Tuberculosis and Respiratory Diseases

The Korean Academy of Tuberculosis and Respiratory Diseases (대한결핵및호흡기학회)
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Localized Fibrosing Mediastinitis with Superior Vena Caval(SVC) Syndrome

국소적 섬유화 세로칸염에 의해 유발된 상대정맥증후군 1예

  • Shin, Sang Yun (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital) ;
  • Kim, Beom Kyung (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital) ;
  • Park, Byung Hoon (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital) ;
  • Park, Seon Cheol (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital) ;
  • Park, Jun Chul (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital) ;
  • Soon, Myoung Kyun (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital) ;
  • Lee, Seung Yul (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital) ;
  • Im, Eui (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital) ;
  • Jeon, Han Ho (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital) ;
  • Jung, Kyung Soo (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital) ;
  • Jeong, Jae Heon (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital) ;
  • Choi, Yu Ri (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital) ;
  • Kang, Kyoung Hoon (Department of Thoracic surgery, National Health Insurance Corporation Ilsan Hospital) ;
  • Choi, Yoon Jung (Department of Pathology, National Health Insurance Corporation Ilsan Hospital) ;
  • Hong, Yong Kook (Department of Radiology, National Health Insurance Corporation Ilsan Hospital) ;
  • Kim, Chong Ju (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital)
  • 신상윤 (국민건강보험공단 일산병원 내과) ;
  • 김범경 (국민건강보험공단 일산병원 내과) ;
  • 박병훈 (국민건강보험공단 일산병원 내과) ;
  • 박선철 (국민건강보험공단 일산병원 내과) ;
  • 박준철 (국민건강보험공단 일산병원 내과) ;
  • 손명균 (국민건강보험공단 일산병원 내과) ;
  • 이승률 (국민건강보험공단 일산병원 내과) ;
  • 임의 (국민건강보험공단 일산병원 내과) ;
  • 전한호 (국민건강보험공단 일산병원 내과) ;
  • 정경수 (국민건강보험공단 일산병원 내과) ;
  • 정재헌 (국민건강보험공단 일산병원 내과) ;
  • 최유리 (국민건강보험공단 일산병원 내과) ;
  • 강경훈 (국민건강보험공단 일산병원 흉부외과) ;
  • 최윤정 (국민건강보험공단 일산병원 병리과) ;
  • 홍용국 (국민건강보험공단 일산병원 영상의학과) ;
  • 김정주 (국민건강보험공단 일산병원 내과)
  • Received : 2007.08.07
  • Accepted : 2007.09.07
  • Published : 2007.10.30
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Abstract

Fibrosing mediastinitis is a rare disease that is characterized by the proliferation of dense fibrous tissue of the mediastinum. The pathogenesis of fibrosing mediastinitis is unknown in most cases. However, histoplasmosis, tuberculosis, autoimmune disease, radiation therapy, and other idiopathic fibroinflammatory diseases have been implicated in some cases. Most clinical features are related to an obstruction or compression of the mediastinal structure. Fibrosing mediastinitis is often progressive and occurs diffusely throughout the mediastinum. We encountered a case of fibrosing mediastinitis of a very focal lesion without evidence of mediastinal involvement. The condition was confirmed by biopsy and graft bypass surgery was performed because of SVC syndrome.

섬유화 세로칸염은 드문 양성질환으로 종격동 조직 내에 국소적이거나 광범위한 심한 섬유화성 병변을 유발하고 세로칸 내 장기들을 침범하거나 압박하여 증상이나 증후를 나타내는 질환이다. 그러나 저자들은 세로칸의 침범이 거의 없으면서 상대정맥 주위에 발생한 아주 국소적인 병변에 의하여 상대정맥증후군을 유발한, 혈관종양과 감별이 필요하였던 국소적 섬유화 세로칸염 1예를 경험하였기에 보고하는 바이다.

Keywords

References

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