Clinical and Experimental Pediatrics

The Korean Pediatric Society (대한소아청소년과학회)
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A Case of Neonatal Lupus with Abnormal Liver Function Test and Skin Lesion

피부 병변과 간기능 이상이 동반된 신생아 루푸스 1례

  • Chung, Ju-Young (Department of Pediatrics, Sanggyepaik Hospital, Inje University College of Medicine) ;
  • Chey, Myoung Jae (Department of Pediatrics, Sanggyepaik Hospital, Inje University College of Medicine)
  • 정주영 (인제대학교 의과대학 상계백병원 소아과) ;
  • 최명재 (인제대학교 의과대학 상계백병원 소아과)
  • Received : 2004.08.17
  • Accepted : 2004.09.17
  • Published : 2005.01.15
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Abstract

Neonatal lupus(NL) is characterized by typical clinical features and the presence of maternal autoantibodies. The principal serologic markers of NL are anti-Ro/SSA or anti-La/SSB maternal autoantibodies, which are transferred across the placenta and can be detected for the first few months of the affected child. The major clinical manifestations are cardiac disease, notably congenital heart block, and cutaneous lupus lesions. Hepatobiliary disease is relatively rare clinical manifestation of NL. We experienced a case of NL with abnormal liver function test and skin lesion.

저자들은 피부 병변과 간기능 이상이 동반된 신생아 루푸스 1례를 경험하여 보고하는 바이다.

Keywords

References

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