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http://dx.doi.org/10.4070/kcj.2012.42.8.571

Cardiac Sarcoidosis Presenting With Complete Atrioventricular Block and Sustained Monomorphic Ventricular Tachycardia  

Lee, Joo-Myung (Cardiovascular Center and Department of Internal Medicine, Seoul National University Hospital)
Oh, Il-Young (Division of Cardiology, Department of Internal Medicine, College of Medicine, Seoul National University and Cardiovascular Center, Seoul National University Bundang Hospital)
Choi, Dong-Ju (Division of Cardiology, Department of Internal Medicine, College of Medicine, Seoul National University and Cardiovascular Center, Seoul National University Bundang Hospital)
Publication Information
Korean Circulation Journal / v.42, no.8, 2012 , pp. 571-574 More about this Journal
Abstract
Sarcoidosis is a rare but potentially fatal multisystem granulomatous disease of unknown etiology. While a number of clinical manifestations may develop, cardiac involvement (prior to or coincident with sarcoidosis of other organs) is an important prognostic factor. Recently, we encountered a patient with cardiac sarcoidosis who presented with complete atrioventricular (AV) block and sustained ventricular tachycardia. An implantable cardioverter-defibrillator was inserted as a precautionary measure for ventricular tachycardia and symp-tomatic complete AV block. $^{18}F$-fluoro-2-deoxyglucose positron emission tomography confirmed a dramatic response to high-dose steroid at four weeks, as demonstrated by a marked decrease in cardiac sarcoid activity from baseline status.
Keywords
Sarcoidosis; Heart failure; Magentic resonance imaging; Tachycardia, ventricular;
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