Annals of Clinical Neurophysiology

The Korean Society of Clinical Neurophysiology (대한임상신경생리학회)
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Isolated facial diplegia variant of Guillain-Barré syndrome with anti-GM1 IgG antibody

  • Jung, Jin Ho (Department of Neurology, Busan Paik Hospital, Inje University College of Medicine) ;
  • Lee, Sukyoon (Department of Neurology, Busan Paik Hospital, Inje University College of Medicine) ;
  • Seo, Jung Hwa (Department of Neurology, Busan Paik Hospital, Inje University College of Medicine) ;
  • Bae, Jong Seok (Department of Neurology, Hallym University College of Medicine) ;
  • Shin, Kyong Jin (Department of Neurology, Inje University Haeundae Paik Hospital) ;
  • Kim, Jong Kuk (Peripheral Neuropathy Research Center, Dong-A University College of Medicine) ;
  • Yoon, Byeol-A (Peripheral Neuropathy Research Center, Dong-A University College of Medicine) ;
  • Oh, Seong-il (Department of Neurology, Busan Paik Hospital, Inje University College of Medicine)
  • Received : 2021.09.27
  • Accepted : 2021.12.01
  • Published : 2022.04.30
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Abstract

Facial diplegia (FD) rarely occurs as a regional Guillain-Barré syndrome (GBS) variant. A 70-year-old male presented with bifacial weakness that had started on the left side and extended to the right after several days. He was then treated using steroids and gradually improved. Serum antiganglioside antibody testing revealed positivity for anti-GM1 IgG antibodies. FD can be idiopathic, but it is an uncommon GBS variant. The ganglioside antibody test may increase the possibility of diagnosing isolated FD.

Keywords

Acknowledgement

This study was supported by the National Research Foundation of Korea (NRF) grant funded by the Korea government (MIST) (No. 2020R1G1A1008446 and 2016R1A5A2007009).

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