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Localized Fibrosing Mediastinitis with Superior Vena Caval(SVC) Syndrome  

Shin, Sang Yun (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital)
Kim, Beom Kyung (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital)
Park, Byung Hoon (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital)
Park, Seon Cheol (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital)
Park, Jun Chul (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital)
Soon, Myoung Kyun (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital)
Lee, Seung Yul (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital)
Im, Eui (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital)
Jeon, Han Ho (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital)
Jung, Kyung Soo (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital)
Jeong, Jae Heon (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital)
Choi, Yu Ri (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital)
Kang, Kyoung Hoon (Department of Thoracic surgery, National Health Insurance Corporation Ilsan Hospital)
Choi, Yoon Jung (Department of Pathology, National Health Insurance Corporation Ilsan Hospital)
Hong, Yong Kook (Department of Radiology, National Health Insurance Corporation Ilsan Hospital)
Kim, Chong Ju (Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital)
Publication Information
Tuberculosis and Respiratory Diseases / v.63, no.4, 2007 , pp. 387-391 More about this Journal
Abstract
Fibrosing mediastinitis is a rare disease that is characterized by the proliferation of dense fibrous tissue of the mediastinum. The pathogenesis of fibrosing mediastinitis is unknown in most cases. However, histoplasmosis, tuberculosis, autoimmune disease, radiation therapy, and other idiopathic fibroinflammatory diseases have been implicated in some cases. Most clinical features are related to an obstruction or compression of the mediastinal structure. Fibrosing mediastinitis is often progressive and occurs diffusely throughout the mediastinum. We encountered a case of fibrosing mediastinitis of a very focal lesion without evidence of mediastinal involvement. The condition was confirmed by biopsy and graft bypass surgery was performed because of SVC syndrome.
Keywords
Fibrosing mediastinitis; Superior vena caval syndrome;
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