• Journal of Chest Surgery
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• 제43권4호
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• pp.450-453
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• 2010

선천성 낭종성 선종양 기형은 폐격리증과 같은 다른 동반된 기형 없이는 혈액공급을 폐동맥에서 받는 것으로 알고 있었으나, 저자들의 증례에서는 다른 기형이 동반되지 않은 단순 선천성 낭종성 선종양 기형이 영양동맥을 가지고 있었다. 술 전 영양동맥이 발견되지 않았어도 선천성 낭성 폐질환에서 영양혈관의 가능성에 유의하여야 할 것이다.

• Journal of Chest Surgery
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• 제13권1호
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• pp.1-12
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• 1980

In 1979 during the period of about 10 months 320 cases of open heart surgery were done in Seoul National University Hospital. There were 220 Congenital anomaly cases consisting of 113 acyanotic and 107 cyanotic varieties, and 1 O0 acquired cardiac lesions. Out of 100 acquired lesions 96 were valvular cues. Among 97 valve replacement cases 3 were Ebstein anomaly treated with plication and tricuspid valve replacement. Operative mortality rate for congenital anomaly was 10.6%, with 2.7% for acyanotic and 22.4% for cyanotic group. For acquired lesions over all operative mortality was 7%. Tetralogy of Fallot, ventricular septal defect, and atrial septal defect were the 3 main congenital anomalies, with 88 cues, 69 cases, and 27 cues respectively. In 61 simple ventricular septal defect without other anomalies operative mortality rate was 1.6%, in 27 atrial septal defect no death and, in tetralogy of Fallot 12.2%. Among 69 ventricular septal defect cases 19[27.5%] type I VSDs, after Kirklin-Becu classification, were found, rather high relative incidence of type I compared with Caucasian patients. Among 97 valve replacement cases 20 double valves were replaced-11 mitral with aortic and 9 mitral with tricuspid valves. Over all operative mortality rate for valve replacement was 8.2% with 3.3% in 61 mitral valve replace-merit. The over all operative mortality rate for 320 open heart surgery cases was 10.6%. Bubble type oxygenator and xenograft bioprosthetic valves were utilized In almost all cases.

• Journal of Korean Neurosurgical Society
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• 제29권3호
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• pp.402-406
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• 2000

The term 'craniovertebral junction' refers to the occipital bone that surrounds the foramen magnum and the atlas and the axis vertebrae. A wide variety of congenital, developmental, and acquired anomalies exist at the craniovertebral junction. The authors present a rare case of the congenital anomaly of the craniovertebral junction consisting of atlantal hypoplasia, atlantal assimilation, and basilar invagination in a 58-year-old male. An occiput-C2 arthrodesis was performed. The clinical and imaging features are described, and the embryology and etiology of this anomaly are discussed.

• Journal of Yeungnam Medical Science
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• 제5권2호
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• pp.101-110
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• 1988

영남대학교 의과대학 흉부외과학 교실에서는 1984년 4월부터 1988년 9월까지 459예의 심장혈관 환자들을 대상으로 수술하여 다음과 같은 성석을 얻었다. 1. 전 459예중 개심술이 355예였고 비개심술이 104예였다. 2. 환자의 연령은 최저 생후 1일에서 최고 65세까지였다. 3. 남녀비는 1:1.3으로 여자에서 조금 많은 분포를 보였다. 4. 개심술중 선천성 심장질환이 270예, 후천성 심질환이 85예로 선천성 심질환이 월등히 많았다. 5. 선천성 심장혈관 질환중 심실중격결손증이 38.7%로 가장 많았고 그 다음이 동맥관개존증, 심방중격결손증, 활로씨 사증후군, 폐동맥 협착증의 순이었다. 6. 수술후 합병증은 60예에서 관찰되었으나 전예에서 경쾌퇴원하였다. 7. 술후 사망은 전체 심장혈관 질환 459예중 15예로 3.3%를 보였고 개심술로 인한 사망은 355예중 14예로 3.9%였다.

• Journal of Chest Surgery
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• 제15권3호
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• pp.325-330
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• 1982

A case of a 7 year old girl with rare congenital anomalies is reported. The anomalies as called Cantrell`s pentalogy is consisted of defect in supraumbilical abdominal wall, ventral diaphragm, adjacent pericardium, and lower sternum associated with cardiac malformation. Her cardiac lesion was muscular diverticulum of left ventricle. The diverticulum was resected and the other defects were repaired successfully.

• Journal of Chest Surgery
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• 제20권3호
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• pp.630-634
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• 1987

Anomalies of the diaphragm, particularly eventration, are not encountered frequently in clinical practices. Diaphragmatic eventration is generally accepted as an anomaly high position of part or all of the diaphragm, usually associated with a marked decrease in muscle fibers and a membranous appearance of the abnormal area. We experienced 3 cases of the congenital diaphragmatic eventration at the department of the thoracic and cardiovascular surgery, Maryknoll Hospital, which were treated successfully.

• Journal of Chest Surgery
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• 제26권2호
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• pp.115-121
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• 1993

Between March, 1988 and July, 1992, 114 patients underwent Open Heart Surgery under hypothermic cardiopulmonary bypass. There were 29 cases of congenital heart anomalies (25％), and 85 cases of acquired heart diseases (75％) consisting of 53 cases of valvular heart disease, 31 cases of ischemic heart disease, and a case of left atrial myxoma. The age distribution of 114 cases was 4 to 73 years, and mean age was 43 years old consisting of mean age of congenital heart disease 23, valvular heart disease 47, and ischemic heart disease 57 years old. Overall operative mortality was about 7.9％.

• Journal of Chest Surgery
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• 제24권1호
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• pp.83-87
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• 1991

A unilateral pulmonary artery agenesis, which develops occasionally as one of the associated anomalies in congenital cardiovascular defect like as tetralogy of Fallot, is very rare anomaly as an isolated congenital defect. The diagnostic approach for the pulmonary artery agenesis is first suggested by the unique appearance of the involved lung on a routinely checked chest roentgenogram, because most patients are asymptomatic unless pulmonary infection had been superimposed. We have recently experienced a case of left pulmonary artery agenesis, which was diagnosed by perfusion scan, digital subtraction angiogram and then treated by left pneumonectomy in a 9 year-old boy, and presented hereby with the review of relevant literature.

• Journal of Korean Neurosurgical Society
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• 제64권3호
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• pp.380-385
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• 2021

Caudal agenesis refers to the congenital malformation with the essential feature of the agenesis of the sacrococcygeal bone. It is associated with various types of spinal cord anomaly as well as with complex anomalies of genitourinary or gastrointestinal system. The wide spectrum of the disease can be attributed to its pathoembryological origin, the secondary neurulation. This review presents the definition, etiology, classification, and clinical features of the disease.

• Journal of Korean Neurosurgical Society
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• 제37권1호
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• pp.29-33
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• 2005

Objective: Congenital dermal sinus is a rare congenital disease that results from the failure of the neuroectoderm to separate from the surface ectoderm during the process of neurulation, where there is communication between the skin and the deeper structures. Their pathogenesis, clinical course and treatment strategy are well known. We analyze our series and compare our results with other series. Methods: Twenty patients were diagnosed as congenital dermal sinus and confirmed pathologically from October 1986 to July 2003 at our hospital. We studied the patients' clinical manifestations, radiological findings and pathological profiles. Results: Seven cases were located in the suboccipital area and 13 cases were located in the spinal area. Interestingly, 4 of 13 spinal lesion cutaneous openings were located lower than the 3rd sacral body level. 8 of 20 lesions were terminated at neural structures, 4 of 20 lesions were terminated at the intradural portion and others terminated at the extradural portion. Nine anomalies were combined with the dermal sinus, including 4 lipomas, 2 Currarino's triad, 1 encephalocele, 1 myelomeningocele and 1 diastematomyelia. Eleven patients had dermoid tumors. Conclusion: Congenital Dermal Sinus must be surgically removed immediately if they are diagnosed. The surgical procedure of congenital dermal sinus is complete removal, but in some cases, complete removal is impossible. In those cases, we removed all epithelial tissues. We consider sacrococcygeal dimple almost invariably have no connection with intraspinal structures. But, if other cutaneous manifestations are combined with cutaneous pits, it can communicate with the sacrococcygeal dimple.