• 제목/요약/키워드: Systemic capillary leak syndrome

검색결과 2건 처리시간 0.016초

소아에서 발생한 전신성 모세혈관 누출 증후군(Systemic Capillary Leak Syndrome) 1례 (A Case of Systemic Capillary Leak Syndrome in a Child)

  • 이택영;정유미;강희경;하일수;정해일;최용
    • Clinical and Experimental Pediatrics
    • /
    • 제45권10호
    • /
    • pp.1298-1301
    • /
    • 2002
  • 전신성 모세혈관 누출 증후군(Systemic Capillary Leak Syndrome)은 Clarkson 등이 처음 기술한 이래 50여명의 증례가 보고된 매우 드문 질환이며, 소아에서는 1995년 Ivan Foeldvari 등이 보고한 예가 유일하다. 저자들은 빈호흡, 청색증, 부종, 소변량 감소를 주소로 내원한 6세 여아에서 저혈압, 혈액농축, 저알부민혈증의 소견을 확인하고 전신성 모세혈관 누출 증후군으로 진단한 예를 문헌 고찰과 함께 보고하는 바이다.

전신성 모세혈관 누출 증후군으로 인한 만성 신질환 1예 (A Case of Chronic Renal Failure Associated with Systemic Capillary Leak Syndrome)

  • 백선하;신나라;김효진;한미연;최동주;방수미;김세중;백진호
    • Journal of Yeungnam Medical Science
    • /
    • 제29권2호
    • /
    • pp.145-149
    • /
    • 2012
  • Systemic capillary leak syndrome (SCLS) is an unusual entity characterized by hypovolemic shock, hemoconcentration, and hypo-albuminemia associated with paraproteinemia as a result of marked capillary hyper-permeability. Complications of this syndrome can include compartment syndromes, pulmonary edema, thrombosis, and acute kidney injury. This paper reports a case of severe SCLS accompanied by acute tubular necrosis caused by hypoperfusion and myoglobinuria secondary to rhabdomyolysis, which resulted in chronic kidney disease that necessitated hemodialysis. However, there have been rare data of residual end-organ damage after acute attacks in Korea. Therefore, this paper reports a case of complicated SCLS enough to hemodialysis and that developed into chronic kidney disease.

  • PDF