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http://dx.doi.org/10.4070/kcj.2012.42.2.136

A Case of Severe Aortic Valve Regurgitation Caused by an Ascending Aortic Aneurysm in a Young Patient With Autosomal Dominant Polycystic Kidney Disease and Normal Renal Function  

Kim, Jeon-Geun (Regional Cardiovascular Center, Division of Cardiology, Department of Internal Medicine, Chungbuk National University School of Medicine)
Kim, Sang-Min (Regional Cardiovascular Center, Division of Cardiology, Department of Internal Medicine, Chungbuk National University School of Medicine)
Lee, Sang-Yeub (Regional Cardiovascular Center, Division of Cardiology, Department of Internal Medicine, Chungbuk National University School of Medicine)
Lee, Ho-Chang (Department of Pathology, Chungbuk National University School of Medicine)
Bae, Jang-Whan (Regional Cardiovascular Center, Division of Cardiology, Department of Internal Medicine, Chungbuk National University School of Medicine)
Hwang, Kyung-Kuk (Regional Cardiovascular Center, Division of Cardiology, Department of Internal Medicine, Chungbuk National University School of Medicine)
Kim, Dong-Woon (Regional Cardiovascular Center, Division of Cardiology, Department of Internal Medicine, Chungbuk National University School of Medicine)
Cho, Myeong-Chan (Regional Cardiovascular Center, Division of Cardiology, Department of Internal Medicine, Chungbuk National University School of Medicine)
Byeon, Sun-Ju (Department of Pathology, College of Medicine, Seoul National University)
Kim, Ki-Bong (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Seoul National University)
Publication Information
Korean Circulation Journal / v.42, no.2, 2012 , pp. 136-139 More about this Journal
Abstract
Aortic aneurysm is one several well-known cardiovascular complications in patients with autosomal dominant polycystic kidney disease (ADPCKD). Commonly affected site of aortic aneurysm and its related dissection in ADPCKD is abdominal aorta. Long standing hypertension, haemodialysis, old age are closely related with discovering of aortic aneurysm and dissection in ADPCKD. However, thoracic aortic aneurysms and its related severe aortic regurgitations (ARs) are rare in younger patients suffering from ADPCKD, especially ones who have normal renal function. Here, we report a case involving a 27-year-old Asian male patient with severe AR due to an ascending aneurysm of the thoracic aorta associated with ADPCKD. The patient had normal renal function without Marfan's habitus. The AR and thoracic aortic aneurysm were corrected surgically.
Keywords
Aortic regurgitation; Aortic aneurysm, thoracic; Polycystic kidney, autosomal dominant;
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