceived social support, and coping who has a child newly diagnosed with congenital heart disease. In this investigation, the relationship between family stress, perceived social support, and coping within the context of a acute, non life- threatening chronic illness in the situation of newly diagnosed as Rolland's typology of chronic illness. The study employed data from a subset of a large longitudinal study, children's chronic illness: parents and family adaptation conducted by M. McCubbin (5 R29 NR02563) which was funded by the NIH. The subject for this study were 92 mothers who have a child under age 12 who was newly diagnosed with congenital heart disease within the last 3-4 months. Results form correlational and regression analysis revealed that perceived social support operated as a resiliency factor between family stress and coping of mothers. Child and family characteristics appeared to be important predictors of perceived social support and mother's coping. Therefore, the findings provide an incremental contribution to the explanation of effects for perceived social support and may challenge resiliency model in previous literature. Further, these findings suggest that perceived social support and coping are both influencing in the resiliency of relatively high risk groups of families who has a child with congenital heart disease.

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Tricuspid Valve Re-Repair in Ebstein Anomaly Using the Cone Technique

  • Kim, Do Jung;Suh, Jee Won;Shin, Yu Rim;Shin, Hong Ju;Park, Han Ki
    • Journal of Chest Surgery
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    • v.49 no.1
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    • pp.35-38
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    • 2016
  • The management of recurrent tricuspid regurgitation after tricuspid valve repair in patients with Ebstein anomaly is difficult, and tricuspid valve replacement is most commonly performed in such patients. We report two cases of recurrent tricuspid regurgitation in patients with Ebstein anomaly that were successfully re-repaired using the cone technique. The cone repair technique is a useful surgical method for reconstructing a competent tricuspid valve, and can be applied in patients who have undergone previous tricuspid valve repair.

Clinical Study of Congenital Diaphragmatic Diseases in Neonates and Infants (소아 횡격막 질환의 임상적 고찰)

  • Kim, Soo-Hong;Cho, Yong-Hoon;Ryu, Je-Ho
    • Advances in pediatric surgery
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    • v.16 no.2
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    • pp.143-153
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    • 2010
  • Congenital diaphragmatic disease is one of the common major congenital anomalies, and its mortality remained still high despite recent medical advances. The aim of this study is to examine the clinical characteristics of congenital diaphragmatic diseases. A total of 39 patients with congenital diaphragmatic disease that underwent surgery from January, 1997 to December, 2009 at Pusan National University Hospital were included in this study. Medical records were retrospectively reviewed. The male to female ratio was 30:9. Six out of 39 cases died (NS) before surgery, 17 patients had Bochdalek's hernia (BH), 11 patients hiatus hernia (HH), 4 diaphragmatic eventration (DE), and 1 Morgagni hernia (MH). There were no differences in mean birth weight and mean gestational age. NS (83.3 %). BH (35.3 %) was diagnosed more frequently than other diseases in the prenatal period. Three patients (17.6 %) of BH expired due to pulmonary hypoplasia and 1 patient had co-existing congenital heart disease. BH was diagnosed more frequently in the prenatal stage and had a higher motality rate than other conditions. Therefore, BH needs to be concentrated more than other anomalies.

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Clinical Evaluation of 111 Cases of Open Heart Surgery (개심술 111례에 대한 임상적 고찰)

  • 표현인
    • Journal of Chest Surgery
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    • v.24 no.9
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    • pp.870-880
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    • 1991
  • One hundred eleven cases of open heart surgery had been performed at the department of thoracic and cardiovascular surgery in College of Medicine Hallym Univ. from November 28, 1984 to August, 1991. There were 68 cases of congenital heart disease and 43 cases of acquired heart disease. Among the 68 cases of congenital heart diseases, 65 cases of acyanotic group and 3 cases of cyanotic group were noted. The majority of acquired heart diseases were valvular heart disease. The congenital heart disease consisted of 33 ASD, 27 VSD, 6 PS, 3 TOF. The sex ratio of congenital and acquired heart diseases was represented as 1.4: 1 and 1; 1.4 respectively. The age distribution of congenital heart diseases ranged from 11 months to 50 years old and that of acquired heart diseases from 15 to 61 years old. The overall operation mortality was 1 case[0.9%].

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The Clinical Experience of 1000 Cases in Open Heart Surgery (개심술 1000예의 임상적 고찰)

  • 정정기
    • Journal of Chest Surgery
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    • v.24 no.3
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    • pp.271-279
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    • 1991
  • From May 1977 to April 1990, 1000 cases of open heart surgery were performed under the cardiopulmonary bypass. There were divided into group A[500 cases, from May 1977 to June 23rd 1986] and group B[500 cases, from June 23rd 1986 to April 1990] which were analyzed, summarized, and compared. Of 1000 cases of open heart surgery, 677 cases[67.7%] were congenital heart diseases, and 323 cases[32.3%] were acquired heart diseases. In 677 cases of congenital heart disease, there were 545 cases with acyanotic congenital heart anomaly[A: 279, B: 266] and 132 cases with cyanotic congenital heart anomaly[A: 87, B: 45]. In 323 cases of acquired heart disease, most cases were valvular heart disease[315 cases, A: 133, B: 182] in which 357 valves were implanted. The operative mortality of congenital R acquired heart disease was 7.8% & 8.0%, and then overall mortality was 7.9%. The operative mortality was markedly decreased. [about half] from 10.0% of A group to 5.6% of B group.

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Pediatric Cardiothoracic CT Guideline Provided by the Asian Society of Cardiovascular Imaging Congenital Heart Disease Study Group: Part 2. Contemporary Clinical Applications

  • Hyun Woo Goo;Suvipaporn Siripornpitak;Shyh-Jye Chen;Oktavia Lilyasari;Yu-Min Zhong;Haifa Abdul Latiff;Eriko Maeda;Young Jin Kim;I-Chen Tsai;Dong Man Seo
    • Korean Journal of Radiology
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    • v.22 no.8
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    • pp.1397-1415
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    • 2021
  • The use of pediatric cardiothoracic CT for congenital heart disease (CHD) was traditionally limited to the morphologic evaluation of the extracardiac thoracic vessels, lungs, and airways. Currently, the applications of CT have increased, owing to technological advancements in hardware and software as well as several dose-reduction measures. In the previously published part 1 of the guideline by the Asian Society of Cardiovascular Imaging Congenital Heart Disease Study Group, we reviewed the prerequisite technical knowledge for clinical applications in a user-friendly and vendor-specific manner. Herein, we present the second part of our guideline on contemporary clinical applications of pediatric cardiothoracic CT for CHD based on the consensus of experts from the Asian Society of Cardiovascular Imaging CHD Study Group. This guideline describes up-to-date clinical applications effectively in a systematic fashion.

Congenital Cystic Adenomatoid Malformation of The Lung - A Case Report - (선천성 낭포성 선양기종: 1례 보고)

  • 김명인
    • Journal of Chest Surgery
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    • v.24 no.8
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    • pp.819-823
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    • 1991
  • The congenital cystic adenomatoid malformation of the lung is a rare disease, and is one of the most common congenital lung diseases which require prompt surgical intervention. The prognosis depends on its tissue type, prompt diagnosis and surgical intervention. The lesion consists of enlarged, variable sized multiple cyst with overgrowth of terminal bronchioles, like hamartoma. This disease can be associated with other vascular anomalies or other congenital defect especially in type II lesion We recently experienced one case of congenital cystic adenomatoid malformation The patient was 2 months old infant who showed respiratory distress without associated anomaly. After right upper lobe lobectomy, the patient was recovered uneventfully.

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Clinical Experience of Open Heart Surgery - Report of 152 Cases - (개심술 152예의 임강적 고찰)

  • Im, Seung-Gyun;Kim, Dong-Gwan
    • Journal of Chest Surgery
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    • v.25 no.2
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    • pp.167-175
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    • 1992
  • During a 4 year period from 1987 to 1991, 152 patients underwent open heart surgery for congenital heart disease and acquired heart disease. Over all operative mortality was 6.6%. There were 76 congenital anomalies consisting of 73 acyanotic and 3 cyanotic and 76 acquired heart disease. The age distribution of 152 cases was 3 months to 62 years. Mean age was 13.0 years in congenital heart anomalies and 38.9 years in acquired heart disease patients.

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Central-Approach Surgical Repair of Coarctation of the Aorta with a Back-up Left Ventricular Assist Device for an Infant Presenting with Severe Left Ventricular Dysfunction

  • Kim, Tae Hoon;Shin, Yu Rim;Kim, Young Sam;Kim, Do Jung;Kim, Hyohyun;Shin, Hong Ju;Htut, Aung Thein;Park, Han Ki
    • Journal of Chest Surgery
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    • v.48 no.6
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    • pp.407-410
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    • 2015
  • A two-month-old infant presented with coarctation of the aorta, severe left ventricular dysfunction, and moderate to severe mitral regurgitation. Through median sternotomy, the aortic arch was repaired under cardiopulmonary bypass and regional cerebral perfusion. The patient was postoperatively supported with a left ventricular assist device for five days. Left ventricular function gradually improved, eventually recovering with the concomitant regression of mitral regurgitation. Prompt surgical repair of coarctation of the aorta is indicated for patients with severe left ventricular dysfunction. A central approach for surgical repair with a back-up left ventricular assist device is a safe and effective treatment strategy for these patients.

Congenital Multiple Cystic Disease of Lung Report of A Case (선천성 다발성 폐낭종의 수술치험 1례)

  • Woo, Chong-Su;Seong, Si-Chan;Jeong, Hwang-Kiw
    • Journal of Chest Surgery
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    • v.12 no.2
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    • pp.89-92
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    • 1979
  • Congenital multiple cystic disease of the lung is a loosely knitted clinical group of disease and shows various clinical and laboratory findings. It is hard to find out definite differences between the bronchogenic cyst and congenital multiple cystic disease of the lung in the embryologic developing process but we can accept the idea, the embryologic developing process is similar one. An 18 years old female patient had left lower lobe bronchiectasis and Rt. Mid. and lower lobe congenital multiple cystic disease of the lung. In BNUH chest surgery department, we managed this patient successfully by doing staged bilateral lung lobar resection.

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