• 대한구순구개열학회지
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• 제3권1호
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• pp.33-36
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• 2000

Cornelia de Lange syndrome is a disorder of unknown biochemical and geneic basis that is recognized on the basis of characteristic facies(low anterior hairline, synophrys, anteverted nares, maxillary prognathism, long philtrum, carp mouth) in association with prenatal and postnatal growth retardation, mental retardation and, in many cases, upper limb anomalies. We treated the patient with incomplete cleft palate related to Cornelia de Lange syndrome.

• Journal of the Korean Association of Oral and Maxillofacial Surgeons
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• 제44권2호
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• pp.86-90
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• 2018

About one-third of patients with transsphenoidal basal encephaloceles have associated congenital anomalies, including cleft palate. Moreover, they are often plagued by symptomatic exacerbations in the form of upper respiratory obstructions, cerebrospinal fluid leaks, meningitis, etc., with few patients being asymptomatic. We herein present a rare asymptomatic case of transsphenoidal basal encephalocele in an 18-month-old child with cleft palate and highlight a modified version of two-flap palatoplasty.

• Journal of the Korean Association of Oral and Maxillofacial Surgeons
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• 제29권3호
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• pp.182-185
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• 2003

저자는 하악 좌측 제2소구치의 치근단 육아조직 수술 도중 우연히 발견된 하치조 관에 발생된 혈관임파종을 치험하였기에 문헌적 고찰과 함께 증례를 보고하며, 혈관임파종의 예후, 치료방법에 대한 보다 더 많은 연구가 필요하리라 사료된다.

• 대한치과교정학회지
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• 제45권6호
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• pp.333-340
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• 2015

Condylar hyperplasia (CH) is a rare disorder characterized by excessive bone growth that almost always presents unilaterally, resulting in facial asymmetry. Classification of the different types of CH can differ depending on the authors. Correct diagnosis is critical in determining the proper treatments and timing. This paper is a review of the recent literature on the epidemiology, etiology, diagnosis, classification, and surgical treatments of CH.

• Imaging Science in Dentistry
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• 제49권4호
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• pp.317-321
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• 2019

Steatocystoma multiplex is an uncommon benign skin disease, which typically manifests as numerous intradermal cysts that can be scattered anywhere on the body. Although usually asymptomatic, it can be significantly disfiguring. One type of steatocystoma multiplex is known to be associated with the autosomal dominant inheritance of a mutation in the gene coding for keratin 17 (KRT17). In such cases, it is often concurrent with other developmental abnormalities of the ectoderm-derived tissues, such as the nails, hair, and teeth. To the best of our knowledge, few cases have been reported of steatocystoma multiplex of the oral and maxillofacial region. This report describes a case of steatocystoma multiplex of both sides of the neck and multiple dental anomalies, with a focus on its clinical, radiological, and histopathological characteristics, as well as the possibility that the patient exhibited the familial type of this condition.

• Maxillofacial Plastic and Reconstructive Surgery
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• 제22권4호
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• pp.442-448
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• 2000

저자들은 2례의 제2새열낭종을 경험하였다. 증례 1은 26세의 여자에서 3년 전부터 서서히 크기가 증가하다가 1년 전 임신과 함께 현저히 크기가 증가한 병력이 있으며, 낭종은 우측 악하부와 흉쇄유돌근 전내측에 위치한 무통성의 파동을 보이는 $7.5{\times}5{\times}4cm$ 크기의 연성 종물로서 내외측으로 누공 형성은 없었다. 증례 2는 56세 남자에서 2년전 악하간극 농양으로 진단하고 절개 및 배농을 시행한 병력이 있으며, 낭종은 좌측 악하부와 흉쇄유돌근 전내측에 위치한 무통성의 파동을 보이는 $5.5{\times}4{\times}3cm$ 크기의 연성 종물로서 역시 내외측으로 누공 형성은 보이지 않았다. 조직학적으로 중층편평상피로 이장되어 있었고 상피 하방에서는 림프양 조직이 관찰되었으며, 완전절제술을 시행한 다음 술후 $3{\sim}4$년이 경과된 현재까지 재발이나 다른 합병증 없이 양호한 경과를 보이고 있다.

• 치과방사선
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• 제29권1호
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• pp.275-282
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• 1999

Purpose: The objective of this study was to compare clinical examination of dental caries and secondary caries with panoramic examination. and to examine bone lesions and dental anomaly of unerupted state. Materials and Methods: In this study. clinical records and panoramic radiographs were available for 89 first grade students in elementary school. Dental caries of occlusal surfaces. proximal surfaces. and buccolingual surfaces were examined. Secondary caries was examined too. In addition. the central lesion and dental anomaly of unerupted state were examined in panoramic radiographs. Results: The obtained results were as followed: 1. Carious detectability of clinical examination in occlusal and buccolingual surface was higher than that of panoramic examination. but it is statistically insignificant(p>0.05). In proximal surface. carious detect ability of panoramic examination was higher than that of clinical examination. and it is statistically significant(p<0.01). 2. In contrast to clinical examination only. when the two examination methods were combined. there was additional detection of dental caries(26.7％ in occlusal surface. 48.2％ in proximal surface. 33.3％ in buccolingual surface. and 38.3％ totally). 3. In detection of secondary caries. panoramic examination had lower ability than clinical examination in all three surfaces. but in case that both methods were combined. totally 36.0％ extra carious lesions were detected. 4. In panoramic examination. detectability of secondary caries in upper teeth is lower than lower teeth. 5. In panoramic examination. it was possible to detect the central lesions and dental anomalies of unerupted state which cannot be detected in clinical examination. Conclusion: It is useful to combine the panoramic examination with clinical examination in order to increase carious detectability and to evaluate the central lesions and dental anomalies of unerupted state

• Imaging Science in Dentistry
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• 제51권4호
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• pp.351-361
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• 2021

Purpose: The clivus is a region in the anterior section of the occipital bone that is commonly imaged on large-volume cone-beam computed tomography (CBCT). There have been several reports of incidental clivus variations and certain pathological entities that have been attributed to the variations. This study aimed to evaluate the effects of these variations within the scope of dentistry. Materials and Methods: Medical databases (PubMed, Scopus, and Web of Science) were searched using a controlled vocabulary (clival anomalies, cone-beam CT, canalis basilaris medianus, fossa navicularis magna, clival variation). The search was limited to English language, humans, and studies published in the last 25 years. The articles were exported into RefWorks^® and duplicates were removed. The remaining articles were screened and reviewed for supporting information on variations of the clivus on CBCT imaging. Results: Canalis basilaris medianus and fossa navicularis magna were the most common anomalies noted. Many of these variations were asymptomatic, with most patients unaware of the anomaly. In certain cases, associated pathologies ranged from developmental (Tornwaldt cyst), to acquired (recurrent meningitis). While no distinct pathognomonic aspects were noted, there were unique patterns of radiographic diagnosis and treatment modalities. Most patients had a normal course of follow-up. Conclusion: Interpretation of CBCT volumes is a skill every dentist must possess. When reviewing large-volume CBCT scans, the clinician should be able to distinguish pathology from normal anatomic variations within the skull base. The majority of clivus variations are asymptomatic and will remain undetected unless incidentally noted on radiographic examinations.

• Journal of the Korean Association of Oral and Maxillofacial Surgeons
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• 제26권1호
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• pp.1-4
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• 2000

저자 등은 경희대학교 구강악안면외과에 내원한 중안면성장 부전을 동반한 하악전돌증 환자의 치료에 있어 관상절개를 통한 Le Fort III 골절단술 및 Le Fort I 골절단술과 양측 하악지시상분 할골절단술을 2회법으로 시행하여 기능적 심미적으로 만족할만한 결과를 얻었기에 보고하는 바이다.

• Maxillofacial Plastic and Reconstructive Surgery
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• 제32권4호
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• pp.373-377
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• 2010

Vascular anomalies are common birthmarks. A eight-month-old male infant had a small size, bright red swelling on the lower lip since birth. On cutaneous examination there was a small brightly erythematous, lobulated, soft plaque on the left side of the lower lip of $10{\times}8{\times}5$ mm. Ultrasonogram examination revealed the lesion and confirmed the diagnosis of capillary hemangioma. The decision to initiate treatment is based on many factors, including size, location and risks and benefits of the proposal therapy. Systemic corticosteroids are decided to prevent the scarring and deforming. Prednisolone was given at a dose of 2 mg/kg/day for 2 weeks followed by tapering for 6 weeks for treatment. After eight weeks there was 80% reduction in the size of the lesion and the left lower lip almost completely cleared without intraoral bleeding. Furthermore, intervention by way of systemic steroids, laser therapy or surgical debulking is appropriate and safe in a select group of patients presenting with a proliferating hemangioma. This report describes a case that was sucessfully treated by systemic steroid therapy for hemangima in intraoral region.