• Journal of Chest Surgery
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• 제17권3호
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• pp.398-401
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• 1984

Aortopulmonary septal defect is rare congenital heart disease. An 8-year-old girl was diagnosed as a ventricular septal defect with patent ductus arteriosus at Department of Thoracic and Cardiovascular Surgery of Chungnam National University Hospital. On operation, the defect was confirmed as an aortopulmonary septal defect [Type I], anomalous origin of right pulmonary artery from aorta [Type Ill] and patent ductus arteriosus. The defect was repaired anatomically with cardiopulmonary bypass. But she was not survived because of uncontrollable bleeding from aorta.

• Journal of Chest Surgery
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• 제29권5호
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• pp.554-558
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• 1996

대동맥 협부 발육부전, 동맥관 개존, 대동맥기시 우폐동맥을 동반한 원위 대동맥폐동맥 중격결손을 가진 생후 50일된 여아에서 동맥관 결찰,대동맥 협부 발육부전 부위의 절제와 대동맥의 단단문합,우폐동맥과 주폐동맥의 직접 연결과자가심낭편을이용한대동맥폐동맥 중격결손의 봉합을 포함한 일차 완전 교정술을 인공 체외 순환과 완전 순환 정지하에 시행하여 좋은 수술 결과를 얻었다.

• Journal of Chest Surgery
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• 제49권5호
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• pp.374-378
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• 2016

A multistage plan and multidisciplinary approach are the keys to successful repair in patients with pulmonary atresia (PA) with ventricular septal defect (VSD) and major aortopulmonary collateral arteries (MAPCAs). In this article, we present a multidisciplinary approach adopted to treat a patient with PA with VSD and MAPCAs associated with left pulmonary artery interruption.

• Journal of Chest Surgery
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• 제24권7호
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• pp.693-700
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• 1991

A rare case of the association of distal aortopulmonary septal defect, aortic origin of the right pulmonary artery, intact ventricular septum, patent ductus arteriosus and interrupted aortic isthmus in a 40-day-old infant is reported. The infant was suffered from two operations with an interval of nine days. At the first operation a 10mm polytetrafluoroethylene prosthesis was inserted instead of the interrupted aortic isthmus and ductus was ligated via the left posterolateral thoracotomy. But the patient could not be weaned from the respirator because of large amount of left-to-right shunt. So the total correction was subsequently performed after an interval of nine days. At the second operation, tunneling of the right pulmonary artery to the main pulmonary artery through the aortopulmonary septal defect was performed using the Dacron patch via a longitudinal transaortic approach and a separate autologous pericardial patch was applied to the longitudinally incised margins of the anterior wall of the ascending aorta. The second postoperative course was relatively uneventful except some respiratory distress and nutritional problems. Now he is at 6 months of age and thrives well without any symptom. Because the success of the surgical repair of this complex anomalies depends upon the accurate diagnosis and meticulous design of each step of procedure prior to operation these problems are also discussed.

• Journal of Chest Surgery
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• 제32권12호
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• pp.1135-1139
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• 1999

Multistage unifocalization and complete repair have been performed for pulmonary atresia ventricular septal defect and major aortopulmonary collateral arteries. We reported a case that divided major aortopulmonary collateral artery was changed into an aneurysm that compressed the left main bronchus. A 1-year-8-month old boy was operated. The Rastelli operation with left pulmonary artery reconstructuion ligation of patent ductus arteriosus and take-down of right Blalock-Taussing shunt was performed on the patient who had pulmonary atreisia ventricular septal defect patent ductus arteriosus and MAPCA at 1 year and 8 months of his age. He previously underwent the unifocalization and right B-T shunt at 9 months of age,. He repeatedly had difficulty in weaning from the mechanical ventilator, After removing the aneurysm from the divided MAPCA that compressed the left main bronchus externally it was possible to wean him from the mechanical ventilator.

• Journal of Chest Surgery
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• 제32권9호
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• pp.823-826
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• 1999

주대동맥폐동맥간 부행혈관, 심실중격결손과 폐동맥 형성부전이 동반된 6개월된 환아에서 Clamshell 절개 를 통한 일차 완전교정술을 시행하였다. 수술 후 특별한 합병증은 없었으며, 초음파 검사상 남아있는 심실중 격결손이나 의미있는 폐동맥 협착 소견을 보이지 않았다. 이러한 질환의 수술적 접근에 \ulcorner폐로 공급되는 혈 류의 형태에 따라 다양한 방법이 존재하는데, 최근 들어서는 일차 완전교정술에 대한 여러 형태의 수술방법 이 제시되고 있으며, 그 적용 또한 확대되고 있다. 본 증례의 경우 Clamshell 절개 방법을 적용함으로써 종격 동내 병변에 대한 접근이 용이하였으며, 수술 결과 및 합병증 등의 측면에서도 일차 완전교정술의 한 방법 으로 고려해 볼만하다고 여겨진다.

• Journal of Chest Surgery
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• 제48권6호
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• pp.411-414
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• 2015

Interrupted aortic arch with an aortopulmonary window is a rare congenital entity that is associated with high morbidity and mortality, especially in premature low-birth-weight infants, and the proper timing of surgical correction remains a matter of debate. We present the case of a premature infant weighing 1.6 kg who successfully underwent one stage surgical repair to treat interrupted aortic arch with an aortopulmonary window. The therapeutic management of this patient is described below, and a review of the literature is presented.

• Journal of Chest Surgery
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• 제30권5호
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• pp.524-527
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• 1997

폐동맥폐쇄, 심실중격결손증 그리고 큰 대동맥폐동맥 부행혈관이 합병된 선천성심장병은 매우 드물고 폐 혈류공급원에 있어서 매우 다양한 형태를 가지는 복합병변이다. 세종병원 흉부외과는 이러한 질환이 있는 9 개월된 남아 1례에서 정중절개를 톤해 자가조직만을 이용한 폐동맥형성을 포함한 조기 일차완전교정술을 시 행하여 좋은 결과를 얻었기에 보고하는 바이다.

• Journal of Chest Surgery
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• 제17권2호
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• pp.250-256
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• 1984

Eisenmenger syndrome is a condition which systemic arterial blood oxygen unsaturation occurs if obstruction in the pulmonary capillaries raises the pulmonary vascular resistance and pulmonary arterial pressure to or beyond systemic levels and then a significant right to left shunt develops across a preexisting cardiac septal defect or an aortopulmonary communication-We have experienced 3 cases of similar condition. Case I is 24 year old man who has had cyanosis and dyspnea on exertion since childhood. His pulmonary arterial pressure was 110/80mmHg. He was operated under diagnosis of the mitral stenosis and tetralogy of Fallot, but it was finally discovered that he had patent ductus arteriosus and ventricular defect was closed with perforated prosthetic patch, but the patient expired due to right heart failure low cardiac output. Case II was 16 year old female who had pulmonary hypertension of 110/85mmHg. She was diagnosed as Eisenmenger syndrome combining with atrial septal defect and patent ductus arteriosus. Case III was 20 year old male. His pulmonary arterial pressure was 110/70mmHg and the underlying defect was patent ductus arteriosus.

• Journal of Chest Surgery
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• 제23권6호
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• pp.1191-1203
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• 1990

Pulmonary atresia and ventricular septal defect with major aortopulmonary collateral arteries [abbreviated as PA+VSD+MAPCA in the following] has limited the success of attempts at accurate diagnosis and complete surgical repair. From April 1986 to September 1990, 23 patients with PA+VSD+MAPCA among 96 patients of PA+VSD in Seoul National University Children’s Hospital were encountered. The group comprised 14 male and 9 female patients with ages ranging from 17 days to 177 months [mean 49.6 months]. We operated one stage total repair on good pulmonary artery sized two patients by R.E.V. [Reparation a l’etage ventriculaire] and Rastelli operation respectively. And the 11 patients who had independent MAPCAs and hypoplastic central pulmonary artery were dealt with unifocalization and modified Blalock-Taussig Shunt and followed by second stage repair in 3 patients later. We successfully had managed 7 patients whose MAPCAs could be ligated with modified Blalock-Taussig Shunt and followed by second stage repair in 3 patients with R.E.V or Rastelli operation. Recently, three obstruction after 11 unifocalization procedures made us to try palliative right ventricle-pulmonary artery conduit operation by Gore-Tex vascular graft interposition under cardiopulmonary bypass. And so we managed another 3 patients with these procedures for the purpose of pulmonary artery growth whose central pulmonary artery were severely hypoplastic. We experienced one death after second stage repair whose central pulmonary artery was created by 12mm Gore-Tex vascular graft and was unifocalized.