Midline One-Stage Complete Unifocalization and Repair for Pulmonary Atresia. Ventricular Septal Oefect associated with Maior Aortopulmonary Collaterals 1 case report

심실중격결손, 큰 대동맥폐동맥 부행혈로를 동반한 폐동맥폐쇄환자의 정중절개일차완정교정술 - 1 례 보고 -

  • 김웅한 (부천세종병원 흉부외과) ;
  • 이영탁 (부천세종병원 흉부외과)
  • Published : 1997.05.01

Abstract

Pulmonary atresia with ventricular septal defect and major aortopulmonary collaterals is a rare and complex lesion in which great morphologic variability exists regarding the sources of pulmonary blood flow. We report a case of this disease with no true central pulmonary arteries in a 9-month-old-boy successfully treated by one-stage complete unifocalization and repair from a midline stemotomy approach.

폐동맥폐쇄, 심실중격결손증 그리고 큰 대동맥폐동맥 부행혈관이 합병된 선천성심장병은 매우 드물고 폐 혈류공급원에 있어서 매우 다양한 형태를 가지는 복합병변이다. 세종병원 흉부외과는 이러한 질환이 있는 9 개월된 남아 1례에서 정중절개를 톤해 자가조직만을 이용한 폐동맥형성을 포함한 조기 일차완전교정술을 시 행하여 좋은 결과를 얻었기에 보고하는 바이다.

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References

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