Childhood Kidney Diseases

Korean Society of Pediatric Nephrology (대한소아신장학회)
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A Case about Cyclosporine Treatment of Kimura's Disease Associated with Steroid Dependant Nephrotic Syndrome

스테로이드 의존형 신증후군과 동반된 기무라병에서 cyclosporine 치료 경험

  • Do, Young-Sun (Department of Pediatrics and Adolescent Medicine, Wonju Christian Hospital Yonsei University Wonju College of Medicine) ;
  • Kim, Hak-Yong (Department of Pediatrics and Adolescent Medicine, Wonju Christian Hospital Yonsei University Wonju College of Medicine) ;
  • NamGoong, Mee-Kyung (Department of Pediatrics and Adolescent Medicine, Wonju Christian Hospital Yonsei University Wonju College of Medicine)
  • 도영선 (연세대학교 원주의과대학 소아청소년과) ;
  • 김학용 (연세대학교 원주의과대학 소아청소년과) ;
  • 남궁미경 (연세대학교 원주의과대학 소아청소년과)
  • Published : 2009.10.31
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Abstract

Kimura's disease is a chronic inflammatory disorder of unknown etiology. A 14 year old boy suffering from steroid dependant nephrotic syndrome, was presented with relapsing painless subcutaneous masses on the left buccal area. Blood analysis showed increased IgE and eosinophilia. During 4 years follow up, he was been treated by low dose steroid and short term cyclosporine. Consequently, frequent relapses of subcutaneous masses and nephrotic syndrome has been relieved. Cyclosporine treatment combined with steroid may be useful for preventing frequent relapse of Kimura's disease.

저자들은 스테로이드 의존형 신증후군 환자에서 진단 8년 만에 두경부 종물이 발생, 혈액 검사상 IgE 증가와 호산구 증가, 경부 컴퓨터 단층 촬영으로 기무라병을 진단하였고, 스테로이드로 치료하였으며, cyclosporine을 투여한 이후 장기간 두경부 종물과 신증후군의 재발을 억제할 수 있었기에 문헌고찰과 함께 보고하는 바이다.

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References

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