• Pediatric Gastroenterology, Hepatology & Nutrition
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• 제15권2호
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• pp.122-126
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• 2012

Benign recurrent intrahepatic cholestasis (BRIC) is a rare autosomal recessive inherited disorder characterized by multiple recurrent episodes of severe cholestatic jaundice without obstruction of extrahepatic bile duct. We present the case of a 7-year-old boy with BRIC confirmed by mutation analysis in the ATP8B1 gene and typical clinical manifestation. Despite inheritance of BRIC, we detected a mutation on only one allele. To our knowledge, this is the first report of BRIC with a confirmed single heterozygote novel mutation in the ATP8B1 gene in Korea.

• 대한소아치과학회지
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• 제8권1호
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• pp.89-102
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• 1981

1147 preschool children aged from 3 to 6 living in some farm villages in Kyungki-do were surveyed on dmf and distribution of dental caries in primary dentition. The results were as follows: 1. dmf rate ... 92.76 % boy ... 94.52 % girl ... 90.5.5 % 2. dmf t rate ... 37.07 % dmf t index ... 7.09 3. dmf s rate ... 13.74 % dmf s index ... 13.14 % 4. df t index ... 6.94 5. Each percentage of d, m & f per dmf teeth d rate ... 89.96 % m rate ... 7.24 % f rate ... 2.67 % 6. Most frequent site of dental caries in each tooth $\underline{A}$ mesial $\overline{A}$ distal $\underline{B}$ mesial $\overline{B}$ distal $\underline{C}$ distal $\overline{C}$ distal $\underline{D}$ disto-occlusal $\overline{D}$ disto-occlusal $\underline{E}$ linguo-occlusal $\overline{E}$ occlusal 7. Order of caries susceptibility $\overline{E}$ $\underline{E}$ $\overline{D}$ $\underline{D}$ $\underline{A}$ $\underline{B}$ $\overline{C}$ $\underline{C}$ $\overline{B}$ $\overline{A}$ 8. All the values in caries criteria showed a marked increae from those of 1968.

• 한국의류학회지
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• 제21권3호
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• pp.544-558
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• 1997

Black street style has made unique fashion in popular music such as Jazz, Soul, Rhythm Il Blues. Reggae, and Rap, and it is counterculture and subculture against white. Furthermore, the black street style has played a starring role in the development of white culture as well as black culture, which emerged in direct opposition to the dominant cultures practised by a fraction of fellow countrymen within the black diaspora. The objectives of this study are to examine the social chronology of the black street style and the contemporary fashion, and the influences of the black street style on white culture. The seeds of black's style were sown in the late forties, developing throughout the fifties with the arrival of black immigrants from the west Indies and its examples were zooties, hip cats 8l hipsters, modernists. Rude boy & two-tone was anti·fashion style in sixties and then rastafarians continued in seventies costume is used to convey an essential symbolic class and ethnic message. The latest black's street fashion is hip-hop dress, which is pluralistic and electric, and funk is also erratic. During its ten-year reign as an international style, it has undergone numerous shifts because it is decline of racism B-boy & flygirls toraggamuffins & bhangra style to acid Jazz. These have played a crucial part in influencing the gigh fashion and avant-grade fashion designers' work. Today's street fashion has characteristics of postmodern culture without a racism in global village. Moreover, pop music stars take an effect on the street style continuously. With the opening of a new century, the study of the street style will overcast popular fashion and suggest the direction of fashion design.

• Pediatric Gastroenterology, Hepatology & Nutrition
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• 제3권1호
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• pp.105-109
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• 2000

저자들은 B형 간염 바이러스에 수직 감염된 13세 된 XLA 환아에서 발생한 간세포 암종 1례를 경험하였기에 보고하는 바이며, 간세포 암종의 발생은 XLA 환아에서 수직 감염된 B형 간염 바이러스가 효과적으로 제거되지 못해 발생되었을 것으로 사료된다.

• Childhood Kidney Diseases
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• 제23권2호
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• pp.111-115
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• 2019

Vitamin D dependent rickets type 1A (VDDR1A) is an autosomal recessive disorder caused by mutations in CYP27B1. Clinical findings are growth retardation, hypotonia, muscle weakness, hypocalcemic seizures, and radiological features of rickets. We aimed to present the VDDR1A case with a genetic study of CYP27B1. The 14-month-old boy was admitted to the hospital due to a seizure. Serum calcium, phosphorus, alkaline phosphatase, parathyroid hormone (PTH), 25(OH) vitamin D, and 1,25(OH)2 vitamin D values were 5.1 mg/dL, 3.7 mg/dL, 705 IU/L, 429 pg/mL, 24.9 ng/mL, and 8.8 pg/mL, respectively. Radiological study showed cupping and fraying of the distal ulna and radius. The molecular genetic study revealed that the patient had a compound heterozygous mutation, $Phe443Profs^*24$ and c.589+1G>A, in CYP27B1. Genetic analysis of the family members presented that the mother was heterozygous for the mutation c.589+1G>A, and that the father was heterozygous for $Phe443Profs^*24$. The patient was treated with calcium lactate and calcitriol. Until now, six Korean patients with VDDR1A have been studied. Including this case, Korean patients with VDDR1A were found to have only three different mutations in 14 alleles, indicating that the mutation in the CYP27B1 gene is homogeneous in the Korean population.

• Journal of Chest Surgery
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• 제15권3호
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• pp.361-365
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• 1982

Coarctation of the aorta is a congenital constriction of the aorta of varying degree usually located slightly distal to the origin of the left subclavian artery. This congenital malformation is found at 5-9% of the congenital heart disease in Europe & North America, but in our country, it is reported as one of rare malformations. We present a case of coarctation of the aorta, which had double diaphragms as discrete form. This is 9 year-old boy, who has suffered from hypertensive symptoms since 6 years before. Coarctation of the aorta was confirmed by aortography, and there was no combined anomalies, and it was postductal type, and coarctations were consisted of two diaphragmatic webs at the both ends with a central aneurysmized. After resection of the coarctated segment completely, Woven Dacron graft was inserted with 18mm in diameter & 2.5cm in length successfully.

• 아동학회지
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• 제31권1호
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• pp.35-46
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• 2010

This study analyzed variables that affect children's leadership qualities. The subjects were 400 five-year-old children and their mothers living in the Seoul metropolitan area. The instruments used in this study were the Young Children's Leadership Scale (Kim, 2006), Temperament(Hong, 2008), Peer Interaction (Choi, 2004), Mother's Verbal Control Modes(Do, 1997), and the HOME instrument (Rhee and Jang, 1982). The data collected was analyzed by descriptive statistics, Pearson's correlation, and multiple regression analysis. Our results indicated that (a) girls' scores on leadership were higher than those of boys. (b) Boys' leadership qualities were related to children's temperament, peer relationship, maternal verbal control modes, and home environment. (c) Girls' leadership qualities were related to children's temperament, peer relationship, and home environment. (d) In particular, it was noted that children's temperament (in terms of their sensitivity/endurance) was the strongest predictor for leadership qualities in both boys and girls.

• Journal of Chest Surgery
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• 제32권12호
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• pp.1135-1139
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• 1999

Multistage unifocalization and complete repair have been performed for pulmonary atresia ventricular septal defect and major aortopulmonary collateral arteries. We reported a case that divided major aortopulmonary collateral artery was changed into an aneurysm that compressed the left main bronchus. A 1-year-8-month old boy was operated. The Rastelli operation with left pulmonary artery reconstructuion ligation of patent ductus arteriosus and take-down of right Blalock-Taussing shunt was performed on the patient who had pulmonary atreisia ventricular septal defect patent ductus arteriosus and MAPCA at 1 year and 8 months of his age. He previously underwent the unifocalization and right B-T shunt at 9 months of age,. He repeatedly had difficulty in weaning from the mechanical ventilator, After removing the aneurysm from the divided MAPCA that compressed the left main bronchus externally it was possible to wean him from the mechanical ventilator.

• 대한가정학회지
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• 제27권4호
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• pp.11-20
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• 1989

Teen-agers are much concerned for their appearances. Their clothes reflect their living conditions and serve as a means to represents themselves as well. They also show great concern for the clothes of students of an age. So to guide their clothing behaviours in school plays a very important role in the living guidance of students. From this point, this study was aimed at examing closely the differences of recations as to the girl students' clothing behaviours between boy students and girl students of high school, and the correlation between environment condition and reaction upon the clothing behaviours of girl students. To check the physical environment condition of the family, the family circumstances test, made and standardized by Jung Won Sik, was used. To check the clothing behaviours of girl students, four items-modesty, fashion and esthetics were made and each item had five questions, wihich comprised fifteen questons all told. The subjects of this study included students in eight high schools located in Incheon, totaling 930 boys and girls. The results of this study were summarized as follows: 1. There are great differences in students' reaction upon girl students' clothing behaviours according to their physical circumstances level, sex, grade years and the degree of concern for other sex. (A) The correlation between students' physical circumstances level and their reaction upon the girl students' clothing behaviours is high in all the three items. The higher the students' circumstancses level is, the lower their reaction upon modesty is, and the higher their reaction upon fashion. In case of esthetics, only girl students show great concern for it. (B) As to the reaction upon the girls students' clothing behaviours by sex, girls show higher concern for modesty, fashion and esthetics than boys. (C) As to the reaction upon the girl students' clothing behaviours by the grade years, the first year students as a whole show higher concern for modesty than second grade year students. (D) As to the reaction upon the girl students' clothing behaviours by the degree of concern for other six, the more concern both the boy and the girl students have for other sex, the higher their reactions are upon fashion and esthetics, but the lower upon modesty. 2. From the point of reactions upon the girl students' clothing behaviours, (A) as to fashion, free variables can explain by 7.8 percent the degree of concern for other sex, physicial circumstances level, and sex in that order. (B) as to fashion, free variables can explain by 5.4 persent the concern for other sex, physicial circumstances level, and sex in that order. (C) as to esthetics, free variables can explain by 4.8 percent the concern for other sex, physicial circumstances level, and sex in that order. From the above analysis, the following are included: The concern for other sex has the greatest influence on the girl students clothing behaviours, the physicial circumstances level the nest, sex the third and the grade year the last.

• 대한영양사협회학술지
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• 제14권1호
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• pp.1-12
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• 2008

The Purposes of this study were to assess high school students' nutrient consumption at the ordinary time and to analyze nutrient contents and nutrition consumption of lunch. The questionnaires for self-reported food consumption were distributed to 210 students enrolled in a boy's high school and a girl's high school located in Seoul area. A final response rate was 87.1%, excluding responses that had significant missing data. Data of self-reported food consumption and BMI(Body Mass Index) were analyzed with descriptive analysis and t-test using SPSS Win(ver. 12.0). To measure the serving size and the waste amount, data were collected for three meals in a three day period at each school. A weighed plate method was employed to measure plate wastes and consumption of the menus served. Nutrient analyses for the served and consumed menus were performed using CAN-PRO. The result of nutrient intake determined by self-reported food consumption demonstrated 74.2% of boys and 70.0% of the girls did not meet EAR(Estimated Average Requirement) for calcium. In addition, the data collection showed that 60.2% boys and 26.7% girls did not consume EAR for Vitamin B$_1$. Nutrient analyses of the served and consumed menus at school lunch were compared with 1/3 of the Dietary Reference Intakes(DRIs) for this age group. The served menus did not meet 1/3 of the Recommended Intake(RI) for calcium, iron, and vitamin B$_2$. In contrast, the menu provided to students exceeded almost five times(490%) more than the sodium needed for 1/3 of the Adequate Intake(AI). Considering the amount of the students' plate waste, intake of vitamin A and vitamin C were below 1/3 of the RI, and calcium, iron, and vitamin B$_2$ intake were also reduced. Students' sodium consumption still exceeded 1/3 of the AI at 340.0%.