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http://dx.doi.org/10.4070/kcj.2013.43.3.204

A Case of Myopathy, Encephalopathy, Lactic Acidosis and Stroke-Like Episodes (MEALS) Syndrome with Intracardiac Thrombus  

Joo, Jung-Chul (Sahmyook Medical Center Seoul Hospital)
Seol, Myung Do (Sahmyook Medical Center Seoul Hospital)
Yoon, Jin Won (Sahmyook Medical Center Seoul Hospital)
Lee, Young Soo (Sahmyook Medical Center Seoul Hospital)
Kim, Dong-Keun (Sahmyook Medical Center Seoul Hospital)
Choi, Yong Hoon (Sahmyook Medical Center Seoul Hospital)
Ahn, Hyo Seong (Sahmyook Medical Center Seoul Hospital)
Cho, Wook Hyun (Sahmyook Medical Center Seoul Hospital)
Publication Information
Korean Circulation Journal / v.43, no.3, 2013 , pp. 204-206 More about this Journal
Abstract
Myopathy, encephalopathy, lactic acidosis and stroke-like episodes (MELAS) is a multisystem clinical syndrome manifested by mitochondrial myopathy, encephalopathy, lactic acidosis and recurrent stroke-like episodes. A 27-year-old female with MELAS syndrome presented with cerebral infarction. Echocardiography revealed a thrombus attached to the apex of the hypertrophied left ventricle, with decreased systolic function. The embolism of the intracardiac thrombus might have been the cause of stroke. There should be more consideration given to the increased possibility of intracardiac thrombus formation when a MELAS patient with cardiac involvement is encountered.
Keywords
MELAS syndrome; Heart; Thrombosis;
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