• 대한두개안면성형외과학회지
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• 제20권2호
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• pp.112-115
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• 2019

Linear scleroderma en coup de sabre (LScs) is a variant of localized scleroderma. This disease typically occurs in patients in their 20s or younger individuals and predominantly occurs in the forehead area. A 26-year-old man with linear scleroderma was surgically treated at our center with Medpor (porous polyethylene) and dermal fat graft for the forehead lesion. After 26 months of postoperative follow-up, the depressed lesion that appeared scarred as well as the margins improved significantly. The surgical treatment of LScs using Medpor and dermal fat graft is an effective treatment modality that can increase patient satisfaction.

• 한국정보전자통신기술학회논문지
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• 제8권5호
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• pp.367-372
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• 2015

본 연구에서는 피부 경화증 환자의 증상정도 알고리즘을 개발하였다. 진단 방법은 피부경화증을 흑백처리 한 후 정상인의 이미지와 비교하였다. 채도, 밝기 및 콘트라스트 조정의 필터를 프로세스를 통해 변환 하였다. 그 결과 화상이 선명한 경화증의 증상을 구별하는데 사용될 수 있었다. 건강한 사람의 영상에서 경화증 환자의 이미지를 주고 폐쇄 프로세스를 적용하여 진폭의 차이로 정상인과 피부 경화증 환자를 결정하였다.

• 대한두개안면성형외과학회지
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• 제18권3호
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• pp.166-171
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• 2017

Background: Localized scleroderma is characterized by a thickening of the skin from excessive collagen deposits. It is not a fatal disease, but quality of life can be adversely affected due to changes in skin appearance, joint contractures, and, rarely, serious deformities of the face and extremities. We present six cases of localized scleroderma in face from our surgical practice. Methods: We reviewed six localized scleroderma cases that were initially treated with medication and then received follow-up surgery between April 2003 and February 2015. Six patients had facial lesions. These cases presented with linear dermal sclerosis on the forehead, oval subcutaneous and dermal depression in the cheek. Results: En coup de sabre (n=4), and oval-shaped lesion of the face (n=2) were successfully treated. Surgical methods included resection with or without Z-plasty (n=3), fat graft (n=1), dermofat graft (n=1), and adipofascial free flap (n=1). Deformities of the affected parts were surgically corrected without reoccurrence. Conclusion: We retrospectively reviewed six cases of localized scleroderma that were successfully treated with surgery. And we propose an algorithm for selecting the best surgical approach for individual localized scleroderma cases. Although our cases were limited in number and long-term follow-up will be necessary, we suggest that surgical management should be considered as an option for treating scleroderma patients.

• 한국균학회지
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• 제50권2호
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• pp.115-123
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• 2022

Two new records of Scleroderma species from South Korea are described here. Comprehensive taxonomic studies of Scleroderma specimens were conducted at the Korea National Arboretum. Based on morphological and molecular data (fungal barcode sequences), two new records (S. laeve and S. nastii) were confirmed. Herein, morphological descriptions, including Scanning Electron Microscope (SEM) images of basidiospore ornamentation, and a taxonomic key of Korean Scleroderma species are provided.

• 대한한방소아과학회지
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• 제33권4호
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• pp.26-36
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• 2019

Objectives This study is to report a case on a patient with scleroderma caused by juvenile idiopathic arthritis. The patient's symptoms were improved by the complex Korean medicine treatment. Methods The patient was treated for 20 days with acupuncture, moxa, physical therapy, herbal medicine (Ganghwalbinsosan, 羌活檳蘇散), and herbal dressing therapy(Dohongsamultang, 桃紅四物湯). Results NRS and mRSS were used evaluate patient's symptoms daily to assess the changes. After 20 days of the treatments, the patient showed improvement of the symptoms including pain, pruritus and scleroderma of the left leg. Conclusions This case study showed that symptoms in the patient with scleroderma caused by juvenile idiopathic arthritis were dramatically improved by the Korean medicine treatment which includes acupuncture, moxa, herbal medicine, and herbal dressing therapy.

• 대한소아치과학회지
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• 제32권2호
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• pp.256-261
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• 2005

피부 경화증(scleroderma)은 만성 결체조직 질환으로 정확한 원인은 밝혀지지 않았으나 자가 면역 질환으로 알려져 있다. 대개 $30{\sim}50$세의 여성에서 호발하며 소아에서는 매우 드물다. 장기의 이환여부에 따라 국소성과 전신성 피부 경화증으로 분류할 수 있다. 국소적 형태는 예후가 양호하고 피부에만, 또는 피하 근육까지 이환되며, 내부 장기에는 이환되지 않는다. 전신적인 형태는 피부와 구강점막 및 위장계, 호흡계, 심혈관계 등을 포함하늘 전신 다발적 발생 (multisystemic involvement)이 특징적이다. 안면피부 이환시 작고 예리한 코, 무표정한 응시 (expressionless stare), 좁아진 입모양(narrow oral aperture) 등이 특징적이다. 대개 레이노 현상(Raynaud's phenomenon)이 존재하며 질환이 진행되면서 개구장애와 혀, 치은의 경화가 나타나게 된다. 피부 석회증(calcinosis cutis), 레이노현상(Raynaud's phenomenon). 식도 기능부전(esophageal dysfunction), 공지증(sclerodactyly), 모세혈관 확장증(telangioectasia)이 복합된 질환을 크레스트 증후군(CREST syndrome)이라 부른다. 피부 경화증의 치료는 국소적 및 전신적 스테로이드 치료, collagen cross-link inhibitor (D-penicillamine), 면역억제제 등을 사용한다. 개구제한의 치료는 설압자를 이용한 mouth stretching exercise를 통해 개선될 수 있다. 본 증례에서는 국소성 피부 경화증으로 진단되고 개구제한이 있는 6세 남아에게 아산화질소와 enflurane을 이용한 깊은 진정요법을 이용하여 상하악 제 1, 2 유구치의 우식치료 치험례를 보고한다.

• 대한한방내과학회지
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• 제25권2호
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• pp.344-351
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• 2004

Systemic sclerosis Sine scleroderma(ssSSc) is an uncommon subtype of Systemic sclerosis(SSc), which is believed to attack internal organs without causing changes in the skin. Electrogastrography has been known to be a simple, non-invasive, and effective method in assessing gastric motility. In this new study, a case of Systemic sclerosis Sine Scleroderma exhibiting gastric symptoms was observed. For this, we applied herbal medicine. manual acupucture, electro-acupucture, and lumbar skin wanning. After applying these therapies, both systemic and dyspeptic symptoms of the patient improved. Electrogastrography suggests a relation between gastric myoelectrical activity and the patient's improvement in dyspeptic symptoms. Therefore, based on study of Oriental medical classics and recent medical articles, clinically emperical success in treating gastric dysmotility was seen in a patient with Systemic sclerosis Sine Scleroderma.

• Journal of Chest Surgery
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• 제21권5호
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• pp.929-934
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• 1988

Progressive systemic sclerosis is a disease of unknown origin and uncommon in the east area. We experienced one case of severe peptic esophageal stricture due to esophageal scleroderma. The patient`s life quality was improved with the esophageal reconstructive procedure using reversed tubed gastric pedicle and his body weight was normalized with regular diet.

• Tuberculosis and Respiratory Diseases
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• 제50권4호
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• pp.493-498
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• 2001

저자들은 4개월간의 호흡곤란을 주소로 내원하여 피부병변은 없었지만 흉강경하 폐생검과 식도내압검사, 핵항체검사 등으로 경피증을 확진한 Systemic sclerosis sine scleroderma 1례를 경험하였기에 문헌 고찰과 함께 보고하는 바이다.

• Maxillofacial Plastic and Reconstructive Surgery
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• 제37권
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• pp.29.1-29.7
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• 2015

Facial asymmetry is found in patients with or without cosmetic facial alterations. Some patients have facial asymmetry that manifests underlying skeletal problems, while others have only limited soft-tissue facial asymmetry. Orthognathic surgery brings about a dermatic change, as soft tissue covers underlying bones. Limited soft-tissue asymmetry, meanwhile, is difficult to correct. The treatment modalities for the creation or restoration of an esthetically pleasing appearance were autogenous fat grafts, cartilage graft, and silicon injections. A young female patient had right-side facial asymmetry. The clinical assessment involved visual inspection of the face and palpation to differentiate soft tissue and bone. Although the extra-oral examination found facial asymmetry with skin atrophy, the radiographic findings revealed no mandibular atrophy or deviation. She was diagnosed as localized scleroderma with muscle spasm. In conclusion, facial asymmetry patients with skeletal asymmetry can be esthetically satisfied by orthognathic surgery; however, facial atrophy patients with skin or subdermal tissue contraction need treatment by cosmetic dermatological surgery and orthodontic correction.