Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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One Stage Repair of Berry Syndrome in a Neonate Using an Autologous Arterial Flap

신생아에서 Berry 증후군의 자가동맥 피판을 이용한 일차 완전교정술

  • Park, Chin-Su (Department of Thoracic and Cardiovascular Surgery, School of Medicine, Pusan National University) ;
  • Sung, Si-Chan (Department of Thoracic and Cardiovascular Surgery, School of Medicine, Pusan National University) ;
  • Chang, Yoon-Hee (Department of Thoracic and Cardiovascular Surgery, School of Medicine, Pusan National University) ;
  • Lee, Hyoung-Doo (Department of Pediatrics, School of Medicine, Pusan National University) ;
  • Son, Song-Su (Department of Thoracic and Cardiovascular Surgery, School of Medicine, Pusan National University) ;
  • Kim, Young-Kyu (Department of Thoracic and Cardiovascular Surgery, School of Medicine, Pusan National University)
  • 박진수 (부산대학교 의학전문대학원 흉부외과학교실) ;
  • 성시찬 (부산대학교 의학전문대학원 흉부외과학교실) ;
  • 장윤희 (부산대학교 의학전문대학원 흉부외과학교실) ;
  • 이형두 (부산대학교 의학전문대학원 소아과학교실) ;
  • 손봉수 (부산대학교 의학전문대학원 흉부외과학교실) ;
  • 김영규 (부산대학교 의학전문대학원 흉부외과학교실)
  • Published : 2008.08.05
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Abstract

Berry syndrome (a distal aortopulmonary window and a right pulmonary artery originating from the ascending aorta, an intact ventricular septum, a patent ductus arteriosus and an interrupted aortic arch) is a rare complex congenital cardiac malformation. We describe a case of one stage repair with using an autologous arterial flap in a 19-day-old neonate who was suffering with this malformation, and we report on the development of postoperative right pulmonary artery stenosis and its successful management with performing multiple balloon angioplasties.

원위부 대동맥-폐동맥창, 우폐동맥 대동맥기시, 온전한 심실중격결손, 개방성동맥관, 대동맥궁차단으로 구성된, 소위 Berry syndrome이라고 불리는 이 기형은 매우 드문 복잡 심기형이다. 생후 19일된 신생아에서 자가동맥 피판을 이용한 일차 완전교정술과 추적관찰에서 발생한 우폐동맥 협착 및 그의 풍선성형술에 의한 성공적 치료를 문헌고찰과 함께 보고한다.

Keywords

References

  1. Berry TE, Bharati S, Muster AJ, et al. Distal aortopulmonary septal defect, aortic origin of the right pulmonary artery, intact ventricular septum, patent ductus arteriosus and hypoplasia of the aortic isthmus: a newly recognized syndome. Am J Cardiol 1982;49:108-16. https://doi.org/10.1016/0002-9149(82)90284-3
  2. Jeong YS, Song MG. Distal type of aortopulmonary septal defect with aortic origin of right pulmonary artery and interrupted aortic arch a case of successful surgical report. Korean J Thorac Cardiovac Surg 1991;24:693-700.
  3. Lee HC, Ryu HY, Jung TE, et al. One stage repair of distal aortopulmonary septal defect, aortic origin of right pulmonary artery, patent ductus arteriosus and hypoplasia of aortic isthmus a case report. Korean J Thorac Cardiovac Surg 1996;29:554-8.
  4. Choi CH, Kim WH, Kwak JG, et al. One stage repair of Berry syndrome in a neonate. Korean J Thorac Cardiovac Surg 2004;37:918-21.
  5. Burke RP, Rosenfeld HM. Primary repair of aortopumonary septal defect, interrupted aortic arch and anomalous origin of the right pulmonary artery. Ann Thorac Surg 1994;58: 543-5. https://doi.org/10.1016/0003-4975(94)92250-0
  6. Chiu I, Wu S, Lee M. One stage repair of interrupted aortic arch and aortopulmonary window with an autologous arterial flap. J Card Surg 1999;14:306-9. https://doi.org/10.1111/j.1540-8191.1999.tb00999.x