A Case of Video-Assisted Thoracoscopic Pneumonectomy for Unilateral Diffuse Pulmonary Arteriovenous Malformation

비디오흉강경을 이용하여 폐절제술로 치료한 편측 미만성 폐동정맥루 1례

  • Jung, Jong Yul (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Lim, Jong Keun (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Chun, Sung Wan (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Suh, Won Na (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Kim, Dae Jun (Department of Thoracic and Cardiovascular Surgery, Yonsei University College of Medicine) ;
  • Lee, Kwang Hun (Department of Diagnostic Radiology, Yonsei University College of Medicine) ;
  • Park, Moo Suk (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Kim, Se Kyu (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Chang, Joon (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Kim, Sung Kyu (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Kim, Young Sam (Department of Internal Medicine, Yonsei University College of Medicine)
  • 정종열 (연세대학교 의과대학 내과학교실) ;
  • 임종근 (연세대학교 의과대학 내과학교실) ;
  • 전성완 (연세대학교 의과대학 내과학교실) ;
  • 서원나 (연세대학교 의과대학 내과학교실) ;
  • 김대준 (연세대학교 의과대학 흉부외과학교실) ;
  • 이광훈 (연세대학교 의과대학 영상진단학과학교실) ;
  • 박무석 (연세대학교 의과대학 내과학교실) ;
  • 김세규 (연세대학교 의과대학 내과학교실) ;
  • 장준 (연세대학교 의과대학 내과학교실) ;
  • 김성규 (연세대학교 의과대학 내과학교실) ;
  • 김영삼 (연세대학교 의과대학 내과학교실)
  • Received : 2006.10.16
  • Accepted : 2006.11.06
  • Published : 2006.12.30

Abstract

Pulmonary arteriovenous malformations (PAVMs) are abnormal direct communications between the pulmonary arteries and veins. PAVMs may occur as either an isolated abnormality or in association with hereditary hemorrhagic telangiectasia, also called Osler-Weber-Rendu disease. The topic of PAVM has recently been extensively reviewed, but little is known about the clinical characteristics and course of patients having a diffuse pattern of the disease. Herein, is reported a case of unilateral diffuse PAVM in an 18 year old female patient, who underwent a right pneumonectomy, under a video-assisted thoracic surgery (VATS) approach, as the diffuse small pulmonary arteriovenous malformation involved the whole right lung.

저자들은 편측성으로 우측 폐전체를 침범한 미만성 폐동정맥루에 대해 색전술 등의 중재적 시술이 불가능하여 비디오흉강경을 이용해서 폐절제술로 치료한 1예를 경험하였기에, 문헌 고찰과 함께 보고하는 바이다.

Keywords

References

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