• Journal of Audiology & Otology
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• v.25 no.1
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• pp.49-54
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• 2021

Type II mucopolysaccharidosis (MPS II) commonly known as Hunter syndrome, is a rare X-linked lysosomal storage disorder caused by iduronate-2-sulfatase deficiency, which in turn causes otorhinolaryngological manifestations, including sensorineural hearing loss (SNHL). Previously, the median survival age of patients with MPS was approximately 13.4 years. However, in the era of enzyme replacement therapy and other multidisciplinary care modalities, the life expectancy has increased. Herein, we report a rare case of an adolescent with MPS II who underwent SNHL treatment with cochlear implantation (CI). Based on unexpected findings of mastoid emissary veins and overgrowth of the vessels around the temporal bone, CI was performed using the transmeatal approach instead of the conventional transmastoid method, to avoid damage to the vessels. The average hearing threshold after CI was 35 dB and no surgical complications were encountered. Adolescent MPS II may present vessel abnormalities, which can reduce the success rate of surgery. In patients with MPS II with SNHL, CI should be performed under careful monitoring of vessel overgrowth. Moreover, with regard to feasibility of CI in adolescent patients with MPS II with SNHL, surgical techniques such as the transmeatal approach should be selected based on adequate assessment of the case.

• Proceedings of the Korean Society for Noise and Vibration Engineering Conference
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• 2004.05a
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• pp.109-114
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• 2004

Measurement of noise is not only to know the information of acoustic pressure but to assess human response for noise. Provided that want to find human response for transportation noise, we will have to reproduce the measured noise. The method of reproduction is largely divided into monaural and binaural reproduction techniques. Human fundamentally hears sound through both ears, which is binaural hearing. And binaural technique includes the more information of physical phenomena like acoustical reflection and deflection. So, binaural reproduction is more suitable for assessment of the psychoacoustical and physiological response for transportation noise exposures.

• Korean journal of aerospace and environmental medicine
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• v.31 no.2
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• pp.51-53
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• 2021

Aviation medical examiners should always keep two principles in mind when evaluating patients with vertigo: Does this disease render him or her incapacitated? And does this disease recur? Meniere's disease accompanies vertigo and hearing symptoms such as hearing loss and tinnitus and is particularly important because it can render the patient incapacitated and has recurrent consequences. In this case, we intended to investigate the course of a patient who was evaluated with symptoms of dizziness and tinnitus and to review the patient's judgment result according to the principles of aeromedical evaluation.

• Neonatal Medicine
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• v.16 no.2
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• pp.213-220
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• 2009

Purpose: Hearing loss is one of the common birth defects in humans, with a reported prevalence of 1-3 per 1000 newborns. We investigated the incidence of hearing loss and evaluated the use of neonatal hearing screening test in neonatal intensive care unit (NICU) graduates who are at greater risk for hearing loss than normal newborns. Methods: The neonates admitted to the NICU of Asan Medical Center from 1 March, 2003 to 30 March, 2008 who were available for follow-up were included. Those who failed the first auditory brainstem response prior to discharge were retested with the stapedial reflex test, auditory brainstem response and tympanometry in the Otolaryngology department. Results: Of 2,137 neonates, 2,000 (93.5%) neonates were tested prior to discharge. Sixty-seven neonates (3.4%) failed the first newborn hearing screening test. Of 67 infants, 52 infants were retested for a second hearing test. Excluding 10 infants (19.2%) who were lost during follow-up, 16 infants were confirmed to have hearing impairment of which 12 and 4 infants had unilateral and bilateral hearing loss, respectively. Of 16 infants, 5 did not meet the criteria set by the Korean National Health Insurance Corporation. Conclusion: The prevalence of hearing impairment in NICU graduates is about 0.8%, excluding those who were lost for follow up, necessitating a systemic and effective hearing assessment program among these high risk infants and more generous national insurance coverage.

• Journal of the Institute of Electronics Engineers of Korea SC
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• v.49 no.2
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• pp.38-45
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• 2012

If an infant with congenital hearing loss is diagnosed in good time and get proper treatment as soon as possible, treatment effect could be maximized and the social costs could be considerably reduced. For these reasons, the medical equipment to screen hearing impairment objectively is needed. The ABR(auditory brainstem response) is typical diagnostic tools for this purpose but there are drawbacks in sense that it does not have frequency specificity and shows hearing information of usually high frequency band. The ASSR(auditory steady-state response) is excellent in frequency specificity, but the rate of wrong diagnosis is slightly high. In this study, we proposed the system which can measure both the ABR and the ASSR, and can show the objective and quantitative indices(Fsp and F-test). It was designed to allow various tests without hardware modification by minimizing hardware components and by increasing software roles. The objective assessment of the developed system was evaluated by experiments with 10 normal persons.

• Journal of Environmental Science International
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• v.8 no.4
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• pp.457-464
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• 1999

To develop managing guidance of occupational noise exposure for metal working facility, we have studied about drafting contour map of noise exposure, methods of noise assessment and actual calculation method of time weighted noise exposure. Therefore we have suggested that contour maps of noisy workplace are very important for controlling metal working fluid facility and two kinds of noise assessment method, so called, personal andstatic exposure are necessary to avoid argument between workers and managing group. Finally we would like recommend that the Korean specification of noise exposure should be modified to protect ONIHL(oocupational noise induced hearing loss).

• Proceedings of the Korean Society for Noise and Vibration Engineering Conference
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• 2007.05a
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• pp.127-131
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• 2007

A laboratory study on low frequency noise assessment was carried out to determine the acceptability limits in the frequency range between 20 and 200 Hz. The acceptability limits were tested in the anechoic chamber to minimize the background noise. A total of 30 test subjects, who were aged between 19 to 33 years, participated in this study. They were exposed to various stimuli for about 1 hour by supra-aural earphone. The experiment consisted of two listening sessions; hearing threshold and the acceptability limits session. The results showed that the trend of the acceptability limits curve was approximately equal to C-weighting curve which had been found to be superior to A-weighting curve in low frequency noise assessment.

• International journal of advanced smart convergence
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• v.5 no.4
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• pp.48-53
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• 2016

In this paper, all elements used in integrated infrastructure for job competency assessments of NCS (National Competency Standards) will be merged into assessment system using multiple devices(ASMD). NCS is a systematic approach on required abilities (knowledge, technical expertise, attitude) to process the tasks in the fields by industry. Competiveness of ASMD design is that no limitation of time and space using personal devices like PC, laptop, smartphone, and tablet, while seeing screen, hearing, touching, speaking, and writing. Question type can be limitless to express the situation. To lead technologies and market for domestic and oversea assessment system, supporting on multiple devices with connectivity that will eliminate limitation of time and space is the key feature for design competitiveness. Design of integrated assessment system proposed in this paper can be applied to NCS, fundamental competency evaluation, online test, job aptitude test, and foreign language test which involve listening, reading, writing, and speaking. Compared with existing evaluation method, reduction of investment and operating cost will be greater. Along with development of ICT technologies, the next generation of integrated assessment system will be quickly changed to ASMD, which already involves connected service between internet and smart devices.

• Journal of the korean academy of Pediatric Dentistry
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• v.39 no.3
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• pp.267-272
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• 2012

Dental professionals are exposed to various occupational risks, among which the problem of hearing damage has been newly revealed. There have been some researches reporting that noise occurring in a dental office exceeds the Occupational Safety and Health Act (OSHA) Standards. Especially, the pediatric dentists are repeatedly exposed to an additional noise source called the crying sound of children in addition to all kinds of noises from dental instruments. Accordingly, this study intended to investigate the noise environment likely to affect pediatric dentists and to examine the possibility of resultant hearing damages. The level of noise was measured respectively, when various dental instruments (ultrasonic scaler, high-speed handpiece, low-speed handpiece) are operated, when children are crying, and when both occasions take place simultaneously (from the distance of 30 cm) with a portable noise meter. And the daily duration of pediatric dentists exposed to the noise environment was surveyed. The results were compared with the standard value of noise threshold of NIOSH, OSHA, and that of hearing damage of CRA News letter respectively. Considering the intensity and exposure time, the noise environment of pediatric dentists exceeds the allowable noise threshold values. Even only one exposure to crying child was likely to lead to permanent hearing damage. Comparatively, pediatric dentists have a higher risk for occupational hearing damages, and some active measures are thought highly desirable to minimize it.

• Journal of Environmental Impact Assessment
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• v.13 no.4
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• pp.165-185
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• 2004

Assessment in Socio-economic items should be used to estimate social influence when policies and projects were introduced. To estimate current situation of socio-economic items 19 Environmental Impact Statement (EIS) of large scale projects were analyzed. The projects were selected based on magnitude of social impact when the projects were implemented. Environmental Impact Statement was categorized into line projects(road construction, railroad construction, stream development, etc), and surface projects(energy development, wetland reclamation, recreation and sport development, and housing and residential development, etc) thus being chosen for 19 projects in each categories. This report was based on the analysis of 7 items in socio-economic environmental items(i.e., population, residents, industry, public facilities, education, transport and historical monument). Most EIS did not follow the regulation suggested by Ministry of Environment, and only current circumstances were briefly described. Indifference of in-depth analysis of socioeconomic environmental items would influence the process of social and environment impact negatively in the midst of construction of National Projects such as Outer Circle Seoul Highways, Saemankeum Reclamation Projects, etc. This abrupt halt of construction was mostly based on a lack of public hearing or public participation. Socio-economic items are also very much lacking in quantitative method and strengthening socio-economic environmental items is needed via checklist or matrix that brings decision-makers better ideas objectively.