• Tuberculosis and Respiratory Diseases
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• 제43권6호
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• pp.1042-1047
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• 1996

The Swyer-James syndrome is a relatively uncommon disease entity presented with unilateral hyperlucent lung due to hypoplasia of a pulmonary artery and bronchiectasis of the affected lung. The main finding is a hyperlucent lung with small hilar shadows on the chest X-ray. Pulmonary angiography is the standard method for diagnosis. We report a case of the Swyer-James syndrome with a brief review of literature.

• Journal of Chest Surgery
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• 제33권1호
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• pp.7-19
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• 2000

Background :To assess the accuracy of Electron-Beam Tomography(EBT) in following evaluation of the pulmonary vascular system after a shunt operation in the cyanotic con-genital heart disease with pulmonary stenosis or pulmonary atresia. Material and Method : Sixteen patients(M:F=11:5) who received Blalock-Taussig(n=8) bidirectional cavo-pulmonary shunt(n=10) and unifocalization (n=2) were ncluded in the study. We evaluated the patency of the shunt the morphology of intrapericardial and hilar pulmonary arteries(PA) peripheral pulmonary vascularity by background lung attenuation and the abundance of arterial & venous collateral. Angiography(n=12) and echocardiography(n=20) were used as the gold standard for the comparison of EBT results. Result: EBT was consistent with angiogram/ echo in 100% of the evaluation for the patency of the shunt and in 12(by angiogram 100%) and 19(by echo 95%) for the detection the hypoplasia stenosis or interruption of central PA In measuring of PA EBT and angiogram corrlated(r=0.91) better than EBT-echo(r=0.88) or echo-angiogram(r=0.72) Abundant systemic arterial collateral were noted in 4 and venous collateral in 3 cases. In evaluating the peripheral pulmonary vascularity the homogenous and normal-ranged lung attenuation(m=6) decreased but homo-genous attenuation(n=1) segment-by-sgment heterogeneous attenuation(n=3) homogenous but asymmetrical attenuation(n=3) segment-by-segment heterogeneous attenuation(n=3) homogenous but asymmetrical attenuation(n=3) and venous congestion(n=2) were observed nd 12 of them were compatible with the blood flow pattern revealed by cardiac catheterization. Conclusion: EBT was accurate in the integrated evaluation of the pulmonary vascular system after the shunt including the patency of the shunt operaion the morphology and dimension of the central and hilar PAs and the loco-regional pulmonary flow in the lung parenchyma. It suggests the useful information about the need of secondary shunt operation the proper timing time for total repair and the need of interventional procedure prior to total repair.

• Tuberculosis and Respiratory Diseases
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• 제40권6호
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• pp.742-746
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• 1993

저자들은 원발성 간암과 동반된 폐동맥 색전증 1예를 경험하였기에 문헌고찰과 함께 보고하는 바이다.

• Journal of Chest Surgery
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• 제15권2호
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• pp.194-203
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• 1982

In this investigation we undertook to evaluate the utility of radionuclide cardiac angiography in the detection of cardiac shunts before and after surgical correction. Time-activity curves of ventricles and lungs were evaluated after bolus intravenous injection of 99mTc-human serum albumin in 512 preoperative patients and 551 post-operative patients. Omitting 31 cases of technical failure due to poor bolus, we detected shunts in 459 cases of 481 preoperative evaluations, so the detectability was 95.4%. The cases which couldn`t be detected by this method had small amount of shunt. Also the degree of shunt detected by radioisotope methods were well correlated with oxymetry method. [r=0.89, p<0.01 ] In postoperative evaluations, 18 out of 411 patients with left to right shunt and 10 out of 140 right to left shunt were found to have remnant shunts with radionuclide cardiac angiography. Of the 28 cases with failed operation, 2 were confirmed in reoperation, 2 by cardiac catheterization, 2 by two -dimensional echocardiography. All except one .f these patients had membranous ventricular septal defects and those with left to right shunts had moderate to severe pulmonary hypertension and shunt amount. Also those had larger septal defects than control group. We consider that radionuclide cardiac angiography is a simple and noninvasive method which can show the preoperative diagnosis and postoperative follow up of cardiac shunts.

• Journal of Chest Surgery
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• 제26권9호
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• pp.710-713
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• 1993

Congenital coronary fistula is a rare condition, and with widespread use of cardiac catheterization, angiography and selective coronary arteriography are being recognized with increasing frequency. Fistula originating from the right coronary artery are more common than those from the left coronary artery. The fistula empties into the right side of the heart in 90% of the cases with the right ventricle being the most common recipient chamber, followed by the right atrium and the pulmonary artery. We report a case of congenital coronary artery fistula of the right coronary artery to the left ventricle with significant shunt in a 20 - year old female. It was detected by transthoracic and transesophageal echocardiography and confirmed by cardiac catheterization and coronary angiography. The fistula opening was closed with 6-0 Prolene continuously under cardiopulmonary bypass and moderate hypothermia [ 28 oC ]. Postoperative course was uneventful and the patient was discharged without specific problem.

• Journal of Chest Surgery
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• 제15권1호
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• pp.112-117
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• 1982

Communications of coronary arteries with the cardiac cavities have first time been described by Krause in 1865 in a case of an accessory artery draining into the pulmonary artery and later Cayla in a case of a right coronary artery entering the right ventricle. The initial cases have been found accidentally at autopsies, however In recent years after the Introduction of angiography and coronary arteriography, the malformation Is diagnosed during life and is corrected surgically. These conditions are unusual entitles since the advent of angiography they are being diagnosed with increasing frequency. Three patients who had surgical correction of coronary-cardiac chamber fistula at our hospital are presented. In the first case and second case, coronary arteriovenous fistula was corrected horizontal mattress suture ligation with pladget under the cardiopulmonary bypass and third case was corrected double ligation with cardiopulmonary bypass standby. The postoperative courses were uneventful. They discharged without any fistula related complica-tions.

• Journal of Chest Surgery
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• 제28권4호
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• pp.409-411
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• 1995

One patient developing left main coronary stenosis following double valve replacement is reviewed. Angina pectoris developed 5 months postoperatively. Coronary perfusion with a balloon tip perfusion catheter was performed during previous operation and was considered technically satisfactory. Coronary angiography confirmed stenosis of the left main coronary artery. There was no further coronary arterial disease. An anterior approach between the aorta and pulmonary artery to expose the left main coronary artery was used and patch angioplasty was done. Repeat coronary angiography showed a widely patent left main coronary artery with excellent runoff. A careful search for coronary arterial injury should be made in all symptomatic patients following aortic valve replacement.

• Journal of Chest Surgery
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• 제29권5호
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• pp.495-503
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• 1996

Fonlan수술의 고위험군 환자에게 시행되는 양방향성 상대정맥-폐동맥 단락술은 비교적 낮은 수술 위험과 동맥혈내 산소포화도의 증가,그리고 체심실에 대한 용적 부담을 줄임으로서 Fontan수술전에 시행하는 효과적인 중간 단계의 고식적 수술로서 알려져있다 그러나 낮은 체정맥압에 의해 유지되는 페혈류인 양방향성 상대정 맥-폐동맥 단락술후 폐동맥의 크기 변화에 대 해서는 아직까지 논란이 되고 있 다. 본 연구에서는 양방향성 상대정맥-폐동맥 단락술이 폐동맥의 크기에 미치는 영향을 밝혀내고자 1992 년 2월부터 1994년 7월까지 서울대학교 의과대학 흉부외과학교실에서 양방향성 상대정맥-폐동맥 단락 술을 받은 19명의 환자를 대상으로 수술전 3.8 $\pm$4.8개월 및 수술후 19.6$\pm$6.2개월에 시행한 심도자 및 혈 관조영술의 결과를 검토하고 이를 통계 처리하였다. 폐동맥의 크기는 폐동맥 지수와 McGoon비를 이 용하였고 환자의 나이,체표면적,혈관 성형술 여부,수술전 폐동맥의 크기,수술후심도자 및 혈관조엮 술까지의 기간 등을 변수로 폐동맥의 성장여부를 연구하였다. 수술전 심도자 및 혈관조영술 당시 환자의 평균 나이는 1).7$\pm$15.6개월, 평균 체 Ⅸ湧岵\ulcorner0.40$\pm$0.12 m2, 동맥혈 산소포화도는 71.4$\pm$12.4% 이었다. 우폐동맥의 지름은 7.1$\pm$1.7mm, 좌폐동맥의 지름은 6.2$\pm$ 1.7 mm, 폐동맥 지수는 191.8$\pm$82.7mm21m2, McGoon 비는 1.73$\pm$0.49 였다. 폐동맥 압력은 6명에 서 측정하였는데 평균 폐동맥 압은 21 mmHg 이 었다. 한편 수술후 심도자 및 혈관조영술 당시 환자의 평균 나이는 39.9$\pm$ 16.2개월, 평균 체표면적은 0.58$\pm$ 0.07m', 동맥 혈 산소포화도는 83.0$\pm$3.8 % 이었다. 우폐동맥의 지름은 9.0$\pm$ 1.5 mm, 좌폐동맥의 지름은 7.7 $\pm$2.Omm, 폐동맥 지수는 197.3$\pm$57.1 mm2/m2, McGoon 비는 1.76$\pm$0.32 였다 수술후 전 환자에서 폐동맥 압력을 측정하였으며 평균 폐동맥 압은 12.8 $\pm$3.6mmHg이 었다. 환자의 성장에 따라 폐동맥의 지름도 증가하였으나 폐동맥 지수나 McGoon비는 증가하지 않았다. 또한 환자의 나이, 술후 동맥혈내 산소포화도의 증가 정도, 혈관 성형술 여부, 수술후 심도자 및 혈큰조 영술까지의 기간 등은 수술후의 폐동맥 지수의 증가에 영향을미치지 못하였으며 단지 수술전의 폐동맥 의 크기가 매우 작을 경우(McGoon 비 1.2 미만)에는 폐동맥 지수가 유의한 증가를 보였는데 이는 수술 \ulcorner 동반된 폐동맥 성형술등의 영향이 있었음을 감안하여야 할 것으로 생각되었다. 한편 수술전 폐동맥 크기에 대한 지표로서 폐동맥 지수(PAI)와 McGoon 비(MGR)와는 다음과 같은 유의한 상관관계가 있 음을 알 수 있었다 상관식 : PAI : MGRxl18.0-12.4. 결론적으로 양방향성 상대정맥-폐동맥 단락술이 동맥혈내 산소포화도는 증가시키나 폐동맥 지수는 단기간의 본 연구에서는 증가하지 않는 것으로 나타났다. 향후 박동성 양방향성 상대정맥-폐동맥 단락 술이나 또는 Blalock-Taussig 단락술등이 폐동맥의 성 장에 미치는 영 향에 대한 연구가 필요할 것으로 생각된다.

• Tuberculosis and Respiratory Diseases
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• 제52권5호
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• pp.545-549
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• 2002

임신시에 발생한 폐동정맥기형은 드문 질환으로 유전성 출혈성 모세혈관확장증과 같이 유전적으로 동반되어 나타날 수 있는 질환이다. 저자들은 임신시에 발생한 호흡곤란과 흉부방사선촬영상의 종괴를 주소로 내원한 환자에서 발견된 폐동정맥기형 1예를 경험하였기에 문헌고찰과 함께 보고하는 바이다.

• Journal of Chest Surgery
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• 제21권1호
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• pp.136-142
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• 1988

Between February, 1983, and March, 1987, thirty-one systemic-pulmonary shunts were performed in 28 patients with cyanotic congenital heart disease. Age ranged from 8 months to 28 years [mean age, 5.4 years, Weight ranged from 7 kg to 48 kg [mean weight, 16kg]. There were 4 classic Blalock-Taussig shunts, 5 central polytetrafluoroethylene shunts, 1 aorta-right pulmonary artery shunt with graft, and 21 modified Blalock-Taussig shunts. One patient required another shunt immediately due to insufficient pulmonary blood flow with patent graft. There was no postoperative death. Conduit diameters included 4mm [2 cases], 5 mm [22 cases], and 6 mm [3 cases]. Long term follow up was available in 27 patients [96.4%] with mean period of 20 months [range, 4 months to 49 months]. The effectiveness of shunt was evaluated by cardiac catheterization with angiography [15 patients] or clinically. They showed improvement of systemic oxygen saturation values by 12% and decrease of hemoglobin by 2.3gm/dl [P<0.01]. There were 2 shunt occlusion in central shunts at 32 and 48 months respectively, and one narrowing of graft in modified Blalock-Taussig shunt at 12 months. The patency rate was 91.6% at 24 months for 5 mm grafts in modified Blalock-Taussig shunt.