• Journal of mucopolysaccharidosis and rare diseases
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• v.4 no.1
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• pp.11-13
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• 2018

In Malaysia, diagnosis and treatment of patients with mucopolysaccharidoses (MPS) is mainly localized at Hospital Kuala Lumpur, which is the national referral center for rare diseases. To date there are 83 patients diagnosed with MPS in our center, with MPS II being the commonest. The Malaysian National Medicines Policy second edition has a specific section on the orphan drugs which includes recombinant human enzyme for enzyme replacement therapy (ERT) in MPS. So far, National Pharmaceutical Regulatory Agency Malaysia has approved recombinant human enzyme for MPS types I (Loranidase), II (idursulfase), IVA (elosulfase alfa), and VI (Galsufase). Access to Idursulfase beta (another recombinant human enzyme for MPS II) and vestronidase alfa-vjbk (MPS VII) required special authorization on named patient basic. Currently there are 25 patients receiving ERT, 70% of the funding are from Ministry of Health (MOH), the remaining 30% are from various charitable funds and humanitarian programs. Thirteen newly diagnosed patients have to queue for an additional fund. Four patients have been treated with Hematopoietic stem cell transplant. MOH has also published guidelines regarding the patient selection criteria for ERT and treatment monitoring schedule.

• Monthly Duck's Village
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• s.85
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• pp.40-46
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• 2010

물새류의 생산물은 총 인구수의 영양학적 기준을 향상시킬 수 있다. 물새류는 사료에 있어서 인간의 식재료와 경합이 적다. 닭과 비교하였을 때, 오리와 거위는 현재 고기 및 식란 생산에 미미한 수준이다. 하지만 특정 국가에서는 오리와 거위로부터 많은 양의 고기와 식란을 생산하고 있으며 지난 20년간 생산이 급격히 증가하였다. 오리고기 생산량은 1991년 76만톤에서 2007년 220만톤으로 상승세를 보였으며, 이는 총 가금산물의 6.6%에 해당하는 양이다. 오리 및 거위고기를 가장 많이 생산하는 나라는 중국으로 각각 전 세계 생산량의 65%, 94%를 차지하고 있다. 중국과 동남아시아 몇 국가에서는 오래전부터 오리식란을 소비해 왔으며, 이는 총 소비량의 10~30%를 차지하고, 물새류의 깃털 및 다운도 널리 이용되고 있다. 오리와 거위를 사육하는 전업농가는 동물 복지와 친환경 등의 요구수준에 맞춰 사육, 영양관리 등을 하는 데 많은 노력을 기울일 필요가 있다. 이러한 농가들은 적절한 기술 및 향상된 개체 확보를 통하여 생산성, 수익, 안전성을 향상할 수 있도록 한다. 효율적인 물새 사양 관리를 위하여 잠재 성장력 활용, 자연 행동 수행, 복지 관리 등 쾌적한 환경 제공이 필요하다. 물새류는 닭에 비해 고온 습윤한 지역에서 잘 견디며, 이러한 조건 하에 물새류는 중요한 식량자원으로 활용될 수 있다.

• Journal of the Korean Professional Engineers Association
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• v.44 no.4
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• pp.24-27
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• 2011

Every government rallies with the private sector to support its traditional cuisines. In Korea, the effort to globalize traditional dishes began with the governments official declaration of "Hansik Globalization" in 2008. Now the mission of globalizing hansik has emerged as one of the most valuable propositions in creating a new value-added rural economy, sharing growth with the tourism industry. The global food industry is reported to be bigger that of the information technology industry by 5.6 times and the automobile industry by 2.5 times as of 2008. And considering that hansik is almost unknown outside of Korea, the potential for growth is huge.

• Korean Journal of Remote Sensing
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• v.39 no.5_4
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• pp.1069-1073
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• 2023

A research project titled as Development of Comprehensive Land Management Technology using Satellite Image Information, funded by the Ministry of Land and Transportation, is being conducted to improve the efficiency of land management and to boost satellite image utilization in the private sector. This editorial describes the introduction of the project and papers presented in this special edition.

• Journal of Korean Medical classics
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• v.30 no.1
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• pp.87-110
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• 2017

Objectives : The purpose of this paper is to study the form, contents and special features found in Qianhuang's life, books, his relationship with his disciples and Shanghansuyuanji's edition and its pass-ons. Methods : The best version among Shanghansuyuanji's copies was selected. Based on this, Qianhuang's life, books and his relationship with his disciples were studied, and Shanghansuyuanji's edition and its pass-ons, form and contents were analyzed. Results & Conclusions: Through study, first I see that Qianhuang was born in the early period of Qing Dynasty and died after the publication of Shanghansuyuanji, Suwen's annotation book probably had not been published yet, his mentor were Fangyouzhi and Yujiayan. Second, I see that he organized Shanghanlun sentences from his own perspective of cause of a disease and cure method. Third, I see that he viewed the diseases of six meridians with the perspective of yinyang and explained the concept of three yins and three yangs in relation to yinyang's ups and downs, and his Yuggyeongjasu theory made possible various interpretations of disease mechanism. Fourth, I see that he held critical views towards the Shanghanlun sentences through the Error Discrimination. Fifth, I see that he viewed disease mechaniam in interdependent relationships or from the point of view of the School of Warming and Tonifying through the Meaning of Herbal Formula. Sixth, I see that he sometimes quoted Neijing in proper ways that fit the disease mechanism in Shanghanlun. On the other hand, he quoted Neijing solely for the reason that identical words are used, but some of these were not proper. Additionally, he criticized the aforementioned annotators for improper quoting Neijing. Consequentially, for reasons mentioned above Qianhuang's Shanghansuyuanji has great importance as a Shanghanlun annotation book.

• Journal of Korean Library and Information Science Society
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• v.48 no.3
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• pp.63-81
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• 2017

This study investigated general problems concerning the social welfare field in the KDC 6th edition based comparative analysis academic characteristics and classification system, and suggested on some ideas for the improvements of them. Results of the study are summarized as follows. First, a main field of the social welfare is generally divided into a general social welfare, social works, and social welfare services to special classes and groups including people with disabilities, young people, aged, women, and families. Second, I analyzed on social welfare from the collection database at the National Library of Korea. Based on analysis of the data. the keyword frequency of social welfare policy and management, pensions, care services, and support works for the underprivileged was relatively high. Third, modified classification of items was basically performed through the academic characteristics of the social welfare and the keyword analysis, and maintaining the existing KDC classification system caused less confusion as much as possible.

• Journal of Korean Association for Spatial Structures
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• v.8 no.2
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• pp.85-93
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• 2008

This study summarizes the results of a research project aimed at investigating the inelastic rotation capacity of beam-column joints of reinforced concrete special moment frames. All of the test specimens were classified as special moment frame (SMF), based on the design and detailing requirements of the ACI 318-02 provisions. The acceptance criteria, originally defined for steel moment frame connections in the 1997 edition of the AISC Seismic provisions, were used to evaluate the beam-column joints of the reinforced concrete moment frames. A total of 39 test specimens were examined in detail. Most of the joints that satisfy the design requirements for special moment frame structures were found to be ductile up to a plastic rotation of 3% without any major degradation in strength. This is mainly due to the stringent ACI 318-02 requirements for special moment frame joints. The presence of transverse beams increases confinement and shear resistance of joints, which results in better performance than for joints without transverse beams. All of the SMF connections that satisfy the ACI 318-02 limitations on joint shear stress turned out to meet the acceptance criteria.

• Proceedings of the Korea Institute of Fire Science and Engineering Conference
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• 1997.11a
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• pp.439-449
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• 1997

Studies have been carried out to determine the effect of sprinklers on fires typical of a number of occupancies including simulated of office furniture, supermarkets, carpet displays, libraries, video stores and liquor stores. After surveys of actual fire loads, the experiments were conducted in a specially designed sprinklered fire-calorimeter with a collecting hood 6 m x6 m leading to a vertical duct 1 m in diameter. Details of the rig are given elsewhere [1]. Only well ventilated fires were studied. Rate of heat release and production of various toxic chemicals were monitored during the tests. Both sprinklered and unsprinklered fires were used. The results were used to establish the unsprinklered burning behaviour and the fire-control effects of sprinklers. Before sprinkler operation, the rate of fire growth could be modelled as 12_fires as given in NFPA 92B (1991 Edition) [2]. It was found that operation of sprirnklers controlled but did not extinguish the fires. This was expected as parts of the fire load were shielded from the spray. Also there were significant increases in the concentration of carbon monoxide when the sprinklers operated. Sprinklers had little effect on the concentrations of other toxic products measured. The results from the tests were extrapolated to large single storey buildings for the same occupancy classes and the results used to compare the required and the available escape times for different occupancies, particularly whether the use of sprinklers would improve the chances of escape from those premises. It was found that in most of the cases studied, adequate escape times will be available without any special measures. For very rapid fire growths, however, special measures, such as availability of trained staff may be needed. Standard response sprinklers will have little impact.

• Journal of Korean Medical classics
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• v.22 no.4
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• pp.51-54
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• 2009

While we study the book "Somun(素問)", we have to take Wangbing(王冰) Note as reference, which has to be understood by later generation on reading the book Sin-gyojeong(新校正) of Imeok(林億) from Song dynasty. At the final period of Edo in Japan, the famous Han medical expert, Yamada(山田) Gyoukou(業廣) sought a complete new way to compile a book named "Somunchajujipso(素問次注集疏)", a notes and commentaries work combined the original text of "Somun(素問)", Wangbing(王冰) Note and Sin-gyojeong(新校正) by taking the reference of generations medical books and notes both China and Japan. There have been many books to give notes on "Somun(素問)" in many generations, but less of them giving notes to the original text, but to Wangbing Note a little bit at most. In "Somunchajujipso", textual research and notes are given as a special example to the forward, original text and explanation part of "Somun", Song dynasty edition. Especially the detail explanation to the forward part of Imeok(林億), no one has done better than Gyoukou(業廣) until now. It sufficiently shows Gyoukou's(業廣) enriched knowledge accumulated by years hard research in Confucian classics, history and medical books, which enable it a worthy reference statement. The issued of the book "Somunchajujipso(素問次注集疏)" expands a new area for the research of "Somun" and present new research improvement of "Somun" in Japan.

• Journal of the Korean Society of Radiology
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• v.7 no.6
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• pp.383-387
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• 2013

Diagnostic imaging systems play a critical role in obtaining anatomical images, which increases the frequency of inspection all over the world. However the likelihood that patients are exposed to relatively high radiation dose increases, which may lead to an increase of patient dose due to unnecessary radiation exposure unless appropriate management is accompanied. Thus the revised edition of IEC 60601-2-44 which is constancy tests for CT equipment which is designated as special medical equipment and is subject to safety management was studied. The results suggested the 3rd has been revised rationally in order to overcome the limitations in the 2nd by adopting clear and enhanced references, which implies the replacement of IEC 60601-2-44 2nd edition with IEC 60601-2-44 3rd will prevent the patients from the harm from improper medical equipment.