Tuberculosis and Respiratory Diseases

The Korean Academy of Tuberculosis and Respiratory Diseases (대한결핵및호흡기학회)
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A Case of Malignant Rhabdoid Tumor in the Anterior Mediastinum

전종격동에서 발생한 악성 횡문근양 종양 1예

  • Oh, Kyung Jin (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Lee, Ki Byung (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Hong, Soon Won (Department of Pathology, Yonsei University College of Medicine) ;
  • Jung, Kyo Tae (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Choi, Hong Kyu (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Kim, Hyung Jung (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Ahn, Chul Min (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Chang, Yoon Soo (Department of Internal Medicine, Yonsei University College of Medicine)
  • 오경진 (연세대학교 의과대학 내과학교실) ;
  • 이기병 (연세대학교 의과대학 내과학교실) ;
  • 홍순원 (연세대학교 의과대학 진단병리학교실) ;
  • 정교태 (연세대학교 의과대학 내과학교실) ;
  • 최홍규 (연세대학교 의과대학 내과학교실) ;
  • 김형중 (연세대학교 의과대학 내과학교실) ;
  • 안철민 (연세대학교 의과대학 내과학교실) ;
  • 장윤수 (연세대학교 의과대학 내과학교실)
  • Received : 2009.09.01
  • Accepted : 2009.09.28
  • Published : 2009.11.30
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Abstract

Malignant rhabdoid tumors arise primarily from the kidney. Extrarenal malignant rhabdoid tumors are rare, with the liver, central nervous system, and skin reported as the primary sites. Malignant rhabdoid tumors of the mediastinum are extremely rare among extrarenal malignant rhadoid tumors; only 3 cases have been reported to date, all characterized by aggressive clinical behavior. We experienced a 35-year-old woman diagnosed with malignant rhabdoid tumor in the anterior mediastinum with multiple metastases. The tumor was surgically unresectable, and treated with palliative radiation therapy. Three-month after radiation treatment, she died from dissemination of the malignant rabdoid tumor.

Keywords

References

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Cited by

  1. Malignant Rhabdoid Tumor of the Mediastinum: A Case Report and Literature Review vol.9, pp.7, 2009, https://doi.org/10.25259/jcis-9-7