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http://dx.doi.org/10.5933/JKAPD.2012.39.2.161

DENTAL TREATMENTS OF THE CHILD WITH LOWE SYNDROME : A CASE REPORT  

Ju, Chan-Hee (Department of Pediatric Dentistry, School of Dentistry, Chonnam National University)
Kim, Seon-Mi (Department of Pediatric Dentistry, School of Dentistry, Chonnam National University)
Choi, Nam-Ki (Department of Pediatric Dentistry, School of Dentistry, Chonnam National University)
Publication Information
Journal of the korean academy of Pediatric Dentistry / v.39, no.2, 2012 , pp. 161-165 More about this Journal
Abstract
Lowe syndrome, also known as oculocerebrorenal syndrome, is a rare genetic disorder involving eyes, kidney, brain and musculoskeletal system, and occurs predominantly in males. The patient with Lowe syndrome is characterized with congenital cataracts, glaucoma, prominent forehead, thin and sparse hair, mental and growth retardation, muscular hypotonia, renal dysfunction, and metabolic bone disease. We have experienced a 10-year-old boy with Lowe syndrome who had poor oral hygiene and trouble for teeth brushing. To manage his behavior and systemic metabolic disorder, sedation was performed during dental care. Excessive calculus formation in this patient is caused by both medication and lack of ability to maintain oral hygiene. The dental management of those patients has to be focused on prevention due to difficulties in dental treatment and dangers of general anesthesia for the Lowe syndrome.
Keywords
Lowe syndrome; Dental management; Prevention;
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Times Cited By KSCI : 1  (Citation Analysis)
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