Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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Anomalous Origin of the Left Coronary Artery from the Pulmonary Artery in Adulthood: Challenges and Outcomes

  • Kothari, Jignesh (Department of Cardio Vascular and Thoracic Surgery, U. N. Mehta Institute of Cardiology and Research Center, B. J. Medical College, Civil Hospital Campus) ;
  • Lakhia, Ketav (Department of Cardio Vascular and Thoracic Surgery, U. N. Mehta Institute of Cardiology and Research Center, B. J. Medical College, Civil Hospital Campus) ;
  • Solanki, Parth (Department of Cardio Vascular and Thoracic Surgery, U. N. Mehta Institute of Cardiology and Research Center, B. J. Medical College, Civil Hospital Campus) ;
  • Parmar, Divyakant (Department of Cardiac Anesthesia, U. N. Mehta Institute of Cardiology and Research Center, B. J. Medical College, Civil Hospital Campus) ;
  • Boraniya, Hiren (Department of Cardio Vascular and Thoracic Surgery, U. N. Mehta Institute of Cardiology and Research Center, B. J. Medical College, Civil Hospital Campus) ;
  • Patel, Sanjay (Department of Research, U. N. Mehta Institute of Cardiology and Research Center, B. J. Medical College, Civil Hospital Campus)
  • Received : 2016.03.03
  • Accepted : 2016.07.29
  • Published : 2016.10.05
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Abstract

Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) is an extremely rare, potentially fatal, congenital anomaly with a high mortality rate in the first year of life. It occurs rarely in adulthood and may appear with malignant ventricular arrhythmia or sudden death. We report a case of a 49-year-old woman with ALCAPA who presented with dyspnea on exertion. Management was coronary artery bypass grafting to the left anterior descending artery and obtuse marginal arteries, closure of the left main coronary artery ostium, and reestablishment of the dual coronary artery system.

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References

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Cited by

  1. Misdiagnosed anomalous left coronary artery from the pulmonary artery as endocardial fibroelastosis in infancy : A case series vol.96, pp.24, 2016, https://doi.org/10.1097/md.0000000000007199
  2. An unusual presentation of anomalous left coronary artery from the pulmonary artery (ALCAPA) syndrome in a 70-year-old man: a case report vol.12, pp.1, 2016, https://doi.org/10.1186/s13256-018-1851-4