Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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Congenital Coronary Artery to Left Ventricular Fistula - A case report-

우관상동맥에서 좌심실로 유출되는 선천성 관상동맥루 -치험 1예-

  • Kim Jin Sun (Department of Thoracic & Cardiovascular Surgery, Sungkyunkwan University School of Medicine) ;
  • Yang Ji-Hyuk (Department of Thoracic & Cardiovascular Surgery, Sungkyunkwan University School of Medicine) ;
  • Kim] Sung-Hye (Department of Pediatrics, Sungkyunkwan University School of Medicine) ;
  • Lee Heung Jae (Department of Pediatrics, Sungkyunkwan University School of Medicine) ;
  • Jun Tae-Gook (Department of Thoracic & Cardiovascular Surgery, Sungkyunkwan University School of Medicine)
  • 김진선 (성균관대학교 삼성서울병원 흉부외과학교실) ;
  • 양지혁 (성균관대학교 삼성서울병원 흉부외과학교실) ;
  • 김성혜 (성균관대학교 삼성병원 소아과학교실) ;
  • 이흥재 (성균관대학교 삼성병원 소아과학교실) ;
  • 전태국 (성균관대학교 삼성서울병원 흉부외과학교실)
  • Published : 2005.07.01
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Abstract

Coronary artery fistula accounts for $0.27\~0.4\%$ of all congenital cardiac defects. In more than $50\%$ of the cases, right coronary artery is involved. The fistula drains into the right heart in $92\%$ of the cases. Left heart is the site of termination in only $8\%$ of the cases, especially less left ventricle $(3\%)$. We experienced a case of right coronary artery to left ventricular fistula in a 3-year-old boy who was diagnosed incidentally and underwent ligation of fistula.

관상동맥루는 선천성 심질환 환자 중에서 $0.27\~0.4\%$의 유병률을 보이는 드문 질환이다. $50\%$이상의 환자에서 우관상동맥이 관상동맥루의 기시부이며 모든 관상동맥루 중 $92\%$는 우측 심장으로 유출된다. 관상동맥루가 좌측 심장으로 개구하는 경우는 $8\%$이며 그 중 좌심실로 유출되는 경우는 더욱 드물다. 본원에서는 3세 된 남자 환아에서 우연히 진단된 우관상동맥과 좌심실간의 관상동맥루를 경험하였기에 이를 보고하는 바이다.

Keywords

References

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