• Journal of The Korean Society of Inherited Metabolic disease
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• v.5 no.1
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• pp.33-43
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• 2005

Purpose: X-linked adrenoleukodystrophy(ALD) is a rare disorder that shows a great deal of phenotypic variability. We subdivided chidhood X-linked ALD patients into several phenotypes by the age at onset, the sites of most severe clinical involvement and the rate of progression of neurologic symptoms. Methods: Thirteen patients who had been diagnosed as X-linked ALD and followed up for at least one year were enrolled from 1996 to 2003. Results: 1. Ten had childhood cerebral ALD, who showed first neurologic symptoms at 7.02 years and progressed rapidly: interval between first symptoms and vegetative state was 1.35 years, and interval from initial symptoms to death was 3.35 years. Treatment with Lorenzo's oil did not prevent neurologic progression. Two patients who underwent umbilical cord blood transplantation died. 2. Two had adolescent cerebral ALD. They had first symptoms at 11.5 years, and showed tendency to progress less rapidly than childhood cerebral form patients. 3. One "Addison only" patient who had adrenal insufficiency without nervous system involvement remained asymptomatic during Lorenzo's oil treatment. 4. All cerebral form patients except one showed the lesions in both parieto-ocipital white matter in brain magnetic resonance imaging. Conclusion: The cerebral ALD was the most common form in childhood and was asoociated with a serious prognosis.

• Clean Technology
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• v.19 no.3
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• pp.313-319
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• 2013

To produce biodiesel efficiently from fish oil containing 4% free fatty acid, esterification and trans-esterification were carried out with Vietnam catfish oil, which was kindly provided from GS-bio company. Heterogeneous solid acid catalysts such as Amberlyst-15 and Amberlyst BD-20 and sulfuric acid as homogeneous acid catalyst were used for the esterification of free fatty acids in the fish oil. Sulfuric acid showed the highest removal efficiency of free fatty acid and the shortest reaction time among three acid catalysts. The base catalysts for trans-esterification such as KOH, $NaOCH_3$ and NaOH were compared with each other and KOH was determined to be the best transesterification catalyst. Some solid material, which assumed to be saponified product from glycerol and biodiesel, were observed to form in the fish oil biodiesel when using $NaOCH_3$ and NaOH as the transesterification catalyst. The initial acid value of fish oil was proven to have a negative effect on biodiesel conversion. Of the three catalysts, KOH catalyst transesterification was shown to have high content of FAME and the optimal ratio of methanol/oil ratio was identified to be 9:1.

• Korean Journal of Food Science and Technology
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• v.54 no.3
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• pp.264-271
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• 2022

In this study, the nutritional properties of sterilized and non-heat-pressed raw perilla oil (SRPO) were studied and its potential as a functional food was evaluated. The copper, cobalt, and calcium levels were high in sterilized and SRPO. The total polyphenol content and ABTS radical scavenging activity were the highest in SRPO, whereas nitrite scavenging activity was the highest in 45℃ cold pressed perilla oil (CPPO). The above results confirmed that sterilized and non-heat-pressed perilla oil had high mineral and total polyphenol contents, as well as ABTS radical scavenging activity and nitrite scavenging ability. The peroxide value of SRPO decreased as the storage period increased, and the acid value of low-temperature pressed perilla oil over 65℃ (LPPO) significantly increased. This work also provided an opportunity to develop a new method for manufacturing perilla oil, and it is hoped that these experiments will form a basis for the commercialization of perilla oil.

• The Transactions of the Korean Institute of Electrical Engineers A
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• v.53 no.9
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• pp.513-520
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• 2004

In the paper, we summarize the result of the experimental research for the overload criteria of domestic distribution transformers considering the electric consumption patterns of customers. For the basic characteristic data of distribution transformer overload, the actual experiments are accomplished. The field data of loads are surveyed from sample transformers for analyzing the consumption pattern of customer load. The load data acquisition devices are equipped, and the algorithm of load pattern classification is applied. In addition to this efforts, various load pattern data. in past are gathered. Then the representative load pattern of each customer type in domestic is extracted. The final results of overload criterions are presented as tabular form through the results of experiments and survey are combined. The field test of the experiment results is peformed using the special manufactured transformers, which can measure both the load and top-oil temperature of transformer. Through this, we verify that the results of field test are similar to the laboratory one and the Proposed overload criteria can be effectively applied to the real system.

• Korean Journal of Plant Tissue Culture
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• v.27 no.4
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• pp.283-297
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• 2000

Seeds are an ideal repository for recombinant proteins in molecular farming applications. However, in order to use plant seeds efficiently for the production of such proteins, it is necessary to understand a number of fundamental biological properties of seeds. This includes a full understanding of promoters which function in a seed-specific manner, the subcellular targeting of the desired polypeptide and the final form in which a protein is stored. Once a biologically active protein has been deposited in a seed, it is also critical that the protein can be extracted and purified efficiently. In this review, these issues are examined critically to provide a number of approaches which may be adopted for production of recombinant proteins in plants. Particular attention is paid to the relationship between subcellular localization and protein extraction and purification. The robustness and flexibility of seed-based production is illustrated by examples close to or already in commercial production.

• Proceedings of the KIEE Conference
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• 2006.07a
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• pp.343-344
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• 2006

Consumption of fossil fuel has been increasing steadily, and it has seriously affected environment. Due to this situation, UN establish ed UNFCC (United rations Framework Convention on Climate Change), and since Feb. 2005, Kyoto Protocol has come into effect for UNFCC obligation. In Korean power system, coal and oil thermal generation emitting large CO2 form about 46% of total generation. Moreover since electricity dem and has been increasing continuously, various alternatives should be designed to comply with Kyoto Protocol. In this paper, we analyze changes of each GENCO's generation pattern and resource planning under CO2 emission constraints. For this analysis, we incorporate CO2 emission constraints and the emission trading mechanism into the conventional OPF model.

• Tribology and Lubricants
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• v.29 no.1
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• pp.39-45
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• 2013

Magnetorheological (MR) fluid belongs to the group of smart materials. In MR fluid, iron particles in base oil form chains in the direction of the applied magnetic field, thus resulting in a variation in the stiffness and damping characteristics of the fluid. Research is being carried out on controlling the stiffness and damping characteristics as well as the tribological characteristics of the MR fluid. In this study, the friction characteristics of MR fluid have been evaluated using three types of materials and magnetic fields of different strengths. The coefficients of friction of the three types of MR fluid are measured, and the relationship between the coefficient of friction and the strength of the applied magnetic field is obtained.

• The Journal of Art Theory & Practice
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• no.10
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• pp.63-84
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• 2010

This essay examines how the figure of Liberty has been refashioned in the streets of post-apartheid South Africa, addressing three public art works installed in Johannesburg over the past decade: Reshada Crouse's oil painting Passive Resistance, Marlene Dumas' tapestry The Benefit of the Doubt and William Kentridge's and Gerhard Marx's sculpture Firewalker. Even as these monumental works all reprise Delacroix's Liberty on the Barricades-an icon of the city street and its revolutionary barricades-so too this trio of Liberties have become mere phantoms of their vaunted archetype. Haunted specters, they quarrel with the mythologized chimera of Liberty, taking issue with the fraught tradition of pinning regime change onto the body of the female nude. Drawing instead on South African histories of women's resistance, in which female nudity has been repeatedly marshaled as a form of dissent, the Liberties circling Johannesburg hybridize their European template with local traditions of female political opposition to colonial and postcolonial male authority.

• Journal of the Korean Society of Manufacturing Process Engineers
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• v.14 no.3
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• pp.43-49
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• 2015

This paper describes the design of a forged fitting form to acquire a method of product design measurement by target measurement standards. The pipefitting connects each pipe and combines seals and nipples with the pipes normally. Therefore, the section combined with the fitting pipe was measured by a 3D scanner, and the acquired measurement and the design measurement were obtained after modification of the forged fitting pipe by that standard. Moreover, the accuracy of the model was verified through leakage testing of the oil and verification of the design measurement for accuracy decisions on the design measurement after modification of the product.

• Journal of ILASS-Korea
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• v.9 no.3
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• pp.29-34
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• 2004

To investigate characteristics and micro-explosion of single-droplets of emulsified fuel, water is mixed with diesel oil by using ultrasonic energy fuel feeding system. The fuel characteristics is analysed through H-NMR spectrum and micro-explosion phenomena of the emulsified fuel is also investigated. The life times of droplets of conventional diesel fuel, ultrasonic energy added diesel fuel and emulsified fuel we obtained additionally. According to this study, the micro-explosion phenomena of single-droplets happen in atmospheric pressure condition, a curve form of emulsified fuel's life tim is different from diesel fuel's one and the change of chemical structures is a cause of ultrasonic-energy-added diesel fuel effect.