• Advances in pediatric surgery
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• 제14권2호
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• pp.196-199
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• 2008

Intraabdominal cystic lymphangioma is an uncommon lesion. It is usually found incidentally in patients presenting with an acute abdomen. Laparoscopic excision of intraabdominal cystic lymphangioma is an easy and safe procedure in children. We report one case of cystic lymphangioma in a 6.year-old female. The lesion was located on the left side of the transverse mesocolon. Laparocopic excision of the cyst was performed without complications.

• 대한기관식도과학회지
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• 제6권1호
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• pp.87-89
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• 2000

A lymphangioma is a benign lesion characterized by proliferation of lymphatic vessels. Occurrence in the oral cavity and oropharynx is rare and is extremely rare in the palatine tonsil. Recently, we experienced a case of lymphagioma on palatine tonsil, so we report this rare case with the review of literatures.

• 대한영상의학회지
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• 제84권2호
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• pp.504-511
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• 2023

혈관림프종은 혈관종과 림프종 성분으로 구성된 드문 종양으로, 증식된 림프관, 모세혈관, 정맥 또는 동맥과 둘러싸는 결합조직 기질로 구성되어 있다. 소장 기원의 혈관림프종은 매우 드물고 그중 소장 장간막 기원은 극히 드물다. 본 증례 보고에서 수술과 면역 화학 염색을 통하여 확인된 55세 남자 환자의 소장 장간막의 혈관림프종 증례를 보고하고자 한다.

• 치위생과학회지
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• 제8권3호
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• pp.207-214
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• 2008

본 연구는 구강내 발생하는 소타액선 종양의 발생 빈도와 조직병리학적 특성에 대한 후향적 연구로서 한국인에서 나타나는 소타액선 종양의 특성을 연구하고자 1990년부터 2006년 8월까지 연세대학교 치과대학 부속병원 구강악안면외과, 연세대학교 의과대학 부속 영동 세브란스병원, 순천향대학교 부속 부천병원에 내원한 200명의 소타액선 종양 환자를 대상으로 치과 및 의과 임상 기록지 검토와 H/E 슬라이드를 재검토하여 다음과 같은 결론을 얻었다. 1. 200명의 환자 중 양성 종양은 123예(61.5%), 악성종양은 77예(38.5%)였으며 남성에서는 87예, 여성에서는 113예였다. 2. 가장 흔하게 발생한 소타액선 종양은 다형성 선종이며 선양 낭성 암종, 점액표피암종, 와틴씨 종양, 선암종과 다형성 선종에서 발생한 악성 종양, 림프관종 등의 순이었다. 3. 호발 부위는 경구개(42.5%), 연구개(9%), 협점막(6%), 입술(3.5%) 부위였다. 4. 발생 연령은 4세부터 70세까지 다양하게 분포하였으며 50대에서 가장 많았다. 양성 종양의 발생 평균 연령은 46.2세였으며 악성 종양의 발생 평균 연령이 56.1세였다. 5. 다형성 선종은 가장 호발한 소타액선 종양으로서 모두 104예였으며 남성 38명, 여성 66명에서 발생하였다. 평균 발생 연령은 46.7세였으며 구개 부위에서 가장 많이 발생하였다. 조직학적 소견은 관 구조 형성, 별 모양, 다각형, 방추형, 형질세포양(plasmacytoid), 연골양, 점액양 구조를 보였으며 불완전한 피막과 종양 피막을 뚫고 다발성으로 발생하는 소견이 관찰되었다. 6. 선양 낭성 암종은 가장 호발한 악성 타액선 종양으로 모두 32예였으며 남성 16명, 여성 16명에서 발생하였다. 평균 발생 연령은 57.4세였으며 경구개 부위에서 가장 많이 발생하였다. 조직학적 소견은 cribriform pattern, 관상 구조, 판상 구조 형성, 종양 세포의 신경 주위 침습 등을 보였다. 7. 점액표피암종은 모두 25예였으며 남성 10명, 여성 15명에서 발생하였다. 평균 발생 연령은 50.0세였으며 경구개 부위에서 가장 많이 발생하였다. 조직학적 소견은 점액 세포, epidermoid-type 세포, intermediate cell의 분포가 대부분 저등급을 보였다. 이외에도 와틴씨 종양, 선암종과 다형성 선종에서 발생한 악성종양, 림프관종 등이 발생하였다. 8. 한국인의 소타액선 종양의 발생 빈도는 양성 종양이 높으며 특히 다형성 선종이 많았고 여성 발생, 구개 부위 발생이 많았으며 다형성 저등급 선암종 등 특정 소타액선 종양의 발생이 극히 적었다.

• Advances in pediatric surgery
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• 제4권2호
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• pp.131-136
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• 1998

Lymphangioma is a congenital malformation of the lymphatic system that expands into the surrounding tissues in a manner similar to a malignant tumor. Surgical excision has been the treatment of choice, but the results are often unsatisfactory due to incomplete resection, fluid collection and recurrences. Intralesional injection of OK-432(lyophilized incubation mixture of Group A Streptococcus pyogenes of human origin) was employed in treating 24 patients with lymphangiomas between 1992 and 1997. The method was used in 21 patients as a primary therapy, and in 3 patients for unresectable or recurrent cases as a secondary treatment. The results were excellent in 8 patients (33.3%), good in 7 patients (21.8 %) and poor in 7 patients (21.8 %). The side effects were fever under $39^{\circ}C$ and local inflammation. However these symptoms subsided in a few days without serious sequelae. These results suggest that intralesional injection of OK-432 is safe and effective treatment for primary lymphangioma as well as a secondary therapy for unresectable or recurrent cases.

• Imaging Science in Dentistry
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• 제30권1호
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• pp.87-91
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• 2000

Lymphangiomas are uncommon benign congenital tumors. Most occur in the head and neck and most lesions present by the age of 2 years. We present our experience with four patients who have lymphangiomas of the head and neck with tongue involvement. First case is a 7-year-old male who has the cystic lymphangioma of left submandibular area. Second a 22-year-old female has a lesion involving the border of right tongue. Third case is the lymphangioma which occurs in the right upper lip of a 6-year old male. The last patient is a 28-year old male who fell down and whose right face was swollen up. He had undergone an operation and been treated with steroid before. The characteristic appearances of imaging methods were described and all lesions best depicted on T2-weighted images. Our experience indicates that MRI is useful in the diagnosis and treatment planning of lymphangioma.

• 대한두경부종양학회지
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• 제33권2호
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• pp.49-53
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• 2017

Foregut cystic developmental malformations are rare developmental anomalies. It is important to diagnose the diseases and manage them properly because these cysts may generate feeding or respiratory difficulties depending on the size and location of the lesions. A newborn was referred for a congenital cervical swelling to our clinic on the second day of his life. Neck SONO and MRI showed an about 6cm sized cystic mass at left submandibular area. Aspirations and sclerotherapies were done repeatedly due to recurred cystic mass. Under the suspicious of cystic hygroma, the mass and submandibular gland were excised. Histologically, it was a benign cyst including gastrointestinal and bronchogenic mucosa and pancreatic tissue. Foregut cyst was suggested for the final diagnosis and the patient was discharged at 9 days after the operation without a complication. He has visited our out-patient department. Although several image studies have been introduced to find out foregut cyst, it is difficult to go through differential diagnosis because of similarity of other benign tumor. Further studies for early diagnosis of cervical foregut cyst are needed for preventing possible related problems.

• Journal of Korean Neurosurgical Society
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• 제30권1호
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• pp.105-109
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• 2001

Lymphangioma is a rare benign developmental vascular tumor that may be found in orbit, skull and elsewhere in head and neck. Few cases of extension of this benign but insidious tumor posteriorly out of the bony orbital cavity have been reported. The patient was 40-year-old man complaining of proptosis of right eye for one month. Physical examination revealed severe right exophthalmus, impairment of eyeball movement in all directions. Visual acuity was much impaired and he could percept only light with right eye. CT and MRI scans showed intraconal and extraconal involvement of ill-defined, heterogenous mass with extension of the tumor posteriorly beyond the orbital cavity involving right frontal and temporal lobe, skull and subcutaneous tissue. The tumor was subtotally removed via orbito-frontal approach without damaging vital neural and orbital component. Then, orbital roof reconstruction and cranioplasty were done with resin. Successful surgical removal of lymphangioma is very difficult due to its severe infiltration to surrounding tissue and tendency to bleed during debulking. We report a rare case of orbital cavernous lymphangioma with intracranial extension treated with surgical decompression, with review of literatures.

• 대한두개안면성형외과학회지
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• 제9권1호
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• pp.38-40
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• 2008

Purpose: Lymphangioma circumscriptum is a rare, congenital benign hamartous malformation, caused by the saccular dilatation of lymph channels lines by normal, single cell, lymphatic endothelia that present as local eruptions of persistent, grouped, translucent vesicles. The lymphangioma circumscriptum lesions may occur on axillary fold shoulder, neck proximal limbs and buccal mucosa. We reported a rare case of lymphangioma circumscriptum on the scalp. Methods: A 15-year-old girl with a $5{\times}3cm$ sized lymphangioma circumscriptum on scalp was examined. It was defined a boundry by ultrasound. And then, a tissue crescent type expander with 120 cc normal saline was inserted on occipital area for a month. After confirmed safety margin of the excised lymphangioma circumscriptum on frozen biopsy and the scalp flap was elevated and covered with empty space. Results: A histopathologic finding revealed that lymphangioma circumscriptum. During 11 months follow up, no relapse was found. Conclusion: We described a rare case of lymphangioma circumscriptum on scalp. By using a tissue expander and excision, we achieved no recurrence and aesthetically satisfactory outcome.

• Advances in pediatric surgery
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• 제15권1호
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• pp.64-67
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• 2009

Splenic cystic lesion is uncommon in children, and cystic lymphangioma of the spleen has not been reported in Korean pediatric patients. Here we report a case of cystic lymphangioma arising from the spleen in a 16 year-old male. The patient presented with left flank pain for 5 days after blunt trauma to the same site. On physical examination, left abdominal tenderness and a palpable spleen were noted. Abdominal ultrasound and MRI revealed multiple septated macro-cystic mass abutting to the spleen medially, suggestive of cystic lymphangioma of the spleen. Laparotomy revealed a 20 cm sized cyst in the spleen, and 2,000mL of dark-brownish fluid was aspirated from the cyst. Splenectomy was performed. Pathological examination revealed the cystic lymphangioma. Post-operative recovery was uneventful, and the patient was discharged at 7 days after surgery.