[KSCI] Korea Science Citation Index Service

http://dx.doi.org/10.3340/jkns.2021.0025

Caudal Agenesis : Understanding the Base of the Wide Clinical Spectrum

Lee, Ji Yeoun (Division of Pediatric Neurosurgery, Seoul National University Children's Hospital)
Shim, Youngbo (Division of Pediatric Neurosurgery, Seoul National University Children's Hospital)
Wang, Kyu-Chang (Neuro-oncology Clinic, Center for Rare Cancers, National Cancer Center)

Publication Information

Journal of Korean Neurosurgical Society / v.64, no.3, 2021 , pp. 380-385 More about this Journal

Abstract

Caudal agenesis refers to the congenital malformation with the essential feature of the agenesis of the sacrococcygeal bone. It is associated with various types of spinal cord anomaly as well as with complex anomalies of genitourinary or gastrointestinal system. The wide spectrum of the disease can be attributed to its pathoembryological origin, the secondary neurulation. This review presents the definition, etiology, classification, and clinical features of the disease.

Keywords

Caudal agenesis; Sacral agenesis; Caudal regression syndrome; Congenital abnormalities; Spinal dysraphism;

Citations & Related Records

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