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http://dx.doi.org/10.7318/KJFC/2022.37.4.363

A Study on the Dietary Behaviors and Nutritional Statuses of Children with Galactosemia in Korea  

Seo, Hye Ji (Department of Nutritional Science and Food Management, Ewha Womans University)
Jeong, Yeseung (Department of Nutritional Science and Food Management, Ewha Womans University)
Kim, Yuri (Department of Nutritional Science and Food Management, Ewha Womans University)
Oh, Jieun (College of Science and Industry Convergence, Ewha Womans University)
Publication Information
Journal of the Korean Society of Food Culture / v.37, no.4, 2022 , pp. 363-375 More about this Journal
Abstract
Galactosemia is a rare, hereditary metabolic disorder caused by the accumulation of galactose and its metabolites in the body due to a lack of enzymes that convert galactose to glucose. This study aimed to investigate the dietary behaviors and nutritional statuses of patients with galactosemia and to provide basic information on the development of nutrition education programs to improve quality of dietary life. A survey was conducted on 13 parents of (<11 years of age) children with galactosemia and 26 parents of (<11 years of age) children without galactosemia. Mean body mass index was greater for school-age children with galactosemia (18.77 kg/m2) than for corresponding normal children (16.55 kg/m2). Underweight and obesity rates of children with galactosemia were greater than those of children without galactosemia. In addition, children with galactosemia had a higher food neophobia rate and thus consumed less food. Normal children exhibited a greater range of food preferences than those with galactosemia, especially for milk and dairy products (p= .001) and fats and sweets (p= .04). Reliable food databases and appropriate dietary recommendations are required to ensure the proper growth of children with galactosemia.
Keywords
Galactosemia; rare metabolic disease; dietary behavior; nutritional status;
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Times Cited By KSCI : 8  (Citation Analysis)
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