Aortic Translocation for Complete Transposition of the Great Arteries with a Ventricular Septal Defect and Pulmonic Stenosis

심실 중격 결손과 폐동맥 협착을 동반한 완전 대혈관 전위에서 대동맥 전위술

  • Jeong, In-Seok (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Institute) ;
  • Lee, Chang-Ha (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Institute) ;
  • Lee, Cheul (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Institute) ;
  • Lim, Hong-Gook (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Institute) ;
  • Kim, In-Sub (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Institute) ;
  • Youn, Hyo-Chul (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Institute)
  • 정인석 (부천세종병원 흉부외과, 세종심장연구소) ;
  • 이창하 (부천세종병원 흉부외과, 세종심장연구소) ;
  • 이철 (부천세종병원 흉부외과, 세종심장연구소) ;
  • 임홍국 (부천세종병원 흉부외과, 세종심장연구소) ;
  • 김인섭 (부천세종병원 흉부외과, 세종심장연구소) ;
  • 윤효철 (부천세종병원 흉부외과, 세종심장연구소)
  • Published : 2008.08.05

Abstract

The Rastelli operation has been a standard procedure for repairing complete transposition of the great arteries combined with a ventricular septal defect and pulmonary stenosis. Yet this procedure has several shortcomings, including the risk of incurring left ventricular outflow tract obstruction on long-term follow-up. In this regard, aortic translocation has recently been regarded as a potent alternative to Rastelli's operation. We report here on a case of complete transposition of the great arteries that was combined with an inlet-extended perimembranous ventricular septal defect and pulmonary stenosis in a 2-year-old boy. All the problems were successfully repaired using the aortic translocation technique. Postoperative echocardiography showed a straight and wide left ventricular outflow tract.

심실 중격 결손과 폐동맥 협착을 동반한 완전 대혈관 전위를 갖는 환자에서 기존의 Rastelli수술법의 만족스럽지 않은 장기 결과가 보고되는 반면, 최근 들어 대동맥 전위술은 이 질환에서 유용한 수술방법으로 보고되고 있다. 본 증례는 우심실 유입부로 연장된 막성주위형 심실중격결손과 폐동맥 협착을 동반한 완전 대혈관 전위로 진단되어 과거에 체폐단락술을 받았던 2세 남자 환아(체중 9.6 kg)에서 우심실에서 분리한 대동맥 근부를 후방의 좌심실쪽으로 전위시켜 좌심실 유출로 재건술을 시행하고, 판막 도관을 이용하여 우심실 유출로 재건술을 시행하였다. 수술 후 시행한 심초음파 검사에서 양호한 혈역학적 소견을 보여 문헌 고찰과 함께 증례 보고를 한다.

Keywords

References

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