• Journal of Chest Surgery
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• 제19권2호
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• pp.319-324
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• 1986

Congenital coronary arteriovenous fistula is uncommon disease, and was first described by Krause in 1865. About 20% of the cases, it associates additional congenital heart diseases. A 5-year-old female patient was diagnosed as coronary AV fistula with VSD, and was taken surgical correction under cardiopulmonary bypass. VSD was small and subarterial in type, and the fistula was dilated as adult thumb tip size at its distal portion. VSD was closed directly through the pulmonary arteriotomy and the aneurysmal dilation was opened vertically, then it was obliterated using 5-0, 6-0 prolene continuous suture fashioning into a long slender tube. Postoperative course was uneventful.

• 대한핵의학회지
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• 제19권2호
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• pp.65-68
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• 1985

The radioisotope study using $^{99m}Tc-macroaggregated$ Albumin is a simple, non-invasive test for the diagnosis of pulmonary arteriovenous fistula(PAVF). It can show the presence. of the right-to-left shunt at the lung level using the dynamic study, and also the shunt fraction can be estimated. Here we presented the results of the radioisotope study on two patients with PAVF. In one patient, the cardiac catheterization was clone and calculated shunt fractions by both method were well matched.

• 대한핵의학회지
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• 제16권1호
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• pp.83-86
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• 1982

The scintigraphic findings of a congenital pulmonary arteriovenous fistula associated with Osler- Weber-Rendu disease are described.

• Tuberculosis and Respiratory Diseases
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• 제52권5호
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• pp.545-549
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• 2002

임신시에 발생한 폐동정맥기형은 드문 질환으로 유전성 출혈성 모세혈관확장증과 같이 유전적으로 동반되어 나타날 수 있는 질환이다. 저자들은 임신시에 발생한 호흡곤란과 흉부방사선촬영상의 종괴를 주소로 내원한 환자에서 발견된 폐동정맥기형 1예를 경험하였기에 문헌고찰과 함께 보고하는 바이다.

• Journal of Chest Surgery
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• 제45권5호
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• pp.326-329
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• 2012

Pulmonary arteriovenous malformation (PAVM) is a rare anomalous direct communication between the pulmonary artery and vein with a considerable risk of serious complications such as cerebral thromboembolism or abscess and pulmonary hemorrhage. Although the past, surgical resection such as lobectomy was mostly used to treat PAVM, the recent development of endovascular treatment has made it a primary consideration to perform transcatheter embolization using coils or detachable balloons. We report a case of successful transcatheter embolization of giant PAVM with the second generation Amplatzer vascular plug II as a new self-expanding device.

• Journal of Chest Surgery
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• 제15권1호
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• pp.112-117
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• 1982

Communications of coronary arteries with the cardiac cavities have first time been described by Krause in 1865 in a case of an accessory artery draining into the pulmonary artery and later Cayla in a case of a right coronary artery entering the right ventricle. The initial cases have been found accidentally at autopsies, however In recent years after the Introduction of angiography and coronary arteriography, the malformation Is diagnosed during life and is corrected surgically. These conditions are unusual entitles since the advent of angiography they are being diagnosed with increasing frequency. Three patients who had surgical correction of coronary-cardiac chamber fistula at our hospital are presented. In the first case and second case, coronary arteriovenous fistula was corrected horizontal mattress suture ligation with pladget under the cardiopulmonary bypass and third case was corrected double ligation with cardiopulmonary bypass standby. The postoperative courses were uneventful. They discharged without any fistula related complica-tions.

• Journal of Chest Surgery
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• 제24권5호
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• pp.491-497
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• 1991

Coronary arteriovenous fistula is a relatively rare congenital heart disease and it drains into right atrium, right ventricle, pulmonary artery, coronary sinus or superior vena cava. We experienced one case of fistulous communication between right coronary artery and right ventricle which was most common condition. The patient was a 12 year old female and the only sign was continuous cardiac murmur. The cardiac catheterization and coronary angiography showed the fistulous communication between right coronary artery and right ventricle and aneurysmal dilatation of right coronary artery. Under the cardiopulmonary bypass with the hypothermic cardioplegia, fistula opening[7mm] which was located at right ventricle below the tricuspid valve annulus between septal and posterior leaflet was closed with 4 - 0 prolene continuous suture through right ventriculotomy. Her postoperative course was uneventful.

• Journal of Chest Surgery
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• 제25권12호
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• pp.1563-1569
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• 1992

From Jan. 1981 to Dec. 1991, we had treated 25 patients with congenital coronary art-eriovenous fistulas [CAVF] in Seoul National University Hospital. A retrospective review was made to delineate the course and the management of CAVF and to clarify the role of surgical treatment. Fifteen patients were male and 10 were female with The mean age of 17.4 years[from 3 months to 58 years]. The most frequent symptom was dyspnea on exertion[56%]. Other symptoms were angina and palpitation. Sixty-eight percent of the patients were symptomatic. Fifty-three percent of patients less than 20 years old were symptomatic and 100% of patients over 20 years old were symptomatic. Three patients had multiple CAVFs. The fistula drained into the right ventricle in 13, pulmonary artery in 9, left ventricle in 4, right atrium in 2, and left atrium in 1. Thirteen patients had other associated cardiac lesions. The mean pulmonary-to-systemic blood flow[Qp /Qs] in the isolate CAVF group was 2.19. All patients were operated on to correct the fistulas and other associated cardiac lesions. All patients were followed from 1 month to 11 years without late death. Postoperative complication rate was 24% -significant arrhythmia [3], recurred CAVF[1], psychosis[1], pneumonia [1]. Symptomatic improvement was evident postoperatively. Below 20 years old, 94% of patients were asymptomatic, but above 20 years old, symptoms persisted in 25%. In summary, early elective repair of CAVF is indicated in all patients because of higher complication rate and frequent persistent symptoms in older patients.

• 한국임상수의학회지
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• 제5권2호
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• pp.111-118
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• 1988

One four-month-old female shepherd mongrel dog with chief complaints of abdominal distension and dysponea was referred. The authors performed physical examination, hematological examination, X-ray examination, exploratory laparotomy, electrocardiography and angiography as antemortem investigation in addition to postmortem examination. This patient revealed complicated congenital cardiac anormaly including patent ductus arteriosus, both atrial and ventricular hypertrophy, distension in the base of the pulmonary artery, pulmonary stenosis, aortic insufficiency, patent foramen ovate and coronary arteriovenous fistula.

• Journal of Chest Surgery
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• 제38권8호
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• pp.529-537
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• 2005

배경: 이소성증후군과 기능적 단심실을 동반한 환자들은 체정맥 또는 폐정맥의 연결이상, 폐쇄부전을 동반한 공통 방실판막, 우심실형의 단심실과 부정맥이 많이 동반되어 폰탄 수술의 결과가 좋지 않은 것으로 알려져 있다. 이 환자들에 대한 심장외 도관 폰탄 수술의 치근 결과를 연구하였다. 대상 및 방법: 1996년부터 2005년까지 기능적 단심실로 폰탄 수술을 받은 62명(연령: $54.79\pm33.97$개월)의 이소성증후군 환자들에 대하여 심장외 도관 폰탄 수술을 시행하였다. 좌측 이소성 환자가 21명이었고, 우측 이소성 환자가 41명이었다. 2명을 제외한 모든 환자들에서 양방향성 대정맥폐동맥 단락술을 시행하였으며, 천공은 좌측 이소성에서 더 적게 필요하였다. 걸과: 좌측 이소성 군에서 하대정맥 단절과 폐동정맥루가 더 많았으며, 우측 이소성 군에서 페정맥의 연결 이상,공통 방실판막과 우심실형의 단심실이 더 많았다. 병원 내 사망은 3예$(4.8\%)$였으며, $48.8\pm31.0$개월간 추적 관찰하여 만기 사망은 3예$(5.2\%)$였다. 누적생존율은 8년에 좌측 이소성에서 $90.5\pm6.4\%$와 우측 이소성에서 $88.6\pm5.4\%$로 차이가 없었다(p=0.94). 재수술의 자유도는 8년에 좌측이소성에서 $73.9\pm11.3\%$와 우측 이소성에서 $82.3\pm6.7\%$ 로 차이가 없었다(p=0.87). 술 후 이소성증후군에서 방실판막 페쇄부전이 진행하였으며, 좌측 이소성 군에서는 폐동정맥루에 대한 재수술과 동결절 기능장애에 의한 인공심박조율기 삽입이 더 필요하였다. 걸론: 이소성증후군이 있는 기능적 단심실 환자는 심장외 도관 폰탄 수술, 천공, 단계적 수술과 동반된 기형의 적극적인 수술로 폰탄 수술 후 생존율은 호전되었다. 그러나 수술 후 방실판막 폐쇄부전, 부정맥, 그리고 페동정맥루에 대한 술 후 지속적인 추적 관찰이 필요하다.