• Title/Summary/Keyword: RARITY

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Subglottic Adenoid Cystic Carcinoma with Lung Metastasis: A Case Report (폐전이를 동반한 성문 하에서 발생한 선양낭성암종 1예)

  • Park, Hyung-Soon;Choi, Hong-Shik;Hong, Soon-Won;Jeung, Hei-Cheul
    • Korean Journal of Bronchoesophagology
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    • v.16 no.1
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    • pp.68-72
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    • 2010
  • Adenoid cystic carcinoma (ACC) of larynx is a rare disease, accounting for less than 1% of laryngeal malignancies, These tumors arise almost exclusively in the subglottic and supraglottic regions, while the proportion of glottic ACCs is small. We describe a case of a young man with a subglottis adenoid cystic carcinoma, The patient underwent laryngeal microscopic surgery and radiotherapy, Five years after radiotherapy, local recurrence and distant metastasis Clung and kidney) was detected and he underwent palliative chemotherapy and local treatment. He is still alive for seven years after the initial diagnosis. The treatment strategies for laryngeal ACC are still controversial due to the rarity of the condition. We suggest that multimodality approach may be helpful in deciding a treatment option, and thorough and consistent follow-up for recurrence is mandatory for these patients.

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Wild Prunus yedoensis and its putative parent in Mt. Halla (II) (한라산 자생 왕벚 및 추정양친에 관한 연구 (II))

  • 한창열
    • Journal of Plant Biology
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    • v.8 no.1_2
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    • pp.11-18
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    • 1965
  • Since Taquet's first discovery of wild P. yedoensis at Mt. Halla, Korea, in 1908, its morphological chracteristics and question of origin of cultivated yedoensis have given controversies to the botanists. Takenaka, through his experiments on the hybridity of cultivated P. yedoensis, recently holds the opinion that P. yedoensis might have originated in Izu peninsula, Japan. The author presents the summarized report on the wild P. yedoensis and its putative parents based on his 2 years' investigated carried out at Mt. Halla during his breeding experiment of genus Prunus. The species of cherry tree used in the present investigation were identified by Prof. Mankyu Park and Mr. Jonghyu Pu, Korean taxonomists. 1) Wild cherry trees which grow wild in Mt. Halla and whose blooming season is April are mostly P. subhirtella var. pendula form. ascendens and P. donarium P. yedoensis is rare in number, around 10 individuals, having been found in a half century. 2) Individuals of wild yedoensis are variable in some of their morphological characteristics. This is, also, true in other species of Prunus. 3) Wild yedoensis whose vigorous growth, sterility, and rarity in number suggest hybrid origin, has intermediate characteristics between the P. subhirtella and P. donarium. 4) Due to the abnormal weather of the island and various environmental factors such as havbitats, some of the early-blooming subhirtella and late-blooming donarium would bloom at the same time, giving these two species the changes to cross. 5) Wild yedoensis is slightly different in some of its quantitative characters from cultivated species.

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The Characteristics of the Cultural Tourism Resources Distribution along the Nakdong River Basin

  • Yhang, Wii-Joo
    • Journal of Environmental Science International
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    • v.12 no.8
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    • pp.835-840
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    • 2003
  • Many various kinds of tourism resources have been distributed along the Nakdong river basin. Previous researches have focused mainly on environmental studies, including water quality control, industrial use of water, biodiversity, etc, with little research done in the field of tourism studies. Central to this study, therefore, is the identification and analysis, from the perspective of cultural tourism, of the area's distribution and characteristics of cultural properties registered by the MOCT. Review of related literature reveals : 1) spatial range bound with the jurisdiction of the river basin like DREO and NRBEO ; 2) analytical subjects limited to cultural properties designated by the three different administrative units of government, city and province. Along with the DREO's predominance over the NRBEO in the total number of cultural properties, the result finds that two cities, Andong and Gyeongju of Gyeongbuk are assigned ownership of most of the cultural properties under the jurisdiction of DREO, while Gyeongnam that of most of the ones under the NRBEO. However, those findings suggest the simple number of cultural properties with no significant level of importance and rarity value reflected. Therefore, future studies need to develop quantified modelling keeping cultural variables in mind and create cultural indices of the competitiveness of the local governments.

A spindle cell squamous cell carcinoma on the cheek presenting with in-transit metastases and a satellite lesion

  • Lee, Eui-Tae
    • Archives of Craniofacial Surgery
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    • v.21 no.1
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    • pp.58-63
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    • 2020
  • Spindle cell squamous cell carcinoma (SpSCC) is a biphasic tumor composed of squamous cell epithelial and spindle cell mesenchymal components, both of which are malignant. Cutaneous SpSCC can cause diagnostic and therapeutic difficulties because of its rarity, heterogeneity, morphological similarity to other cutaneous spindle cell neoplasms, and uncertain pathogenesis and prognosis, particularly when the squamous cell carcinoma component is minimal or missing. Intransit metastasis and satellite lesion (satellitosis) constitute a spectrum of non-nodal regional metastases. Here the author reports the first known case of cutaneous SpSCC presenting with intransit metastases and a satellite lesion, which were exceptionally aggressive. A 77-year-old female patient presented with a 3×3×0.5 cm mass on her right cheek. Despite wide excision and postoperative radiation, the patient resulted in local recurrence and multiple distant metastases within 3 months. If many high-risk factors-particularly satellitosis and in-transit metastases are observed in a tumor with epithelial to mesenchymal transition, then further wide excision and adjuvant chemoradiation should be considered early in the treatment process. A multidisciplinary approach could be the key to cure the most aggressive malignancies of the skin, as in other organs.

Perforated Early Gastric Cancer -A case report- (진행성 위암으로 오인된 조기위암 천공 1예)

  • Lee Moon Soo;Kim Sung Yong;Oh Sang Hyun;hCae Man Kyu;Chung Il Kwon;Baek Moo Jun;Park Kyung Kyu;Kim Chang Ho;Cho Moo Sik
    • Journal of Gastric Cancer
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    • v.1 no.1
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    • pp.64-67
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    • 2001
  • An exceedingly rare case of perforated early gastric cancer is reported. A 68-year-old man developed peritonitis due to perforation of early gastric cancer. An emergency radical operation was performed and was followed by an uneventful recovery. Histologic examination of the surgical specimen showed type III early gastric cancer composed of a signet ring cell carcinoma. Five years after surgery, the patients was alive with no evidence of tumor recurrence. The rarity of this complication in early gastric cancer is discussed, and a review of the literature is presented.

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Orthodontic and surgical management of cleidocranial dysplasia

  • Park, Tina Keun Nan;Vargervik, Karin;Oberoi, Snehlata
    • The korean journal of orthodontics
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    • v.43 no.5
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    • pp.248-260
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    • 2013
  • Cleidocranial dysplasia (CCD), an autosomal dominant disorder with a prevalence of 1 in 1,000,000 individuals, is mainly caused by mutations in Runx2, a gene required for osteoblastic differentiation. It is generally characterized by hypoplastic clavicles, narrow thorax, and delayed or absent fontanel closure. Importantly, its orofacial manifestations, including midfacial hypoplasia, retained primary teeth, and impacted permanent and supernumerary teeth, severely impede the well-being of affected individuals. Successful treatment of the orofacial problems requires the combined efforts of dental specialists. However, only a few successfully treated cases have been reported because of the rarity of CCD and complexity of the treatment. This article presents the University of California, San Francisco (UCSF) treatment protocol for the dentofacial manifestations of CCD based on two treated and 17 diagnosed cases. The records of two patients with CCD who had been treated at the UCSF School of Dentistry and the treatment options reported in the literature were reviewed. The UCSF treatment protocol produced a successful case and a partially successful one (inadequate oral hygiene in the retention stage resulted in decay and loss of teeth). It provides general guidelines for successfully treating the orofacial manifestations of CCD.

Development of Evaluation Indices for Forest Landscape Classification (산림경관 등급화를 위한 평가지표 개발)

  • Kang, Mi-Hee;Kim, Seong-Il
    • Journal of Korean Society of Forest Science
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    • v.99 no.6
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    • pp.777-784
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    • 2010
  • The purpose of this study was to develop evaluation indices for forest landscape classification. The indices were chosen to enable forest managers to establish effective landscape management strategies through three times of focus group interviews and email survey with experts. The 13 landscape evaluation indices were finally divided into four categories. They were ecological health (degree of green naturality, degree of ecological naturality, disease and insect damage, crown vitality), aesthetic visual quality (naturalness, harmony, diversity, traditionality, aesthetic appreciation, rarity), and sensitivity (level of tourism/recreational use), interruptions (damaged land, artificial structures). The five-level was suggested for the forest landscape classification system.

A Study on Aesthetic Characteristics of T-shirt Design (티셔츠 디자인의 미적 특성)

  • Choi, Jung-Hwa
    • Fashion & Textile Research Journal
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    • v.9 no.4
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    • pp.363-372
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    • 2007
  • T-shirt has changed into advanced and stylish outwear by new paradigm, taste of consumer, awareness of recycling, spread of subculture, DIY culture, refusal of standardization and pursuit of high quality goods, etc. The purpose of this study was to analyze aesthetic characteristics of t-shirt designs that changed into diverse designs in world fashion college since 2000. The method of this study was to analyze documentaries, fashion magazines and internet fashion site. Aesthetic characteristics of t-shirt designs were expressed in deconstruction, mixture, integration and imitation. And each of external expressions and internal meanings was as follows: First, deconstruction was expressed in partial cutwork and three dimensional texture by sewing and construction drape. It means breaking the conventional structure and break-ing the boundary of t-shirt and another item and possibility of multi-vocal analysis. Second, mixture was expressed in collage of diverse ornaments, diverse fabrics and diverse patterns. It means exceeding the limit of material, elaboratenes and high quality of handwork, reflection of self-identity, brand image, fashion trend, consumer's psychology and mind of experimentation and couture. Third, integration was expressed in extension of length, width, use and style. It means unification of functions, deconstruction of items and extension of meanings and images. Forth, imitation was expressed in stain of dye, irregular and ripped sign, cut out, rough warp, drawing and washing, etc. It means subculture, rarity value, monopolization, diversity, familiarity, yearning and uniqueness.

Endoscopic Balloon Dilation for Treatment of Congenital Antral Web

  • Peck, Jacquelin;Khalaf, Racha;Marth, Ryan;Phen, Claudia;Sosa, Roberto;Cordero, Francisco Balsells;Wilsey, Michael
    • Pediatric Gastroenterology, Hepatology & Nutrition
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    • v.21 no.4
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    • pp.351-354
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    • 2018
  • Congenital antral webs are a rare but relevant cause of gastric outlet obstruction in infants and children. The condition may lead to feeding refusal, vomiting, and poor growth. Due to the relative rarity of the disease, cases of congenital antral web are frequently misdiagnosed or diagnosed with significant delay as physicians favorably pursue diagnoses of pyloric stenosis and gastric ulcer disease, which are more prevalent. We report a case of an eight-month-old female who presented with persistent non-bilious emesis, feeding difficulties, and failure to thrive and was discovered to have an antral web. The web was successfully treated with endoscopic balloon dilation, which resolved her symptoms. Two years later, the patient remains asymptomatic and is thriving with weight at the 75th percentile for her age.

Gastric Xanthoma in the Pediatric Population: A Possible Herald for Malignancy?

  • Russell, Joseph D.;Peck, Jacquelin;Phen, Claudia;Linehan, Janna L.;Karjoo, Sara;Nguyen, Johnny;Wilsey, Michael J.
    • Pediatric Gastroenterology, Hepatology & Nutrition
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    • v.23 no.1
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    • pp.110-114
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    • 2020
  • Gastric xanthoma is frequently an incidental finding on upper endoscopy in adults. Gastric xanthomas (GX) can be mistaken for malignancies and warrant prompt histologic diagnosis. The underlying etiology is not fully understood; however, it has been linked to Helicobacter pylori gastritis and gastric cancer. GX in the pediatric population is largely unreported in the literature. Because of the relative rarity, documentation with case reports are essential to provide as much data as possible to see if there is a correlation between GX and malignant potential in the pediatric population. Our group is reporting two cases, a 10-year-old male and a 7-year-old male, both who presented with chronic dysphagia, upper abdominal pain, nausea, vomiting, and loss of appetite. Upper endoscopies for both patients revealed small polypoid lesions located in the antrum with foamy histiocytes on histology, leading to the diagnosis of gastric xanthoma.