• Childhood Kidney Diseases
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• v.20 no.2
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• pp.79-82
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• 2016

Fabry disease is an X-linked lysosomal storage disorder caused by a deficiency of the enzyme ${\alpha}-galactosidase$ A, resulting in the accumulation of glycosphingolipids within the lysosomes of various cell types. It has a wide spectrum of clinical phenotypes, and renal failure is a serious complication. Fabry disease is confirmed either by measurement of ${\alpha}-galactosidase$ A activity or by genetic testing for GLA mutations. Renal biopsy findings on light microscopy, specifically enlarged podocytes with foamy cytoplasm, and osmiophilic inclusion bodies in the cytoplasm in all types of renal cells on electron microscopy, are characteristic of this disease. The predominant differential diagnosis is iatrogenic phospholipidosis in association with certain drugs that can cause cellular injuries indistinguishable from Fabry disease. Here, we report the case of a 10-year-old boy with microscopic hematuria who underwent a renal biopsy that showed morphological findings consistent with Fabry disease, although the patient had neither a GLA mutation nor a history of drug consumption. Six years later, spontaneous regression of this renal pathology was observed in a second renal biopsy examination.

• Korean Institute of Interior Design Journal
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• v.14 no.1
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• pp.142-150
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• 2005

This study is arranged the principles of the preservation and restoration in pre-modern architecture, presented guideline of the Intoner restoration in there, and attempted relative-analysis by cases of Japan in curtain of Saporo Houheikan. The method of Original- restorations and Repairs must be preserved In materials and technologies in order to hand over the future generations. The process and method of restorations are the important Cultural Properties as Architecture's itself. And Restorations of industrial manufactures hold the the important position in restoration of pre-modern Architectures. Because industrial technologies are developed and forgotten in rapid. Specially, because industrial materials as curtains were apt to recognize as consumption goods, historicity in that are contained the history of fabric, industrial technologies, and relations of traditional technologies. Conclusionaly, restorations of interior materials in our country are required of \circled1the construction of workframe in search and restoration for original preservation, \circled2the conception of refaires and establishment of investigation, \circled3the stocking of restoration-technologies of pre-modern cultural properties of architectures, \circled4the recognitions of record-preservation, \circled5the improvement of organization, upbring of technicians, establishment of theorical systems.

• Journal of the Korean Society for Aeronautical & Space Sciences
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• v.40 no.1
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• pp.86-92
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• 2012

The well-used actuators for the attitude control of spacecrafts are thruster, reaction wheel, control moment gyroscope, and magnetic torquer. Among them, the control moment gyroscope(CMG) which generates the torque based on the gyroscopic principle in physics, has an advantage of the high torque output compared to the low power consumption. This paper introduces an outline of CMG hardware technology, its application history in spacecrafts, and their associated hardware characteristics. Moreover, its spin-off cases to the other industrial fields such as ship, robotics, and MEMS including their research trend are provided.

• Journal of Nutrition and Health
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• v.27 no.10
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• pp.1058-1069
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• 1994

This study was performed to study the effects of dietary factors on breast and cervical cancer incidence in female Koreans. The subjects were 60 breast and 109 cervical cancer patients recruited from five general hospitals in Seoul. Food intake, anthropometric measurement, and blood compositions were studied through personal interview and using medical records, from August 1991 to September 1992. Body weight, body mass index, triceps skinfold thickness and body muscle mass were at upper limit of normal value, which suggest that these patients had a tendency of overweight. The levels of hemoglobin and hematocrit of the patients were below the normal values. The values of serum protein, albumin, and calcium were in the normal range but close to the lower bound. Therefore the nutritional status assessed by blood composition seems to be marginal. The results of diet history showed that most of the nutrient intake of the subjects met with RDA. The fat intake were 22.9-36.9g/day which supplies about 15-16% of total calories. The results of this study do not agree with those reports of western societies which showed the positive correlation between calorie and fat intake and the incidence of breast and cervical cancer. Even through the calories and fat intake of the subjects were not high, it was higher than national average, especially in breast cancer patients. From this study, dietary factors does not seem to be a major risk factor in cancer incidence in Korea. However, the tendency of the increasing consumption of fat could be a contributing risk factor together with overweight.

• Steel and Composite Structures
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• v.18 no.6
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• pp.1517-1539
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• 2015

Eccentrically braced frames (EBFs) often use conventional steel with medium yield strength. This system requires structural members with large cross-sections for well seismic behavior, which leads to increased material costs. In eccentrically braced frames with high strength steel combination (HSS-EBFs), links use Q345 steel (specified nominal yield strength 345 MPa), braces use Q345 steel or high strength steel while other structural members use high strength steel (e.g., steel Q460 with the nominal yield strength of 460 MPa or steel Q690 with the nominal yield strength of 690 MPa). For this approach can result in reduced steel consumption and increased economic efficiency. Several finite element models of both HSS-EBFs and EBFs are established in this paper. Nonlinear hysteretic analyses and nonlinear time history analyses are conducted to compare seismic performance and economy of HSS-EBFs versus EBFs. Results indicate that the seismic performance of HSS-EBFs is slightly poorer than that of EBFs under the same design conditions, and HSS-EBFs satisfy seismic design codes and reduce material costs.

• Steel and Composite Structures
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• v.28 no.4
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• pp.427-438
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• 2018

Static stability is a decisive factor in the design of domes. Stability-related external factors, such as load and supports, are incorporated into structural vulnerability theory by the definition of a relative rate of joint well-formedness ($r_r$). Hence, the instability mechanism of domes can be revealed. To improve stability, an optimization model against instability, which takes the maximization of the lowest $r_r$ ($r_{r,min}$) as the objective and the discrete member sections as the variables, is established with constraints on the design requirements and steel consumption. Optimizations are performed on two real-life Kiewitt-6 model domes with a span of 23.4 m and rise of 11.7 m, which are initially constructed for shaking table collapse test. Well-formedness analyses and stability calculation (via arc-length method) of the models throughout the optimization history demonstrate that this proposed method can effectively enhance $r_{r,min}$ and optimize the static stability of shell-like structures. Additionally, seismic performance of the optimum models subjected to the same earthquake as in the shaking table test is checked. The supplemental simulations prove that the optimum models are superior to the original models under earthquake load as well.

• Journal of Nutrition and Health
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• v.31 no.1
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• pp.62-71
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• 1998

As stomach cancer is very prevalent in Koreans, various factors, especially dietary factors, related to stomach cancer incidence were examined in a case-control study. The study population consisted of 105 individual s diagnosed for stomach cancer in two general hospitals and 124 control subjects, matched for age and sex, in Seoul. Data for general characteristics, family history, smoking and alcohol consumption, personality , dietary habits and food preference were obtained by self-administered questionnaire and personal interview. Heredity was found to be one of the most important factors causing stomach cancer. In addition, genetic inheritance tended to differ between the sexes. The male patients showed significantly higher incidence of their father's relatives than mother's relatives but the female patients showed higher incidence of their mother's relatives that father's relatives. Smoking was significantly related to stomach cancer. It was also found that the cases drank alcohol more frequently and in much greater quantity than the controls. Personality was related to the incidence of stomach cancer. The cases tended to be more sensitive , impatient, and anxious to do things quickly. With regards to dietary habits, the male cases had meals significantly more irregularly than the male controls. The relative risk of preferencefor salty food and ramen showed to be significantly very high. The male cases consumed carbonated beverages and instant foods, low intake of green yellow vegetables, smoking of cigarettes and drinking of alcohol may contribute to the risk of stomach cancer.

• Korean Journal of Agricultural Science
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• v.29 no.2
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• pp.135-148
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• 2002

In recent years, domestic market environment of rice production is confronted with the problems of excessive production and decrease in per capita consumption, resulting in steady decline of domestic rice price. Moreover, as new trade negotiations of WTO or FTA are being forwarded, cheap price of imported rice will also make the rice production environment being worse off. One of the possible production strategies to relieve this situation could be expanding farm size, which increases market competitiveness in terms of cost-saving. Since 1990's, one of the main agricultural policies for rice production in Korea has been expanding farm size. This study aims at 1)exploring brief history of Korean government's agricultural policy for expanding farm size, 2)examining economic effect of farming size expansion, and 3)discussing major role of government to promote appropriate programs for rice-farming and producers. Main conclusion suggests that appropriate farming size should be expanded upto at least five hectares per farm, with producers' effort to reduce farming costs and continuous investments on agricultural infrastructures including irrigation systems, etc. Continuous government's investment on operation and maintenance on water facility is also one of the important factors in expanding farm size.

• Korean Journal of Health Education and Promotion
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• v.27 no.3
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• pp.13-22
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• 2010

Objectives: The aims of this study were to provide basic information on health behaviors of diabetics by age groups, compared to non-diabetics group. Methods: 2007 National Health Nutrition and Examination Survey Data were used to compare health behaviors between the diabetics group (191 diabetics who had been diagnosed by a doctor) and the non-diabetics group (382 general population) according to age groups. For the purpose of analysis, $x^2$-test (Fischer's exact test) and conditional logistic regression were used. Results: There were significant differences in health behaviors between the diabetics group and the non-diabetics group according to the history of health screening, BMI and alcohol consumption, and there were different pattern of health behaviors by age group. Conclusion: When developing and implementing health education and specific intervention programs for the correction of health behaviors among diabetics, one should consider age, age-adjusted health behavior patterns and priority.

• Proceedings of the Korean Institute of Building Construction Conference
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• 2011.11a
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• pp.31-32
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• 2011

Granulated slag from metal industries and fly ash from the combustion of coal are industrial by-products that have been widely used as mineral admixtures in normal and high strength concrete. Due to the reaction between calcium hydroxide and fly ash or slag, the hydration of concrete containing fly ash or slag is much more complex compared with that of Portland cement. In this paper, the production of calcium hydroxide in cement hydration and its consumption in the reaction of mineral admixtures is considered in order to develop a numerical model that simulates the hydration of concrete containing fly ash or slag. The heat evolution rates of fly ash- or slag-blended concrete is determined by the contribution of both cement hydration and the reaction of the mineral admixtures. Furthermore, the temperature distribution and temperature history in hardening blended concrete are evaluated based on the degree of hydration of the cement and the mineral admixtures. The proposed model is verified through experimental data on concrete with different water-to-cement ratios and mineral admixture substitution ratios.