Multiple Cardiac Papillary Fibroelastoma of the Aortic Valve

대동맥 판막에 위치한 다발성 심장 유두상 섬유탄력종

  • Seo, Hong-Joo (Department of Thoracic and Cardiovascular Surgery, Chosun University College of Medicine) ;
  • Na, Chan-Young (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute) ;
  • Yu, Jai-Kun (Department of Thoracic and Cardiovascular Surgery, Chosun University College of Medicine)
  • 서홍주 (조선대학교 의과대학 흉부외과학교실) ;
  • 나찬영 (부천세종병원 흉부외과) ;
  • 유재근 (조선대학교 의과대학 흉부외과학교실)
  • Published : 2008.08.05

Abstract

Cardiac papillary fibroelastomas are the second most common primary cardiac tumor. This tumor is usually benign and it involves the cardiac valve. However, most cardiac papillary fibroelastomas originate from a single site, and the incidence of cardiac papillary fibroelastomas originating from multiple sites is very rare (5%). A 55-year-old woman who presented with momentary dizziness and syncope was evaluated by performing echocardiography. Multiple tumors attached to the aortic valve were noted. The mass was removed freely without leaving any defect on the aortic valve leaflet. After the recovery period, the patient is currently being followed up at the outpatient department.

심장 유두상 섬유탄력종은 원발성 종양 중 두 번째로 많이 호발하는 양성종양으로 주로 심장판막에 발생한다. 그러나 대부분 한곳에서 발생하며 다발성으로 발생하는 경우는 전체 심장 유두상 섬유탄력종의 5%로 아주 드문 경우이다. 55세 여자가 내원 10일전부터 발생한 순간적인 어지러움 및 실신으로 내원 시 검사한 심초음파상 대동맥 판막에 부착된 다발성 종양이 발견되어 수술 시행하였으며, 대동맥 판막의 손상 없이 대동맥 판막에 부착된 종양만 제거하였고, 환자 퇴원 후 외래 추적 관찰 중이다.

Keywords

References

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