• 제목/요약/키워드: Vascular anomaly

검색결과 85건 처리시간 0.031초

비전형적인 심하복벽동맥의 주행을 파악하기 위한 수술 전 CT Angiography의 유용성 (Atypical Patterns of Deep Inferior Epigastric Artery: Clinical Implication of Preoperative CT Angiography)

  • 이택종;김성찬;엄진섭;김은기
    • Archives of Reconstructive Microsurgery
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    • 제21권1호
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    • pp.8-13
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    • 2012
  • Purpose: Purpose: The free deep inferior epigastric artery perforator (DIEP) flap is a popular option for autologous breast reconstruction. However, the anatomy of the deep inferior epigastric artery(DIEA) may vary from one individual to another. Unexpected vascular anomaly can confuse the surgeon and affects on the safety of the free DIEP flap. Materials and Methods: Thirty five consecutive patients who underwent free DIEP/TRAM flap for immediate breast reconstruction between Mar. 2010 and Oct. 2010 were enrolled in this study. Computed tomography angiography (CT angiography) of abdomen was evaluated part of our standard preoperative assessment: atypical patterns of DIEA/DIEP were evaluated by preoperative CT angiography and compared with intraoperative finding. Results: Atypical patterns of DIEA/DIEP which may affect preoperative planning were noted as the following: Circummusclar/subfascial DIEA (n=1), DIEA running underneath rectus muscle (n=8), septocutaneous perforator (n=3), peritoneo-cutaneous perforator (n=1), a large branch going into peritoneum (n=1), and very early division and muscle penetration of DIEA (n=1). Conclusion: Atypical DIEA/DIEP that might change the operation plan is not rare, so the individualized planning based on the preoperative CT angiography is recommended. Preoperative CT angiography could help to select reliable and easy-to-dissect perforator in free DIEP/TRAM breast reconstruction.

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모야모야병에서 염기성 섬모 세포 성장 인자의 역할 (The Role of Basic Fibroblast Growth Factor in Moyamoya Disease)

  • 김동석;최중언;김세혁;양국희;김현숙
    • Journal of Korean Neurosurgical Society
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    • 제30권1호
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    • pp.5-11
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    • 2001
  • Objectives and Importance : The present study investigated the levels of basic fibroblast growth factor(bFGF) in the CSF of patients with moyamoya disease and its clinical significance. Methods : The levels of bFGF in CSF, taken from 26 hemispheres of 14 moyamoya patients and 20 patients without vascular anomaly(control group), were measured by an enzyme-linked immunosorbent assay. We analyzed the correlation between the level of bFGF and the clinical factors such as age, onset pattern, development of neovascularization, and cerebral circulation. Results : The CSF of moyamoya patients contained a high concentration of bFGF to a significant extent. The bFGF level was apparently elevated in the patients in whom neovascularization from indirect revascularization, such as modified encephalo-duro-arterio-synangiosis(EDAS) was well developed. A linear correlation between the values of bFGF and clinical progression was noted. Conclusions : The elevation of bFGF in moyamoya disease seems to be specific. Clinically, the bFGF level may be considered a useful indicator to predict the efficacy of indirect revascularization.

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Clinical Outcome of Nonfistulous Cerebral Varices: the Analysis of 39 Lesions

  • Kim, Hye Seon;Park, Seong-Cheol;Ha, Eun Jin;Cho, Wong-Sang;Kim, Seung-Ki;Kim, Jeong Eun
    • Journal of Korean Neurosurgical Society
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    • 제61권4호
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    • pp.485-493
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    • 2018
  • Objective : Cerebral varices (CVs) without an arteriovenous shunt, so called nonfistulous CVs, are very rare, and their etiology and natural course are not well understood. The aim of this study is to evaluate the clinical outcomes of nonfistulous CVs by the analysis of 39 cases. Methods : From 2000 to 2015, 22 patients with 39 nonfistulous CVs (${\geq}5mm$) were found by searching the medical and radiologic records of our institute. Clinical data and radiological data including numbers, sizes and locations of CVs and associated anomalies were retrospectively collected and analyzed. Previously reported cases in literature were reviewed as well. Results : The mean age of the patients was 21 years (range, 0-78 years). On average, $1.8{\pm}1.2CVs$ were found per patient. CVs were categorized as either fusiform or saccular depending on their shapes. Two patients had saccular type CVs, seventeen patients had fusiform types, and three patients had both fusiform and saccular CVs. Eight patients had associated compromise of the vein of Galen and the straight sinus. Four of those patients had sinus pericranii, as well. Five patients had CVs that were distal draining veins of large developmental venous anomalies. One patient had associated migration anomaly, and two patients had Sturge-Weber syndrome. Six patients with an isolated cerebral varix were observed. Of the 39 CVs in 22 patients, 20 lesions in 14 patients were followed up in outpatient clinics with imaging studies. The average follow-up duration was 6.6 years. During this period, no neurological events occurred, and all the lesions were managed conservatively. Conclusion : Nonfistulous CVs seemed to be asymptomatic in most cases and remained clinically silent. Hence, we suggest conservative management.

우세우심실 또는 우단심실증에서의 변형 Fontan 수술 (Modified Fontan Procedure for Single or Dominant Right Ventricle)

  • 백완기
    • Journal of Chest Surgery
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    • 제24권3호
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    • pp.310-321
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    • 1991
  • Between April 1986 and September 1990, 34 patients with a single or dominant right ventricle underwent modified Fontan procedure for definite palliation in Seoul National University Children`s Hospital. Their age at operation ranged from 8 months to 14 years [Mean 5.5 years]. The ventricular chamber was solitary and of indeterminate trabecular pattern in 6 patients. 28 patients had posteriorly located rudimentary chamber, all of which were trabecular pouches having no communication with outlet septum. The patterns of atrioventricular connection were common inlet[9], double inlet [11], left atrioventricular valve atresia [12] and right atrioventricular valve atresia with L-loop [2]. Pulmonary outflow tracts were atretic in 7 patients and stenotic in 26 patients. Major associated anomalies included anomalous systemic venous drainage [15], dextrocardia [12] and total anomalous pulmonary venous connection[3]. Shunt operations were previously performed in 13 patients and pulmonary artery banding and atrial septectomy in 1 patients. Surgery included intraatrial baffling in 26 patients, bidirectional cavopulmonary shunt in 13 patients, atrioventricular valve obliteration in 3 patients and atrioventricular valve replacement in 3 patients. Central venous pressure measured postoperatively at intensive care unit ranged from 18cm H2O to 28cm H2O [mean 23.2cm H2O]. Hospital mortality was 35.3% [12/34], all died out of low output syndrome. Suspected causes of low output syndrome include ventricular dysfunction [8], hypoplastic or tortuous pulmonary artery [2] and elevated pulmonary vascular resistance [2]. 19 patients had 31 major complications including low output syndrome [18], arrhythmia [4], acute renal failure [3] and respiratory failure [3]. Mortality rate was significantly higher in the groups receiving intraatrial baffling and AV valve replacement respectively [p<0.05]. 20 patients were followed up postoperatively with the mean follow-up period 15.0$\pm$11.6 months. There were no late death and follow-up catheterization was performed in 10 patients. Mean right atrial pressure was 15.4$\pm$6.8mmHg and ventricular contraction was reasonable in all but one case. Thus, Fontan principle can be applied successfully to all the patients with complex cardiac anomaly of single ventricle variety and better results can be anticipated with judicious selection of patient and improvement of postoperative care.

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산전 초음파로 발견되고 출생 후 4회의 코일 색전술과 심 교정술로 치료된 심실 중격 결손을 동반한 선천성 간내 문맥전신성 단락 1례 (A Case of Congenital Intrahepatic Portosystemic Shunt Associated with VSD Detected by Antenatal Sonography and Treated with Four Coil Embolizations and Open Heart Surgery after Birth)

  • 나지윤;김은선;김상덕;김이경;김한석;최중환;천정은;정진욱
    • Neonatal Medicine
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    • 제15권2호
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    • pp.176-182
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    • 2008
  • 드문 선천성 문맥전신성 단락에 대한 표준화된 치료는 없으나 저자들은 출생 직후부터 심부전 증상을 보인 환아에서 심실 중격 결손증을 동반한 선천성 문맥전신성단락을 4회의 코일 색전술 및 심 교정술로 치료한 증례를 경험하였기에 문헌고찰과 함께 보고하는 바이다.

자기공명혈관조영술로 진단된 제2형 전환추동맥(Proatlantal Artery): 증례 보고 (Persistent Proatlantal Artery in Magnetic Resonance Angiography: A Case Report)

  • 전성우;장혁원;김미정;조지형
    • Investigative Magnetic Resonance Imaging
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    • 제17권1호
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    • pp.55-58
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    • 2013
  • 전환추동맥은 드물게 보고된 태생기 경-기저동맥문합 잔류동맥의 하나이다. 태생 3주경에 발생하는 경-기저동맥문합은 삼차동맥, 귀동맥, 설하동맥, 그리고 전환추동맥으로 이루어지며, 정상인에서는 태생 6주경 전환추동맥을 마지막으로 모두 퇴화된다. 일반적으로 전환추동맥은 주로 내경동맥에서 기원하며 경추 가로돌기구멍을 통과하지 않는 제1형과, 외경동맥에서 기원하여 첫째 경추 가로돌기구멍을 통과하는 제2형으로 나뉘며, 임상적인 증상을 일으키는 경우는 드물다. 그러나 비교적 잘 동반되는 척추동맥의 무형성을 포함한 두개강내 동맥기형이 있을 수 있으며, 이는 경동맥 내막 절제술 및 외경동맥 색전술 등의 시술시 의의가 있어 심도 있는 이해가 필요하다. 이에 저자들은 자기공명혈관조영술로 진단된 제2형 전환추동맥 증례보고와 문헌고찰을 하고자 한다.

지속성 좌측 상대정맥 환자에서 발생한 드문 색전성 뇌졸중 (Unusual paradoxical embolic stroke in a patient with persistent left superior vena cava)

  • 권태훈;최강운;김병준;조재호;이재영;박규환;이상희;손장원
    • Journal of Yeungnam Medical Science
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    • 제32권2호
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    • pp.118-121
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    • 2015
  • Cardiogenic embolic stroke accounts for approximately 20% of ischemic strokes and the likelihood of its recurrence is high. Paradoxical embolism may be an important cause of cardioembolic stroke, which can be evaluated through multiple diagnostic modalities including transesophageal echocardiography (TTE) or transcranial Doppler. A persistent left superior vena cava (PLSVC) is a rare congenital vascular anomaly, which mainly drains to the right atrium via the coronary sinus. Although rare, PLSVC draining into the left heart predisposes the patient to paradoxical embolism through a right-to-left shunt. We report on a 78-year-old female patient with an ischemic stroke associated with PLSVC draining into the left atrium through the pulmonary vein, which was investigated via TTE with an agitated saline test and computed tomography.

누두흉과 선천성 낭종성 선종양 기형의 최소 침습적인 동시수술 -1예 보고- (Minimally Invasive Simultaneous Treatment for Congenital Cystic Adenomatoid Malformation associated with Pectus Excavatum - A case report -)

  • 조덕곤;조민섭;김경수;왕영필;조규도
    • Journal of Chest Surgery
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    • 제39권2호
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    • pp.171-175
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    • 2006
  • 최소 침습성 흉부수술은 최근에 가장 발전되어온 중요한 수술의 한 분야이다. 선천성 낭종성 선종양 기형은 비교적 드물게 발생하는 폐질환으로 누두흉, 선천성 심장 및 폐혈관 질환 같은 여러 가지 선천성 기형 등이 동반될 수 있다. 저자들은 우하엽 폐에 선천성 낭종성 선종양 기형이 있으며 누두흉이 동반된 5세 된 남아 환자를 최소 침습적인 방법으로 치료 경험하였다. 저자들은 흉강경을 이용하여 우하엽 폐절제술을 실시하였고, 동시에 누두흉에 대해서는 흉골 하 금속막대를 이용한 너스 술식으로 교정하였다. 이와 같이 이러한 질환에 대한 최소 침습적인 수술방법은 유용하고 미용적으로 우수하다.

소아의 Dieulafoy병 치험 1례 (A Case of Dieulafoy's Disease in a Child)

  • 이의성;오창희;김제우;정기섭;한석주
    • Pediatric Gastroenterology, Hepatology & Nutrition
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    • 제2권1호
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    • pp.80-84
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    • 1999
  • Dieulafoy's disease, a vascular anomaly mainly in the upper stomach, is a rare but potentially life-threatening cause of upper gastrointestinal bleeding. Pathogenesis is still controversial, but the most accepted theory is that a persistent caliber vessel in the submucosa is exposed by a small mucosal erosion leading to massive bleeding. The bleeding site is usually within 6 cm of the esophagogastric junction in the cardia or fundus of the stomach. The treatment of choice is therapeutic endoscopy or surgery. The age of patients reported is mainly between 50 and 70 years, and patients of pediatric age are extremely rare. We are reporting a 5-year-old male patient who had Dieulafoy's disease which was diagnosed by emergency upper gastrointestinal endoscopy. Endoscopic finding was a nodular lesion with an adherent clot on the lessor curvature of the stomach 2 cm below the esophagogastric junction. Epinephrine and $Beriplast^{(R)}$ was injected in the lesion. On the second day after endoscopic sclerotherapy, the patient had recurred massive hematemesis and accompanying shock. So we performed gastrotomy and ligation. After the operation, he showed an improved general condition and was discharged at the 12th hospital day.

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개에서 컴퓨터단층촬영에 의해 진단된 후대정맥 분절 무형성증 2 례 (Computed Tomographic Findings of Segmental Caudal Vena Cava Aplasia in Two Dogs)

  • 이인;최수영;이기자;최호정;이영원
    • 한국임상수의학회지
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    • 제32권2호
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    • pp.196-199
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    • 2015
  • 유선종양의 병력이 있는 7년령의 중성화하지 않은 암컷 닥스훈트견과 중성화하지 않은 수컷 요크셔테리어견이 유선종양의 전이평가와 정기 검진을 위해 내원하였다. 두 증례 모두에서 복부 컴퓨터단층촬영 검사가 실시되었으며, 후대정맥 분절 무형성증이 우연히 발견되었다. 닥스훈트견은 복강내의 신후-후대정맥 분절이 결손되었고, 요크셔테리어견은 신전-후대정맥 분절이 신후-후대정맥 분절과 연속되지 않았다. 두 증례 모두에서 장골 정맥의 합류로 형성된 신전-후대정맥 분절이 확장된 홀정맥으로 연속되었다. 개에서 컴퓨터 단층촬영을 이용하여 복강내 혈관 기형을 평가할 때, 우연히 발견될 수 있는 후대정맥 분절 무형성증을 고려해야 한다.