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http://dx.doi.org/10.5933/JKAPD.2014.41.2.166

Basal Cell Nevus Syndrome : A Case Report  

Kim, Jeeyoun (Department of Pediatric Dentistry, Sacred Heart Hospital, Hallym University)
Oh, Sohee (Department of Pediatric Dentistry, Sacred Heart Hospital, Hallym University)
Publication Information
Journal of the korean academy of Pediatric Dentistry / v.41, no.2, 2014 , pp. 166-173 More about this Journal
Abstract
The basal cell nevus syndrome is also known as the Gorlin-Goltz syndrom. It is a dominant autosomal disorder which is characterized by keratocystic odontogenic tumors in the jaw, skeletal abnormalities, and multiple basal cell nevi carcinomas. This study reports an 11-year-old boy with multiple odontogenic keratocysts in the jaw, hypertelorism, and frontal bossing. When a young patient has cystic lesions with an impacted permanent teeth, it is important to preserve the teeth. For a growing patient with impacted permanent teeth, a more conservative method is suggested, which will enable the preservation the permanent teeth in Gorlin-Goltz syndrome.
Keywords
Basal cell nevus syndrome; Impacted permanent teeth; Keratocystic odontogenic tumor;
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