• Journal of The Korean Society of Inherited Metabolic disease
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• v.3 no.1
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• pp.69-74
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• 2003

• Journal of The Korean Society of Inherited Metabolic disease
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• v.3 no.1
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• pp.58-61
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• 2003

• Journal of The Korean Society of Inherited Metabolic disease
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• v.3 no.1
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• pp.63-63
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• 2003

• Journal of The Korean Society of Inherited Metabolic disease
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• v.3 no.1
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• pp.64-68
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• 2003

• Journal of The Korean Society of Inherited Metabolic disease
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• v.3 no.1
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• pp.75-85
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• 2003

• Journal of The Korean Society of Inherited Metabolic disease
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• v.3 no.1
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• pp.97-99
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• 2003

• Journal of The Korean Society of Inherited Metabolic disease
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• v.3 no.1
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• pp.28-31
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• 2003

• Journal of The Korean Society of Inherited Metabolic disease
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• v.3 no.1
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• pp.38-44
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• 2003

• Journal of The Korean Society of Inherited Metabolic disease
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• v.22 no.2
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• pp.53-57
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• 2022

Congenital metabolic disorders are rare inherited disorders resulting from a defect in biochemical and metabolic pathways affecting proteins, fats, carbohydrates metabolism or impaired organelle function. Depending on the abnormality of biochemical metabolism, various precursors and their abnormal metabolites can accumulate in the body and the final products which are critical in normal physiology can be deficient, resulting in disease. Congenital metabolic disorders present complicated medical conditions involving several human organ systems, including nervous system, eyes, liver, and kidneys. Various proteins and lipids are involved in the development and homeostasis of the skin, so many congenital metabolic disorders present abnormal changes in skin and hair. In this review, congenital metabolic diseases related to amino acid and lipid metabolism accompanying skin abnormalities will be discussed.

• The Korean Journal of Physiology and Pharmacology
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• v.16 no.3
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• pp.175-180
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• 2012

Yoga has been known to have stimulatory or inhibitory effects on the metabolic parameters and to be uncomplicated therapy for obesity. The purpose of the present study was to test the effect of an 8-week of yoga-asana training on body composition, lipid profile, and insulin resistance (IR) in obese adolescent boys. Twenty volunteers with body mass index (BMI) greater than the 95th percentile were randomly assigned to yoga (age $14.7{\pm}0.5$ years, n=10) and control groups (age $14.6{\pm}1.0$ years, n=10). The yoga group performed exercises three times per week at 40~60% of heart-rate reserve (HRR) for 8 weeks. IR was determined with the homeostasis model assessment of insulin resistance (HOMA-IR). After yoga training, body weight, BMI, fat mass (FM), and body fat % (BF %) were significantly decreased, and fat-free mass and basal metabolic rate were significantly increased than baseline values. FM and BF % were significantly improved in the yoga group compared with the control group (p<0.05). Total cholesterol (TC) was significantly decreased in the yoga group (p<0.01). HDL-cholesterol was decreased in both groups (p<0.05). No significant changes were observed between or within groups for triglycerides, LDL-cholesterol, glucose, insulin, and HOMA-IR. Our findings show that an 8-week of yoga training improves body composition and TC levels in obese adolescent boys, suggesting that yoga training may be effective in controlling some metabolic syndrome factors in obese adolescent boys.