쿠싱 증후군 일으킨 카르시노이드종양의 1예 보고: 코르티코트로핀분비호르몬 분비하는 종양 의증

A Case Report of Thymic Carcinoid Tumor Associated with Cushing's Syndrome: Possible Corticotropin-Releasing Hormone Secreting Tumor

  • 전순호 (한양대학교 의과대학 구리병원 흉부외과) ;
  • 노선균 (한양대학교 의과대학 서울병원 흉부외과) ;
  • 오영하 (한양대학교 의과대학 구리병원 병리과) ;
  • 강준구 (한림대학교 의과대학 평촌병원 내과) ;
  • 염종훈 (한양대학교 의과대학 구리병원 마취과) ;
  • 이철범 (한양대학교 의과대학 구리병원 흉부외과)
  • Chon Soon-Ho (Department of Thoracic and Cardiovascular Surgery, Hanyang University Guri Hospital, Hanyang University College of Medicine) ;
  • Ro Sun-Kyun (Department of Thoracic and Cardiovascular Surgery, Hanyang University Hospital, Hanyang University College of Medicine) ;
  • Oh Young-Ha (Department of Pathology, Hanyang University Guri Hospital, Hanyang University College of Medicine) ;
  • Kang Jun-Goo (Department of Internal Medicine, Hallym University Pyongchon Hospital, Hanyang University College of Medicine) ;
  • Yeom Jong-Hoon (Department of Anesthesiology, Hanyang University Guri Hospital, Hanyang University College of Medicine) ;
  • Lee Chul-Burm (Department of Thoracic and Cardiovascular Surgery, Hanyang University Guri Hospital, Hanyang University College of Medicine)
  • 발행 : 2006.10.01

초록

쿠싱증후군과 연관된 흉선 carcinoid종양은 드문 질병으로 그 예후가 나쁜 것으로 알려져 있다. 그중 부신피질자극 호르몬 분비 촉진 호르몬을 생산하는 흉선 carcinoid 종양은 훨씬 더 드물다. 우리는 거대한 전방 종격동 종양을 갖고 있는 58세 여자 환자에 대해 보고하려고 한다. 환자는 흉선제거술 5개월 후 전반적인 부종과 호흡곤란으로 다시 입원하였다. 환자는 재발과 전이가 발견되었고 쿠싱증후군으로 진단 받았다.

Thymic carcinoid tumor associated with Cushing's syndrome is a rare disease with a poor prognosis. Thymic carcinoid with Cushing's syndrome caused by CRH (corticotropin-releasing hormone) production is even rarer. We report a 58-year-old woman with a huge anterior mediastinal mass. Five months after thymectomy the patient was readmitted with symptoms of generalized edema and dyspnea. Recurrence and metastases were discovered and Cushing's syndrome diagnosed.

키워드

참고문헌

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