• Journal of Chest Surgery
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• 제23권1호
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• pp.158-161
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• 1990

A congenital coronary artery fistula is an uncommon anomaly which has a direct communication between a coronary artery and the lumen of any one of the four cardiac chambers, or the coronary sinus, or its tributary veins or the superior vena cava. The right coronary artery is involved most frequently, and the abnormal communication in most often is to the right ventricle followed in incidence by drainage into the right atrium and the pulmonary artery. Recently. we experienced a case of congenital coronary artery fistula associated with valvular heart disease. The fistulous communication was noted between the left circumflex artery and the left atrial appendage. Under the cardiopulmonary bypass, the internal obliteration of the left atrial appendage, mitral valve replacement, and aortic valve exploration were accomplished. Postoperative hospital course was uneventful and the patient was discharged without any problems.

• 대한영상의학회지
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• 제85권2호
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• pp.428-433
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• 2024

이중 좌전하행 관상 동맥은 일반 인구에서 약 1%의 유병률을 보이는 드문 선천성 기형이다. 지금까지 이중 좌전하행 관상동맥 기형은 10가지 유형으로 보고되었다. 그중 제4형 이중 좌전하행 관상동맥은 가장 희귀한 유형 중 하나이다. 이중 좌전하행 관상동맥에 대한 지식과 인식은 정확한 진단과 관상동맥 우회 수술 및 경피적 관상동맥 중재술을 계획하는 데 중요하다. 저자들은 수개월 동안 소화불량과 발한을 주소로 내원하였고 짧은 좌전하행 관상동맥의 주요 대각분지에 약 50%-70% 협착이 있었던, 제4형 이중 좌전하행 관상동맥 기형을 가진 59세 남성의 증례를 보고하고자 한다.

• Journal of Chest Surgery
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• 제30권10호
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• pp.1024-1027
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• 1997

좌 관상동맥 폐동맥 이상 기시증은 드문 선천성 심기형으로 유아기에 심부전을 일으키는 질환으로서 수술적인 치료를 하지 않을 경우 대부분 치명적인 것으로 알려져 있다 대혈관 전위의 교정술이 보편화되면서 신생아에서 관상동맥 이식에 대한 기술이 발전되어 근래에는 좌 관상동맥을 대동맥에 이식하여 이중 관상동 맥 체계를 만들어주는 수기가 본 질환의 일차 선택 수술법으로 인정되고 있다. 본 교실에서는 심부전으로 입원한 생후 44일된 여아에서 좌 관상동맥 폐동맥 이상 기시증이 발견되어 좌 관상동맥 대동맥 이식술로 치 료하여 좋은 결과를 얻었으므로 문헌 고찰과 함께 보고하는 바이다.

• Journal of Chest Surgery
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• 제39권10호
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• pp.779-781
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• 2006

좌주관상동맥 폐쇄증은 매우 드문 선천성 관상동맥 기형의 하나로 좌주관상동맥의 근위부가 단절되어 있어서 대부분의 경우 실신이나 성장지연, 심근경색 등의 증상을 나타내며 수술적 치료를 요한다. 호흡곤란을 주소로 내원한 생후 14개월 여아에서 좌주관상동맥 폐쇄증이 진단되어 내흉동맥을 이용한 관상동맥 우회술 시행 후 1년 이상의 추적관찰로 좋은 결과를 확인할 수 있었기에 보고하는 바이다.

• Journal of Chest Surgery
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• 제28권2호
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• pp.188-192
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• 1995

A 50 year old man with acute aortic dissection DeBakey type I, involving right coronary artery and aortic valve, underwent replacement of the ascending aorta and aorto-right coronary bypass grafting. The operative findings showed a large transverse intimal tear was at about 4cm above the aortic valve. The dissection extended out into the proximal right coronary artery. And we found that the right coronary artery originated from the left sinus of Valsalva, run transversally in the aortic wall, with partial rupture. Postoperatively he had no ischemic cardiac symptoms and neurologic complications. He was discharged on postoperative 9th day with good result.

• Journal of Chest Surgery
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• 제35권12호
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• pp.894-897
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• 2002

우관상동맥의 폐동맥 이상 기시증(ARCAPA)은 매우 드문 선천성 심기형으로 증세가 없는 건강한 환자에서 급사를 초래할 수 있으며 주로 부검시 혹은 수술 중 우연히 발견된다 환아는 2세된 여아로 우관상동맥의 폐동맥 기시 이상을 심장초음파 검사로 진단하였고 관상동맥조영촬영으로 확진하였으며 이상 기시하는 우관상동맥을 대동맥으로 성공적으로 전이하였다.

• Clinical and Experimental Pediatrics
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• 제59권sup1호
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• pp.80-83
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• 2016

Isolated anomalous right coronary artery originating from the pulmonary artery (ARCAPA) is a rare congenital coronary anomaly that is asymptomatic and discovered incidentally in most cases. ARCAPA is generally not considered a fatal defect in infancy or childhood, although cases of sudden death have been reported. Here, we report a 2-month-old female infant who presented with a prolonged fever that was determined to be caused by rhinovirus infection. Myocardial ischemia of the left ventricular posterior wall was already seen on echocardiography, and ARCAPA was discovered incidentally. The patient underwent successful surgical reimplantation of the right coronary artery to the aortic root to re-establish dual ostial circulation.

• Journal of Chest Surgery
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• 제27권12호
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• pp.1036-1041
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• 1994

Emergency operation was performed in a patient with severe aortic insufficiency caused by type A acute aortic dissection with aberrant high take-off origin of single coronary artery. The single coronary artery was found to arise from an unusual position high in the ascending aorta. Dissection was begun in the aortic root and involved the single coronary ostium. Valve competance was restored by resuspension of the commissures. the false lumen was obliterated with strips of Teflon felt and surgical glue. The aortic tissues were firmly reinforced and sutured. The proximal aortic stump was anatomically reconstructed, and fortunately the aortic valve was preserved and coronary reimplantation avoided. The patient was discharged at postoperative 13 days without specific complications. Postoperative course during the 18 months follow-up was uneventful.

• Journal of Chest Surgery
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• 제49권5호
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• pp.383-386
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• 2016

Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) is an extremely rare, potentially fatal, congenital anomaly with a high mortality rate in the first year of life. It occurs rarely in adulthood and may appear with malignant ventricular arrhythmia or sudden death. We report a case of a 49-year-old woman with ALCAPA who presented with dyspnea on exertion. Management was coronary artery bypass grafting to the left anterior descending artery and obtuse marginal arteries, closure of the left main coronary artery ostium, and reestablishment of the dual coronary artery system.

• Journal of Chest Surgery
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• 제27권6호
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• pp.472-476
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• 1994

The incidence of single coronary artery is extremely rare in a review of congenital anomalies of the coronary arteries. This 27-year-old male patient was referred for the evaluation of cardiac condition showing exertional dyspnea[NYHA class II-III] and chest discomfort for about 1 year. A complete catheterization study including angiogram disclosed large single coronary artery arising from left aortic sinus [Ogden classification L-4] associated with bicuspid aortic valvular stenosis and low grade supravalvular aortic stenosis. Calcified stenotic aortic valve was fully removed with caution and the 19mm St. Jude Medical valve was then implanted in the small nortic annulus. The patient had an uneventful recovery and was discharged on 13th postoperative day.