Journal of Korean Neurosurgical Society

The Korean Neurosurgical Society (대한신경외과학회)
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Globus Pallidus Interna Deep Brain Stimulation for Chorea-Acanthocytosis

  • Lee, Jae-Hyeok (Department of Neurology, Pusan National University School of Medicine) ;
  • Cho, Won-Ho (Department of Neurosurgery, Pusan National University School of Medicine) ;
  • Cha, Seung-Heon (Department of Neurosurgery, Pusan National University School of Medicine) ;
  • Kang, Dong-Wan (Department of Neurosurgery, Pusan National University School of Medicine)
  • Received : 2014.02.26
  • Accepted : 2014.05.13
  • Published : 2015.02.28
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Abstract

Chorea-acanthocytosis (ChAc) is a rare hereditary disorder characterized by involuntary choreiform movements and erythrocytic acanthocytosis. Pharmacotherapy for control of involuntary movements has generally been of limited benefit. Deep brain stimulation (DBS) has recently been used for treatment of some refractory cases of ChAc. We report here on the effect of bilateral high-frequency DBS of globus pallidus interna in a patient with ChAc.

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References

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