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http://dx.doi.org/10.4046/trd.2009.67.5.462

A Case of Malignant Rhabdoid Tumor in the Anterior Mediastinum  

Oh, Kyung Jin (Department of Internal Medicine, Yonsei University College of Medicine)
Lee, Ki Byung (Department of Internal Medicine, Yonsei University College of Medicine)
Hong, Soon Won (Department of Pathology, Yonsei University College of Medicine)
Jung, Kyo Tae (Department of Internal Medicine, Yonsei University College of Medicine)
Choi, Hong Kyu (Department of Internal Medicine, Yonsei University College of Medicine)
Kim, Hyung Jung (Department of Internal Medicine, Yonsei University College of Medicine)
Ahn, Chul Min (Department of Internal Medicine, Yonsei University College of Medicine)
Chang, Yoon Soo (Department of Internal Medicine, Yonsei University College of Medicine)
Publication Information
Tuberculosis and Respiratory Diseases / v.67, no.5, 2009 , pp. 462-466 More about this Journal
Abstract
Malignant rhabdoid tumors arise primarily from the kidney. Extrarenal malignant rhabdoid tumors are rare, with the liver, central nervous system, and skin reported as the primary sites. Malignant rhabdoid tumors of the mediastinum are extremely rare among extrarenal malignant rhadoid tumors; only 3 cases have been reported to date, all characterized by aggressive clinical behavior. We experienced a 35-year-old woman diagnosed with malignant rhabdoid tumor in the anterior mediastinum with multiple metastases. The tumor was surgically unresectable, and treated with palliative radiation therapy. Three-month after radiation treatment, she died from dissemination of the malignant rabdoid tumor.
Keywords
Rhabdoid Tumor; Mediastinum;
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