• 제목/요약/키워드: Dystrophic epidermolysis bullosa

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탄소방전등(Carbon Arc)을 이용한 mitis형 열성 이영양성 수포성 표피 박리증 환자의 치험 1례 (A Case Study with Carbon Arc Therapy on Recissive Dystrophic Epidermolysis Bullosa-mitis)

  • 김지현;강은교;전성하;권강
    • 한방안이비인후피부과학회지
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    • 제21권2호
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    • pp.154-164
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    • 2008
  • Epidermolysis Bullosa(EB) is rare, chronic mechanobullous disease, which easily produce bulla by minor trauma or spontaneously. There are three major forms of Epidermolysis bullosa - Epidermolysis bullosa simplex, Junctional epidermolysis bullosa, Dystrophic epidermolysis bullosa. This report is on the 21-year-old female patient who has Dystrophic epidermolysis bullosa(Recessive Dystrophic epidermolysis bullosa-mitis). The Korean medical treatments such as acupuncture and herbal medication were used, with light therapy : Carbon Are, which is known for effect of dermal resuscitation. As a result, Carbon Arc and Korean medical treatment's effect of dermal resuscitation is proved in this study. But more cases are necessary for establishing more effective treatment methods.

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열성 이영양성 수포성 표피박리증 환자 1례 보고 (A Case Study on Recessive Dystrophic Epidermolysis Bullosa-mitis (RDEB-mitis))

  • 권강
    • 한방안이비인후피부과학회지
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    • 제20권1호통권32호
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    • pp.265-284
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    • 2007
  • Introduction : There are three major forms of Epidermolysis Bullosa(EB) - EB Simplex(EBS), Junctional EB(JEB) and Dystrophic EB(DEB). DEB is divided into two groups that Dominant DEB(DDEB) and Recessive DEB(RDEB). RDEB has two types that Hallopeau-Siemens(generalized type) and mitis(localized type). Objects : This study was carried out to observe the progress of Recessive Dystrophic Epidermolysis Bullosa-mitis(RDEB-mitis) disease and find effective remedy. Methods: Both diagnosis and treatment were divided into three groups voluntarily. l. diagnosis - dermatic symptoms, mucosal symptoms, general symptoms 2. treatment - herbal medications, moxibustion, medicines used extemally(外用藥) Results : After treating 9 months, the condition of the patient grew better and the grades of severity of ROEB-mitis disease were lower at each diagnosis item. Conclusions : As above results, oriental medical treatments were very effective for this disease. But more case studies are necessary for establishing more effective diagnosis and treatment methods.

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열성 이영양성 수포성 표피박리증 환자에서 전신마취를 통한 치과치료: 증례 보고 (DENTAL CARIES CONTROL IN A GIRL WITH RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA UNDER THE GENERAL ANESTHESIA : A CASE REPORT)

  • 조성현;송제선;이효설;최형준;최병재;김성오;이제호
    • 대한장애인치과학회지
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    • 제8권2호
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    • pp.109-112
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    • 2012
  • 본 증례는 열성 이영양성 수포성 표피박리증을 가진 2세 8개월 된 환자로 다발성 우식증 소견을 보여 전신마취하에 치료하였다. 1. 환자는 열성 이영양성 수포성 표피박리증으로 전신에 흉터가 있었으며 심한 빈혈 및 패혈증 증상이 있어 수혈 및 항생제 등으로 먼저 전신상태를 회복하였다. 2. 전신마취하에 모든 절치의 발치 및 구치 부위의 치수치료와 기성금속관 수복을 시행하였다.

심부하복벽동맥 천공지 유경 피판을 이용한 이영양성 수포성 표피박리증에 합병된 서혜부 편평 세포 상피암의 치료 - 증례 보고 - (Pedicled Deep Inferior Epigastric Perforator Flap for Treatment of Dystrophic Epidermolysis Bullosa-Associated Squamous Cell Carcinoma in the Groin - Case Report -)

  • 김경필;김지훈;김의식;황재하;김광석;이삼용
    • Archives of Reconstructive Microsurgery
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    • 제19권2호
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    • pp.97-100
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    • 2010
  • Purpose: Epidermolysis bullosa is a rare genetic disease, characterized by the presence of extremely fragile skin and formation of recurrent blister resulting from even a minor mechanical injury. Squamous cell carcinoma (SCC) is recognized as a complication of the chronic scarring associated with dystrophic epidermolysis bullosa (DEB). When a soft tissue defect happens in a patient with epidermolysis bullosa, it is difficult to cover it with a skin graft or a flap. We describe the successful use of a pedicled deep inferior epigastric perforator flap for the reconstruction of SCC associated with DEB in the groin. Methods: A 29-year-old man diagnosed with DEB at birth sustained an ulcer increasing in the right groin for the last 7 months. Under general anesthesia, the mass lesion and lymph nodes were removed and the resulting defect was covered with a pedicled deep inferior epigastric perforator flap. Results: The flap survived completely and his postoperative course was uneventful. Histopathological examination revealed a SCC in the right groin and malignant tumor cells in the removed lymph nodes as well. Additional positron emission tomogram showed a malignant lesion in the ileocecal area with regional lymph node metastasis. The patient was referred to an oncologist for chemotheraphy, but the patient refused to take it. During a 4-month follow-up period, there was no recurrence in the right groin. Conclusion: We suggest that perforator flaps can be considered as a reliable alternative for the reconstruction of soft tissue defects in a patient with DEB.

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수포성 표피 박리증 환자의 치과적 관리 : 증례보고 (DENTAL TREATMENT OF PEDIATRIC EPIDERMOLYSIS BULLOSA PATIENTS : CASE REPORTS)

  • 한은옥;김성희;김신;정태성
    • 대한장애인치과학회지
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    • 제8권2호
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    • pp.122-126
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    • 2012
  • 수포성 표피 박리증을 가진 환자들은 구강내 수포 형성, 연조직 점막의 박리, 개구 제한 등의 이유로 치과치료를 시행하는데 있어 상당한 어려움이 있다. 그러므로 치과 치료시 많은 주의사항이 필요하며, 무엇보다 치과 질환의 예방이 중요하다. 수포성 표피 박리증 환자에 있어 이른 시기부터의 구강 관리는 기능적 치열을 유지시켜 주어 저작 효율을 높여주고 영양 공급 면에서도 도움을 주어 성장 발육을 돕는다. 따라서 지속적인 식이 상담과 구강 위생 관리 교육, 불소 도포 등을 위한 정기 검진이 수포성 표피 박리증 환자에서는 필수적이다.