• Journal of mucopolysaccharidosis and rare diseases
• /
• v.2 no.1
• /
• pp.8-12
• /
• 2016

Mucolipidosis (ML) is a kind of skeletal dysplasia. Characteristic X-ray findings of the bone may contribute to the early diagnosis and treatment of ML II/III. Skeletal radiographs show distinctive patterns at different ages: neonatal hyperparathyroidism, osteodystrophy (similar to chronic osteitis fibrosa cystica), and dysostosis multiplex. Patients with ML II/III show a mixture of osteodystrophic bone changes and atypical changes of dysostosis multiplex: proximal pointing of the metacarpals in the wrist, dysplastic changes in the lower third of the ilia, marked broadening of the ribs becoming oar-shaped, and beaking of the lower thoracic and lumbar vertebrae. In ML II, the osteodystrophy has clinical and radiographic features of neonatal hyperparathyroidism. In some neonatal subjects, chemical hyperparathyroidism is also demonstrated. After transient hyperparathyroidism in newborns, the progressive osteitis fibrosa cystica develops from 3-6 months of age. Patients with ML III show prominent skeletal involvement, particularly the destruction of vertebral bodies and the femoral heads. Intravenous pamidronate treatment is well tolerated, and it can produce clinical effects, with a reduction in bone pain and improvements in mobility in patients with ML III. In this review, the skeletal manifestations of ML II and III are investigated.

• Proceedings of the Korean Society of Broadcast Engineers Conference
• /
• 2009.01a
• /
• pp.742-745
• /
• 2009

This paper proposes a wireless LAN antenna system that tracks an object automatically by using image-based tracking. The proposed system consists of a camera and a pan-tilt unit in addition to a directional wireless LAN antenna. The camera and the directional antenna are set in same direction and they are set on the pan-tilt unit. A target object which has a wireless LAN receiver is tracked by using images captured by the camera. And the directional antenna faces in same direction as the camera by the pan-tilt unit. Therefore, the directional antenna keeps pointing the receiver, and a transmitting efficiency is improved. A result of a fundamental experiment shows that a receiver attached to a flying airship was tracked by a prototype of the proposed antenna system. The airship flied about, and the proposed antenna system was set on a roof of a building. The experimental result indicates an effectiveness of the proposed system compared to the conventional directional LAN antenna.

• Proceedings of the Korean Institute of Information and Commucation Sciences Conference
• /
• 2013.05a
• /
• pp.172-174
• /
• 2013

Today, one of the most important reasons that Media franchise becomes a core part in the visual contents is that they can create added value and profit optimization easily with main source contents. For succeeding in media franchise, outstanding main contents develop and planning ability which can graft main contents onto other genres are required. This paper will analyze media franchise success cases, with The Maple story as the center, will inquire How he succeed in Korea contents market, and will suggest pointing spot of Korea style media franchise. planning ability and several other causes.

• Proceedings of the Korean Society for Agricultural Machinery Conference
• /
• 2000.11b
• /
• pp.300-306
• /
• 2000

This paper introduces a new concept of automation for bio-production with tele-operative system. The proposed system showed practical and feasible way of automation for the volatile bio-production process. Based on the proposition, recognition of the job environment with object identification was performed using computer vision system. A man-machine interactive hybrid decision-making, which utilized a concept of tele-operation was proposed to overcome limitations of the capability of computer in image processing and feature extraction from the complex environment image. Identifying watermelons from the outdoor scene of the cultivation field was selected to realize the proposed concept. Identifying watermelon from the camera image of the outdoor cultivation field is very difficult because of the ambiguity among stems, leaves, shades, and especially fruits covered partly by leaves or stems. The analog signal of the outdoor image was captured and transmitted wireless to the host computer by R.F module. The localized window was formed from the outdoor image by pointing to the touch screen. And then a sequence of algorithms to identify the location and size of the watermelon was performed with the local window image. The effect of the light reflectance of fruits, stems, ground, and leaves were also investigated.

• Proceedings of the KSRS Conference
• /
• 2007.10a
• /
• pp.195-198
• /
• 2007

GOCI(Geostationary Ocean Color Imager) is the core paryload of the geostationary satellite COMS(Communication, Ocean and Meteological Satellite) for ocean monitoring. It is scheduled to be launched at the end of 2008. GOCI observes ocean color around the Korean Peninsula over $2500km{\times}2500km$ area. Whole field of view is divided into 16 solts and scan mechanism enables to point each slot position. Tilted two-axis scan method is used to observe entire field of view with great pointing stability. Vignetting of the optical system appears when the partial obscuration by intermediate optical components occurs. It leads to the variation of the illumination in the image and gradual fading near the edge of the field. It should be prohibited for the stable radiometric performances. In this work, vignetting analysis of GOCI optical system is performed. For the systematic approach, GOCI optical system is divided into scan mechanism part and telescope part. Vignetting analysis of each part is performed and each result is combined for the overall vignetting performances. The analyzed results can be applied to the selection of slot acquisition angle of scan mechanism to minimize vignetting effects.

• Transactions of the Korean Society for Noise and Vibration Engineering
• /
• v.26 no.4
• /
• pp.391-397
• /
• 2016

Vibration disturbances induced by the reaction wheels can severely degrade the performance of high precision payloads on board satellites with high pointing stability requirements. The unwanted disturbances produced by the reaction wheels are composed of fundamental harmonic disturbances due to the flywheel imbalance and sub/higher harmonic disturbances due to bearing irregularities, motor imperfections and so on. Because the wheel speed is constantly changed during the operation of a reaction wheel, the vibration disturbance induced by the reaction wheels can magnify the satellite vibration when the rotating frequency of wheel meets the natural frequency of satellite structure. In order to provide an effective isolation of the reaction wheel disturbances, isolation performance of a hybrid vibration isolator is investigated. In this paper, hybrid vibration isolator that combines passive and active components is developed and its hybrid isolation performance using notch filter control is evaluated in single-axis. The hybrid isolation performance using notch filter control show additional performance improvement compared to the results using only passive components.

• Transactions of the Korean Society for Noise and Vibration Engineering
• /
• v.24 no.7
• /
• pp.517-524
• /
• 2014

Micro-vibration induced by on-board equipments such as fly-wheel and cryogenic cooler with mechanical moving parts affects the image quality of high-resolution observation satellite. Micro-vibration isolation system has been widely used for enhancing the pointing performance of observation satellites. In general, the micro-vibration isolation system requires a launch locking mechanism additionally to guarantee the structural safety of mission payloads supported by the isolation system with low stiffness under launch environment. In this study, we propose a passive launch and on-orbit vibration isolation system using shape memory alloy mesh washers for the micro-vibration isolation of spaceborne compressor, which does not require the additional launch locking mechanism. The basic characteristics of the isolator were measured in static and free vibration tests of the isolator, and a simple equivalent model of the isolator was proposed. The effectiveness of the isolator design in a launch environment was demonstrated through sine vibration, random vibration and shock tests.

• Fire Science and Engineering
• /
• v.22 no.5
• /
• pp.125-136
• /
• 2008

Corruption of the bureaucratic society can cause the whole society to corrupt and it can also increase public expense gradually because of the civil society's distrust of the administration. Throughout experience of front-line firefighters, this study lets the entire firefighters take an interest in increasing integrity and make it the primary assignment of fire administration. It is the most important to find out the illogical systems and try to improve them in order to solve the increasingly secret and sophisticated forms of corruption completely. The purpose of this study is to show the ways to improve firefighters' integrity by analyzing and pointing out the main factor and the realities of corruption of firefighters.

• Journal of Fashion Business
• /
• v.7 no.6
• /
• pp.21-31
• /
• 2003

The CLI(Consumer Life Information) is a new study to unite and create new values recognizing the importance of knowledge and information in information-oriented society based on domestic science and digital technology. The objective of this research is to define academic identity of consuming science and CLI, to analyze the theory, styles, manners, psychology and the concept of consumption, which is the base of consuming life, and to present the direction of CLI with tasks and three major axises of CLI. Nowadays, international order demands new paradigms from human beings. Especially, vision and creation of the values are settled as methodological ways considering the economic power. The CLI should be on the same horizon adjusting social change of pointing values and quality in consuming patterns of diversity and variety. Therefore, I would suggest the ways for the CLI to head for as follows. First, it is to perceive the 3 major Axises & Task of CLI. Second, it is to develope service (experiencing goods) and goods that can lead consuming lives. Third, it is to study merchandising strategy, to create new signs and symbols of goods, and to collaborate of R & D(reseach and developement) and Business. Fourth, it is to head for globalization. Consequantly, this study will be helpful to establish the theory of relationship between producer and consumer in fashion business included research and developments of qualitative goods.

• Journal of the Korean Society for Aeronautical & Space Sciences
• /
• v.40 no.3
• /
• pp.237-242
• /
• 2012

Spaceborne pulse tube-type cryogenic compressors are widely used for space applications. To guarantee cooling performance of the compressor, mission life time and micor-vibration stability, suitable thermal control of compressor is required. Micro-vibration of the compressor is the one of the sources to degrade the pointing performance of observation satellite. In the present work, on-orbit thermal design of compressor in order not to degrade the performance of micro-vibration isolation system keeping the thermal control performance has been proposed and investigated through thermo-mechanical analysis.