• Journal of the korean academy of Pediatric Dentistry
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• v.35 no.3
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• pp.532-538
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• 2008

Lesch-Nyhan syndrome is a rare X-linked recessively inherited disorder, caused by complete absence or decrease in activity of hypoxanthine guanine phosphoribosyl transferase(HPRT), an enzyme involved in purine metabolism. This enzyme deficiency gives rise to nephropathy symptoms, such as hyperuricosuria and hyperuricemia by excessive uric acid production and neuropathy symptoms, such as mental retardation, choreoathetosis and self mutilation behavior. Patients with Lesch-Nyhan syndrome have tendency to bite their lip, tongue and finger. In severe cases, partial or even total amputation of tongue or finger occur. Self-inflicted bites are often complicated by secondary infection to the injured site as well as pain. Furthermore tissue loss by biting results in esthetic problems. The dental management of self mutilation includes treatment with appliances such as soft mouth guard or lip bumper, extraction of all the teeth, and orthognathic surgery. We report a case of a 13 year-old boy with Lesch-Nyhan syndrome, who severely injured himself on his tongue. At first, conservative treatment using soft mouth guard was considered, but it could not prevent trauma on his tongue. Therefore, extraction of the lower anterior and posterior teeth was carried out.

• Journal of the korean academy of Pediatric Dentistry
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• v.32 no.2
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• pp.306-311
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• 2005

Lesch-Nyhan syndrome is a rare disorder of purine metabolism, first described in 1964. The incidence is estimated to be 1:100,000 birth. It is an X-linked recessive disorder in which affected males have a virtually complete deficiency of the enzyme hypoxanthine guanine phosphorybosyl transferase(HGPT). This enzyme deficiency gives rise to excessive uric acid production and consequent hyperuricemia. Lesch-Nyhan syndrome is clinically characterized by mental retardation, choreoathetosis, spastic cerebral palsy, and severe self-mutilation behavior. Patient with Lesch-Nyhan syndrome mostly bite their lip, tongue and finger. In severe cases, partial or total amputation of the lip and tongue is common. Self-inflicted bites are often further complicated by secondary infection to injuried site as well as pain. And tissue loss by biting results in esthetic problems. This report presents a Lesch-Nyhan syndrome patient with self-mutilation, who have a destruction of perioral tissue, especially the lower lip. He was treated successfully with soft mouthguard, psychological and pharmacological method.

• Clinical and Experimental Pediatrics
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• v.55 no.6
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• pp.215-218
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• 2012

Mucoceles are common benign cystic lesions of the oral cavity that develop following extravasation or retention of mucous material from the major or minor salivary glands. Mucoceles are usually located in the lower lip (60 to 70% of cases), and the floor of the mouth is only involved in 6 to 15% of cases. Submandibular gland mucocele is extremely rare but should be considered in the differential diagnosis of swelling at the submandibular triangle in young children. We present the rare case of a 16-month-old child who was diagnosed with bilateral submandibular gland mucocele, presenting as serial swellings in both submandibular regions. We removed the cystic mass with the submandibular and sublingual glands to prevent recurrence.

• Speech Sciences
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• v.9 no.3
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• pp.201-210
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• 2002

This paper explores whether there is correlation between consonants' place and duration of adjacent vowels in English and Korean. The results showed that in English the vowels preceding alveolar stops were in general longer than the vowels before bilabial or velar stops. Consonants appeared to have their inherent length due to their place and to exhibit some compensatory effects on the duration of preceding vowels. This effect can be explained in a physiological term that the tongue tip is the organ which might be more agile in articulatory movement than the tongue body for the velars or the lower lip (and the jaw) for the bilabials is and the shorter production time of the alveolars caused the lengthening of the adjacent vowels. However, this physiological account did not hold in the case of Korean, which exhibited less consistent patterns across speakers for the consonants' place and the vowel duration. The segmental duration seemed to be timed quite consistently within a language but the pattern was not universal across languages.

• Maxillofacial Plastic and Reconstructive Surgery
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• v.11 no.1
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• pp.237-241
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• 1989

Hemangioma can present difficult management problems to the oral & maxillofacial surgeon when their removal is indicated. Cryosurgery has also been employed for the treatment of hemangiomas and offers several advantages over the other treatment methods. This is a case report of hemangioma which was treated by cryosurgery. The cryosurgery technique has proved to be painless, bloodless and safe. The healing process was completed at 4 weeks postoperatively with minimal invisible scar.

• Maxillofacial Plastic and Reconstructive Surgery
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• v.18 no.2
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• pp.279-285
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• 1996

The odontogenic keratocyst(OKC) was used of term and described some of clinical, radiological and microscopic features by Philipsen 1956. The microscopic finding of OKC is characterized by the production of keratin, Which sometimes fills the lumen and thinning of epithelium of cyst. The most clinical importance of OKC is its extraordinary recurrence rate owing to the incomplete removal of the cyst wall. The final diagnosis of OKC should be evaluated by histologic findings and follow-up of any case of OKC with annual roentgenograms and clinical evaluations is essential for at least five years after surgery. This article is report of 2 cases of large OKC involved both molar portion and symphysis of mandible with facial asymmetry, severe bone destruction and paresthesia of lower lip on clinically, roentgenographically. By the postoperative findings the patients showed normal regeneration of bone defect area without recurrence signs by panorama films after surgery.

• Journal of Dental Anesthesia and Pain Medicine
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• v.20 no.2
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• pp.95-99
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• 2020

Various dental procedures, such as injection administration, surgical treatment, and endodontic treatment, can cause injury to the nerves. The most commonly injured nerves are the inferior alveolar and lingual nerves. This can manifest as altered sensation to the area of innervation of the injured nerve, such as the lower lip, chin, teeth, tongue, and mucosa. Altered sensations or loss of sensation are relatively infrequent complications in daily dental practice. Here, we report an uncommon case of altered sensation in the midfacial region caused by an endodontic procedure and discuss the need to consider local dental causes in the differential diagnosis of numbness in the facial region.

• Animal Systematics, Evolution and Diversity
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• v.26 no.3
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• pp.295-305
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• 2010

Two ampithoid species, Ampithoe lacertosa Bate and A. tarasovi Bulycheva, are redescribed. A. tarasovi has been misidentified as A. lacertosa in Korea. A. tarasovi can be distinguished from A. lacertosa in having the following characteristics: the apical and medial lobes of outer lobe are separated in the lower lip, the carpus of male gnathopod 1 is about 1.4 times as long as the propodus, the palm of male gnathopod 2 has a sloped quadrate hump and a posterodistal tooth, the peduncle of uropod 3 is approximately 2 times as long as the rami, and the length of the carpus is longer than that of the propodus of female gnathopod 1. This study provides detailed descriptions and figures for both species. A. tarasovi is reported for the first time as a member of the Korean fauna.

• The korean journal of orthodontics
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• v.9 no.1
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• pp.15-22
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• 1979

This study was undertaken to establish the cephalometric standard of Hellman dental age IVA group of Korean. The subjects consisted of 40 males and 44 females with normal occlusion and aceptable profile. The results were obtained. 1) The tables of standard deviation from the measurements were made. 2) All linear measurement was greater in male than in female. 3) Female had more convex profile than male, 4) Facial convexity, upper and lower lip of esthetic line were gradually decreased with. age. 5) Upper incisor was gradually labioversioned with age.

• Journal of the korean academy of Pediatric Dentistry
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• v.44 no.3
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• pp.365-369
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• 2017

Local anesthetics are widely used in clinical dentistry. However, while rare, there have been some reports of true hypersensitivity to local anesthetics. A case of hypersensitivity in a 26-month-old boy is reported. After administering local anesthesia with lidocaine, treatment was performed while the patient was under oral sedation. After treatment, the patient presented with lower lip edema. Treatment with anti-histamines and a steroid successfully reversed his symptoms.